Adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda: A case report and literature review

Roxana Mititelu; Zainab Ridha; Lydia Ouchene; Elena Netchiporouk

doi:10.1177/2050313X21993304

Adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda: A case report and literature review

SAGE Open Med Case Rep. 2021 Mar 19:9:2050313X21993304. doi: 10.1177/2050313X21993304. eCollection 2021.

Authors

Roxana Mititelu¹, Zainab Ridha², Lydia Ouchene³, Elena Netchiporouk¹

Affiliations

¹ Division of Dermatology, McGill University Health Centre, Montreal, QC, Canada.
² Faculty of Medicine, Université Laval, Quebec City, QC, Canada.
³ Faculty of Medicine, McGill University, Montreal, QC, Canada.

Abstract

The en coup de sabre variant of linear scleroderma typically occurs in children. We report a unique case of adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda. The patient was treated with oral steroids and oral methotrexate improving her cutaneous disease. This case highlights the importance of a thorough cutaneous examination as this adult patient developed an entity traditionally believed to occur in childhood.

Keywords: Scleroderma; adult-onset scleroderma; en coup de sabre scleroderma; linear scleroderma; localized scleroderma; morphea.

Publication types

Case Reports