Atypical imaging in a desmoplastic non-infantile astrocytoma

Childs Nerv Syst. 2017 Mar;33(3):517-520. doi: 10.1007/s00381-016-3274-0. Epub 2016 Oct 20.

Abstract

Introduction: Desmoplastic infantile tumors, especially desmoplastic astrocytomas, are uncommon neoplasms that are generally seen within first 2 years of life. Their occurrence in slightly older children is very rare. The typical radiological appearance is a large cystic lesion with small enhancing solid part.

Case: In the present report, we describe a 10-year-old child with atypical appearance of desmoplastic non-infantile astrocytoma which was predominantly solid on imaging.

Conclusion: Although rare, desmoplastic astrocytomas may present even in older children and should be considered in the differential diagnoses. These tumors may present as predominantly solid enhancing lesions and add to the radiological dilemma.

Keywords: Astrocytoma; Desmoplastic astrocytoma; Desmoplastic infantile tumors; Desmoplastic non-infantile astrocytoma; Desmoplastic non-infantile ganglioglioma; Non-infantile.

Publication types

  • Case Reports

MeSH terms

  • Astrocytoma / diagnostic imaging*
  • Brain Neoplasms / diagnostic imaging*
  • Child
  • Diagnosis, Differential
  • Female
  • Humans
  • Magnetic Resonance Imaging*