No abstract available
MeSH terms
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Amino Acid Metabolism, Inborn Errors / blood*
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Amino Acid Metabolism, Inborn Errors / enzymology
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Diabetic Ketoacidosis / blood*
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Female
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Gas Chromatography-Mass Spectrometry
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Hemiterpenes
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Humans
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Infant
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Isovaleryl-CoA Dehydrogenase
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Oxidoreductases / deficiency*
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Oxidoreductases Acting on CH-CH Group Donors*
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Pentanoic Acids / blood*
Substances
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Hemiterpenes
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Pentanoic Acids
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isovaleric acid
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Oxidoreductases
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Oxidoreductases Acting on CH-CH Group Donors
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Isovaleryl-CoA Dehydrogenase