Idiopathic intracranial hypertension (IIH) is a disease particularly affecting young obese women of child-bearing age. IIH can occur at any trimester during pregnancy. There is no increase in maternal, fetal, or neonatal mortality or morbidity in pregnant women diagnosed with IIH. Visual outcome is the same for nonpregnant patients with IIH. Acetazolamide is the mainstay of medical therapy for IIH. No evidence has been found with respect to the adverse effects of acetazolamide use during pregnancy. This medication can be taken during pregnancy but with caution and justification.