Notch2 haploinsufficiency results in diminished B1 B cells and a severe reduction in marginal zone B cells

J Immunol. 2003 Sep 15;171(6):2783-8. doi: 10.4049/jimmunol.171.6.2783.

Abstract

Recent studies have implicated a role for Notch in the generation of marginal zone (MZ) B cells. To further investigate the role of Notch in the B cell lineage, we have analyzed the effects of reduced Notch2 signaling in mice expressing one functional allele of Notch2 (Notch2(+/-)). Notch2(+/-) mice have reduced B1 B cells of the peritoneal cavity and show a severe reduction in MZ B cells of the spleen. The reduction in MZ B cells was not due to the disruption of splenic architecture, disregulated terminal differentiation, nor to increased apoptosis within the MZ B cell compartment. Rather, our data suggest that Notch2 haploinsufficiency leads to impaired development of MZ B cells, possibly by impacting the formation of immediate MZ B precursors. These results provide evidence that Notch2 plays a determining role in the development and/or the maintenance of B1 B and MZ B cells.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Alleles
  • Animals
  • Apoptosis / genetics
  • Apoptosis / immunology
  • B-Lymphocyte Subsets / metabolism
  • B-Lymphocyte Subsets / pathology*
  • Cell Differentiation / genetics
  • Cell Differentiation / immunology
  • Female
  • Genetic Carrier Screening
  • Haplotypes
  • Lymphocyte Count
  • Lymphopenia / genetics*
  • Lymphopenia / immunology
  • Lymphopenia / pathology*
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Peritoneal Cavity / pathology
  • Receptor, Notch2
  • Receptors, Cell Surface / deficiency*
  • Receptors, Cell Surface / genetics*
  • Receptors, Cell Surface / physiology
  • Spleen / anatomy & histology
  • Spleen / immunology
  • Spleen / pathology

Substances

  • Notch2 protein, mouse
  • Receptor, Notch2
  • Receptors, Cell Surface