Aim: This report concerns the most recent knowledge on osteodysplasies, anomalies in the development of the bone tissue, that may concern one or more skeleton segments affecting children.
Case report: The case of a 7-year-old patient is reported, whose left hemimandible showed a radio transparency with a size of 10 x 7 mm. After the usual preliminary diagnostic investigations, it was decided to carry out an ablation. The neoplastic formation was completely enucleated using a conservative operation technique.