Thomas PJ - Search Results

1

The primary folding defect and rescue of ΔF508 CFTR emerge during translation of the mutant domain.

Hoelen H, Kleizen B, Schmidt A, Richardson J, Charitou P, Thomas PJ, Braakman I. Hoelen H, et al. Among authors: thomas pj. PLoS One. 2010 Nov 30;5(11):e15458. doi: 10.1371/journal.pone.0015458. PLoS One. 2010. PMID: 21152102 Free PMC article.

2

Solubilizing mutations used to crystallize one CFTR domain attenuate the trafficking and channel defects caused by the major cystic fibrosis mutation.

Pissarra LS, Farinha CM, Xu Z, Schmidt A, Thibodeau PH, Cai Z, Thomas PJ, Sheppard DN, Amaral MD. Pissarra LS, et al. Among authors: thomas pj. Chem Biol. 2008 Jan;15(1):62-9. doi: 10.1016/j.chembiol.2007.11.012. Chem Biol. 2008. PMID: 18215773

3

Biochemical and biophysical approaches to probe CFTR structure.

Schmidt A, Mendoza JL, Thomas PJ. Schmidt A, et al. Among authors: thomas pj. Methods Mol Biol. 2011;741:365-76. doi: 10.1007/978-1-61779-117-8_24. Methods Mol Biol. 2011. PMID: 21594797 Free PMC article.

4

Introduction to section IV: biophysical methods to approach CFTR structure.

Mendoza JL, Schmidt A, Thomas PJ. Mendoza JL, et al. Among authors: thomas pj. Methods Mol Biol. 2011;741:321-7. doi: 10.1007/978-1-61779-117-8_21. Methods Mol Biol. 2011. PMID: 21594794 Free PMC article.

5

CFTR Folding Consortium: methods available for studies of CFTR folding and correction.

Peters KW, Okiyoneda T, Balch WE, Braakman I, Brodsky JL, Guggino WB, Penland CM, Pollard HB, Sorscher EJ, Skach WR, Thomas PJ, Lukacs GL, Frizzell RA. Peters KW, et al. Among authors: thomas pj. Methods Mol Biol. 2011;742:335-53. doi: 10.1007/978-1-61779-120-8_20. Methods Mol Biol. 2011. PMID: 21547742 Free PMC article.

6

Requirements for efficient correction of ΔF508 CFTR revealed by analyses of evolved sequences.

Mendoza JL, Schmidt A, Li Q, Nuvaga E, Barrett T, Bridges RJ, Feranchak AP, Brautigam CA, Thomas PJ. Mendoza JL, et al. Among authors: thomas pj. Cell. 2012 Jan 20;148(1-2):164-74. doi: 10.1016/j.cell.2011.11.023. Cell. 2012. PMID: 22265409 Free PMC article.

7

The cystic fibrosis-causing mutation deltaF508 affects multiple steps in cystic fibrosis transmembrane conductance regulator biogenesis.

Thibodeau PH, Richardson JM 3rd, Wang W, Millen L, Watson J, Mendoza JL, Du K, Fischman S, Senderowitz H, Lukacs GL, Kirk K, Thomas PJ. Thibodeau PH, et al. Among authors: thomas pj. J Biol Chem. 2010 Nov 12;285(46):35825-35. doi: 10.1074/jbc.M110.131623. Epub 2010 Jul 28. J Biol Chem. 2010. PMID: 20667826 Free PMC article.

8

Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis.

Hutt DM, Herman D, Rodrigues AP, Noel S, Pilewski JM, Matteson J, Hoch B, Kellner W, Kelly JW, Schmidt A, Thomas PJ, Matsumura Y, Skach WR, Gentzsch M, Riordan JR, Sorscher EJ, Okiyoneda T, Yates JR 3rd, Lukacs GL, Frizzell RA, Manning G, Gottesfeld JM, Balch WE. Hutt DM, et al. Among authors: thomas pj. Nat Chem Biol. 2010 Jan;6(1):25-33. doi: 10.1038/nchembio.275. Epub 2009 Dec 6. Nat Chem Biol. 2010. PMID: 19966789 Free PMC article.

9

Effects of the delta F508 mutation on the structure, function, and folding of the first nucleotide-binding domain of CFTR.

Thomas PJ, Pedersen PL. Thomas PJ, et al. J Bioenerg Biomembr. 1993 Feb;25(1):11-9. doi: 10.1007/BF00768063. J Bioenerg Biomembr. 1993. PMID: 7680027

10

N-Alpha-Acetyltransferases and Regulation of CFTR Expression.

Vetter AJ, Karamyshev AL, Patrick AE, Hudson H, Thomas PJ. Vetter AJ, et al. Among authors: thomas pj. PLoS One. 2016 May 16;11(5):e0155430. doi: 10.1371/journal.pone.0155430. eCollection 2016. PLoS One. 2016. PMID: 27182737 Free PMC article.

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