ATP1A3 mutation in the first asian case of rapid-onset dystonia-parkinsonism

Mov Disord. 2007 Sep 15;22(12):1808-9. doi: 10.1002/mds.21638.

Abstract

We report a 38-year-old Korean man with sporadic rapid-onset dystonia-parkinsonism (RDP), who had a Thr 618 Met mutation in the Na(+)/K(+)-ATPase alpha3 subunit gene (ATP1A3). At the age of 21, he acutely developed severe dystonia and parkinsonism, which rapidly deteriorated into a wheelchair-bound state within 4 days. He is the first Asian RDP patient confirmed by genetic testing, ascertaining that RDP gene mutation is present in Asians. Pathophysiological considerations are briefly discussed.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Dystonic Disorders / complications
  • Dystonic Disorders / genetics*
  • Humans
  • Korea / ethnology
  • Male
  • Methionine / genetics
  • Mutation*
  • Parkinsonian Disorders / complications
  • Parkinsonian Disorders / genetics*
  • Sodium-Potassium-Exchanging ATPase / genetics*
  • Threonine / genetics

Substances

  • Threonine
  • Methionine
  • Sodium-Potassium-Exchanging ATPase