Wegener's granulomatosis: unusual presentations

Hosp Med. 2000 Apr;61(4):250-3. doi: 10.12968/hosp.2000.61.4.1313.

Abstract

Wegener's granulomatosis is a necrotizing vasculitis characterized by respiratory tract involvement and focal glomerulonephritis. Rare presentations include abdominal pain as a result of gut involvement, pericarditis, cardiac arteritis and blindness. Detection of antineutrophil cytoplasmic antibodies should not be used as a substitute for a histological diagnosis.

Publication types

  • Review

MeSH terms

  • Antibodies, Antineutrophil Cytoplasmic / analysis
  • Diagnosis, Differential
  • Gastrointestinal Diseases / etiology
  • Granulomatosis with Polyangiitis / classification
  • Granulomatosis with Polyangiitis / complications*
  • Granulomatosis with Polyangiitis / diagnosis
  • Heart Diseases / etiology
  • Humans
  • Nervous System Diseases / etiology

Substances

  • Antibodies, Antineutrophil Cytoplasmic