[Idiopathic interstitial pneumonias]

Rev Prat. 2014 Sep;64(7):933-7, 939-40.
[Article in French]

Abstract

Idiopathic interstitial pneumonias represent approximately 30% of all interstitial lung diseases. The new classification of idiopathic interstitial pneumonias published in 2013 distinguishes 6 major entities, including chronic fibrosing forms (idiopathic pulmonary fibrosis and nonspecific interstitial pneumonia), acute/subacute forms (cryptogenic organizing pneumonia and acute interstitial pneumonia) and smoking-related disorders (respiratory bronchiolitis interstitial lung disease and desquamative interstitial pneumonia). Pleuroparenchymal fibroelastosis is individualized as a new rare clinco-pathologic entity. For cases not fitting any specific clinic- pathological category, a pragmatic classification based on disease behavior is proposed.

Publication types

  • English Abstract
  • Review

MeSH terms

  • Genetic Diseases, Inborn / diagnosis
  • Genetic Diseases, Inborn / etiology
  • Genetic Diseases, Inborn / therapy
  • Humans
  • Idiopathic Interstitial Pneumonias* / classification
  • Idiopathic Interstitial Pneumonias* / diagnosis
  • Idiopathic Interstitial Pneumonias* / etiology
  • Idiopathic Interstitial Pneumonias* / therapy
  • Idiopathic Pulmonary Fibrosis / diagnosis
  • Idiopathic Pulmonary Fibrosis / etiology
  • Idiopathic Pulmonary Fibrosis / therapy
  • Lung Diseases, Interstitial / diagnosis
  • Lung Diseases, Interstitial / etiology
  • Lung Diseases, Interstitial / therapy
  • Tobacco Use Disorder / complications

Supplementary concepts

  • Interstitial Pneumonitis, Desquamative, Familial