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Page 1
Familial liver adenomatosis associated with hepatocyte nuclear factor 1alpha inactivation.
Bacq Y, Jacquemin E, Balabaud C, Jeannot E, Scotto B, Branchereau S, Laurent C, Bourlier P, Pariente D, de Muret A, Fabre M, Bioulac-Sage P, Zucman-Rossi J. Bacq Y, et al. Gastroenterology. 2003 Nov;125(5):1470-5. doi: 10.1016/j.gastro.2003.07.012. Gastroenterology. 2003. PMID: 14598263
Subsequently, we screened 9 relatives in the 2 independent families for diabetes, hepatocellular adenomas, and HNF-1alpha germline mutations. RESULTS: In family A, a father and his son presented with an intraperitoneal hemorrhagic rupture of a liver adenom …
Subsequently, we screened 9 relatives in the 2 independent families for diabetes, hepatocellular adenomas, and HNF-1alpha germline mu …
Natural history of liver adenomatosis: A long-term observational study.
Barbier L, Nault JC, Dujardin F, Scotto B, Besson M, de Muret A, Bourlier P, Zucman-Rossi J, Salamé E, Bacq Y. Barbier L, et al. J Hepatol. 2019 Dec;71(6):1184-1192. doi: 10.1016/j.jhep.2019.08.004. Epub 2019 Aug 13. J Hepatol. 2019. PMID: 31419515
BACKGROUND & AIMS: Liver adenomatosis (LA) is characterized by the presence of at least 10 hepatocellular adenomas (HCAs), but the natural history of this rare liver disorder remains unclear. ...LAY SUMMARY: Liver adenomatosis is a rare dise …
BACKGROUND & AIMS: Liver adenomatosis (LA) is characterized by the presence of at least 10 hepatocellular adenomas (HCAs), …
Childhood cancers: hepatoblastoma.
Herzog CE, Andrassy RJ, Eftekhari F. Herzog CE, et al. Oncologist. 2000;5(6):445-53. doi: 10.1634/theoncologist.5-6-445. Oncologist. 2000. PMID: 11110595 Free article. Review.
Hepatoblastoma is the most common primary liver tumor in children, accounting for just over 1% of pediatric cancers. The etiology is unknown, but it has been associated with Beckwith-Weidemann syndrome, familial adenomatosis polypi, and low birth weight. ...
Hepatoblastoma is the most common primary liver tumor in children, accounting for just over 1% of pediatric cancers. The etiology is …
Liver adenomatosis in patients with hepatocyte nuclear factor-1 alpha maturity onset diabetes of the young (HNF1A-MODY): Clinical, radiological and pathological characteristics in a French series.
Haddouche A, Bellanne-Chantelot C, Rod A, Fournier L, Chiche L, Gautier JF, Timsit J, Laboureau S, Chaillous L, Valero R, Larger E, Jeandidier N, Wilhelm JM, Popelier M, Guillausseau PJ, Thivolet C, Lecomte P, Benhamou PY, Reznik Y. Haddouche A, et al. J Diabetes. 2020 Jan;12(1):48-57. doi: 10.1111/1753-0407.12959. Epub 2019 Jul 10. J Diabetes. 2020. PMID: 31166087
Liver adenomatosis was confirmed by liver computed tomography, magnetic resonance imaging (MRI), and/or histopathology. ...CONCLUSIONS: The frequency of LA in a cohort of screened HNF1A-MODY patients and the high incidence of LA progression and/or hemorrhage …
Liver adenomatosis was confirmed by liver computed tomography, magnetic resonance imaging (MRI), and/or histopathology. …
Familial pheochromocytoma.
Irvin GL 3rd, Fishman LM, Sher JA. Irvin GL 3rd, et al. Surgery. 1983 Dec;94(6):938-40. Surgery. 1983. PMID: 6648808
In this group a father and three daughters were recognized to have the familial variety of this disease. Malignant hypertension, which began at an early age, was the most prominent characteristic. ...In contrast to most recent reports of familial pheochromocytoma, t …
In this group a father and three daughters were recognized to have the familial variety of this disease. Malignant hypertension, whic …
Hepatic adenomatosis in a young woman with non-familial maturity-onset diabetes of the young type 3.
Miles DA, Holmes S, Minuk GY. Miles DA, et al. Can Liver J. 2021 Aug 9;4(3):328-331. doi: 10.3138/canlivj-2020-0010. eCollection 2021 Summer. Can Liver J. 2021. PMID: 35992257 Free PMC article.
Hepatic adenomatosis (HA) is a rare condition in which multiple adenomas exist in an otherwise healthy liver. ...In this report, we describe a 17-year-old woman with H-HA and non-familial MODY3....
Hepatic adenomatosis (HA) is a rare condition in which multiple adenomas exist in an otherwise healthy liver. ...In this repor …
Hepatocyte nuclear factor-1 alpha gene inactivation: cosegregation between liver adenomatosis and diabetes phenotypes in two maturity-onset diabetes of the young (MODY)3 families.
Reznik Y, Dao T, Coutant R, Chiche L, Jeannot E, Clauin S, Rousselot P, Fabre M, Oberti F, Fatome A, Zucman-Rossi J, Bellanne-Chantelot C. Reznik Y, et al. J Clin Endocrinol Metab. 2004 Mar;89(3):1476-80. doi: 10.1210/jc.2003-031552. J Clin Endocrinol Metab. 2004. PMID: 15001650
The familial screening confirmed the clinical heterogeneity of the liver phenotype, from silent liver adenomatosis to fatal hemorrhage. These observations warrant the systematic screening for liver adenomatosis in MODY3 families to …
The familial screening confirmed the clinical heterogeneity of the liver phenotype, from silent liver adenomatosis …
Endoscopic ultrasound in the assessment of advanced duodenal adenomatosis in familial adenomatous polyposis.
Labib PL, Goodchild G, Turbett JP, Skipworth J, Shankar A, Johnson G, Clark S, Latchford A, Pereira SP. Labib PL, et al. BMJ Open Gastroenterol. 2019 Sep 20;6(1):e000336. doi: 10.1136/bmjgast-2019-000336. eCollection 2019. BMJ Open Gastroenterol. 2019. PMID: 31645990 Free PMC article.
OBJECTIVE: Current surveillance strategies for duodenal adenomatosis in familial adenomatous polyposis (FAP) miss malignancies and underestimate cancer risk in ampullary disease. ...
OBJECTIVE: Current surveillance strategies for duodenal adenomatosis in familial adenomatous polyposis (FAP) miss malignancies …
Hepatic adenoma and focal nodular hyperplasia.
Shortell CK, Schwartz SI. Shortell CK, et al. Surg Gynecol Obstet. 1991 Nov;173(5):426-31. Surg Gynecol Obstet. 1991. PMID: 1658955 Review.
Hepatic adenoma and focal nodular hyperplasia are benign lesions of the liver. The incidence of these conditions has been increasing since 1970. Hepatic adenoma primarily affects young women of childbearing age who have a long history of using oral contraceptives, while fo …
Hepatic adenoma and focal nodular hyperplasia are benign lesions of the liver. The incidence of these conditions has been increasing …
35 results