Defects of the respiratory chain

Baillieres Clin Endocrinol Metab. 1990 Sep;4(3):583-619. doi: 10.1016/s0950-351x(05)80069-2.
No abstract available

Publication types

  • Review

MeSH terms

  • Adenosine Triphosphate / biosynthesis
  • Animals
  • DNA, Mitochondrial / genetics
  • Electron Transport Complex III / deficiency
  • Energy Metabolism*
  • Humans
  • Metabolism, Inborn Errors*
  • Mitochondria, Muscle / metabolism*
  • Mitochondria, Muscle / pathology
  • Muscular Diseases* / metabolism
  • Muscular Diseases* / pathology
  • Muscular Diseases* / therapy
  • NAD(P)H Dehydrogenase (Quinone)
  • Oxygen Consumption
  • Quinone Reductases / deficiency

Substances

  • DNA, Mitochondrial
  • Adenosine Triphosphate
  • NAD(P)H Dehydrogenase (Quinone)
  • Quinone Reductases
  • Electron Transport Complex III