No abstract available
MeSH terms
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Adenosine Triphosphate / biosynthesis
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Animals
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DNA, Mitochondrial / genetics
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Electron Transport Complex III / deficiency
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Energy Metabolism*
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Humans
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Metabolism, Inborn Errors*
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Mitochondria, Muscle / metabolism*
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Mitochondria, Muscle / pathology
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Muscular Diseases* / metabolism
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Muscular Diseases* / pathology
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Muscular Diseases* / therapy
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NAD(P)H Dehydrogenase (Quinone)
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Oxygen Consumption
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Quinone Reductases / deficiency
Substances
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DNA, Mitochondrial
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Adenosine Triphosphate
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NAD(P)H Dehydrogenase (Quinone)
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Quinone Reductases
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Electron Transport Complex III