Otitis media as a sign of Wegener's granulomatosis in childhood

Acta Otolaryngol Suppl. 2000:543:48-50. doi: 10.1080/000164800453937.

Abstract

Wegener's granulomatosis (WG) is a rare disease among paediatric patients. Chronic otitis media with or without facial nerve dysfunction is a known manifestation of the disease among adults. A case of a 15-year-old boy with WG, whose initial symptoms were acute otitis media and facial nerve paralysis, is presented. The otorhinolaryngological manifestations, as well as diagnostic and current treatment modalities in paediatric patients with WG, are discussed.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Administration, Oral
  • Adolescent
  • Adult
  • Anti-Infective Agents, Urinary / administration & dosage
  • Anti-Infective Agents, Urinary / therapeutic use
  • Anti-Inflammatory Agents / administration & dosage
  • Anti-Inflammatory Agents / therapeutic use
  • Antineoplastic Agents, Alkylating / administration & dosage
  • Antineoplastic Agents, Alkylating / therapeutic use
  • Biopsy
  • Chronic Disease
  • Cyclophosphamide / administration & dosage
  • Cyclophosphamide / therapeutic use
  • Diagnosis, Differential
  • Drug Therapy, Combination
  • Ear, Middle / diagnostic imaging
  • Facial Nerve / physiopathology
  • Facial Paralysis / etiology
  • Facial Paralysis / physiopathology
  • Granulomatosis with Polyangiitis / complications*
  • Granulomatosis with Polyangiitis / drug therapy
  • Humans
  • Injections, Intravenous
  • Male
  • Otitis Media / diagnosis*
  • Otitis Media / etiology*
  • Prednisone / administration & dosage
  • Prednisone / therapeutic use
  • Severity of Illness Index
  • Tomography, X-Ray Computed
  • Trimethoprim, Sulfamethoxazole Drug Combination / administration & dosage
  • Trimethoprim, Sulfamethoxazole Drug Combination / therapeutic use
  • Turbinates / pathology

Substances

  • Anti-Infective Agents, Urinary
  • Anti-Inflammatory Agents
  • Antineoplastic Agents, Alkylating
  • Trimethoprim, Sulfamethoxazole Drug Combination
  • Cyclophosphamide
  • Prednisone