A case of an infant with flail tricuspid valve due to spontaneous papillary muscle rupture: was neonatal lupus the culprit?

G A Fleming; F G Scholl; A Kavanaugh-McHugh; M R Liske

doi:10.1007/s00246-007-9109-8

A case of an infant with flail tricuspid valve due to spontaneous papillary muscle rupture: was neonatal lupus the culprit?

Pediatr Cardiol. 2008 Mar;29(2):442-5. doi: 10.1007/s00246-007-9109-8. Epub 2007 Sep 20.

Authors

G A Fleming¹, F G Scholl, A Kavanaugh-McHugh, M R Liske

Affiliation

¹ Division of Pediatric Cardiology, Monroe Carell Jr. Children's Hospital, Vanderbilt University, Nashville, TN 37232-9119, USA. gregory.fleming@vanderbilt.edu

PMID: 17882476
DOI: 10.1007/s00246-007-9109-8

Abstract

A 3-month-old infant presented in extremis with a flail tricuspid valve. The authors theorized that the genesis of her papillary muscle rupture was perinatal ischemia compounded by worsening pulmonary valvular stenosis leading to excessive fiber tension. Her underlying diagnosis of autoimmune-mediated heart block with endocardial fibroelastosis and prenatal glucocorticoid steroid treatment represents potentiating factors.

Publication types

Case Reports

MeSH terms

Cardiac Surgical Procedures / methods
Cardiomyopathies / complications*
Cardiomyopathies / diagnostic imaging
Cardiomyopathies / surgery
Diagnosis, Differential
Echocardiography, Doppler, Color
Female
Follow-Up Studies
Humans
Infant
Papillary Muscles*
Rupture, Spontaneous
Suture Techniques
Tricuspid Valve Insufficiency / diagnostic imaging
Tricuspid Valve Insufficiency / etiology*
Tricuspid Valve Insufficiency / surgery