Abstract
Wegener's granulomatosis is a necrotizing vasculitis characterized by respiratory tract involvement and focal glomerulonephritis. Rare presentations include abdominal pain as a result of gut involvement, pericarditis, cardiac arteritis and blindness. Detection of antineutrophil cytoplasmic antibodies should not be used as a substitute for a histological diagnosis.
MeSH terms
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Antibodies, Antineutrophil Cytoplasmic / analysis
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Diagnosis, Differential
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Gastrointestinal Diseases / etiology
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Granulomatosis with Polyangiitis / classification
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Granulomatosis with Polyangiitis / complications*
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Granulomatosis with Polyangiitis / diagnosis
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Heart Diseases / etiology
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Humans
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Nervous System Diseases / etiology
Substances
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Antibodies, Antineutrophil Cytoplasmic