Polymyositis presenting with respiratory failure

Indian J Chest Dis Allied Sci. 2011 Oct-Dec;53(4):229-31.

Abstract

Polymyositis is a systemic autoimmune disorder characterised by inflammatory myopathy of the skeletal muscles predominantly affecting the proximal muscles and associated with extra-muscular manifestations like dysphagia and skin involvement. In this case report, we describe the occurrence of diaphragmatic weakness and respiratory failure due to polymyositis with relatively well preserved power in limb muscles.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Cyclophosphamide / administration & dosage
  • Female
  • Humans
  • Immunosuppressive Agents / administration & dosage
  • Lung / diagnostic imaging
  • Methylprednisolone / administration & dosage
  • Polymyositis / complications*
  • Polymyositis / diagnosis*
  • Polymyositis / drug therapy
  • Polymyositis / pathology
  • Pulse Therapy, Drug
  • Respiration, Artificial
  • Respiratory Insufficiency / etiology*
  • Respiratory Insufficiency / therapy
  • Respiratory Paralysis / etiology*
  • Tomography, X-Ray Computed

Substances

  • Immunosuppressive Agents
  • Cyclophosphamide
  • Methylprednisolone