A common variant in BRCA2 is associated with both breast cancer risk and prenatal viability

Nat Genet. 2000 Nov;26(3):362-4. doi: 10.1038/81691.

Abstract

Inherited mutations in the gene BRCA2 predispose carriers to early onset breast cancer, but such mutations account for fewer than 2% of all cases in East Anglia. It is likely that low penetrance alleles explain the greater part of inherited susceptibility to breast cancer; polymorphic variants in strongly predisposing genes, such as BRCA2, are candidates for this role. BRCA2 is thought to be involved in DNA double strand break-repair. Few mice in which Brca2 is truncated survive to birth; of those that do, most are male, smaller than their normal littermates and have high cancer incidence. Here we show that a common human polymorphism (N372H) in exon 10 of BRCA2 confers an increased risk of breast cancer: the HH homozygotes have a 1.31-fold (95% CI, 1.07-1.61) greater risk than the NN group. Moreover, in normal female controls of all ages there is a significant deficiency of homozygotes compared with that expected from Hardy-Weinberg equilibrium, whereas in males there is an excess of homozygotes: the HH group has an estimated fitness of 0.82 in females and 1.38 in males. Therefore, this variant of BRCA2 appears also to affect fetal survival in a sex-dependent manner.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alleles
  • Animals
  • BRCA2 Protein
  • Birth Weight
  • Breast Neoplasms / epidemiology
  • Breast Neoplasms / genetics*
  • Case-Control Studies
  • DNA Repair
  • Exons / genetics
  • Female
  • Fetal Death / epidemiology
  • Fetal Death / genetics*
  • Gene Frequency
  • Genes, Tumor Suppressor*
  • Genetic Predisposition to Disease
  • Genetic Variation*
  • Genotype
  • Humans
  • Infant, Newborn
  • Male
  • Mice
  • Neoplasm Proteins / deficiency
  • Neoplasm Proteins / genetics*
  • Neoplastic Syndromes, Hereditary / epidemiology
  • Neoplastic Syndromes, Hereditary / genetics*
  • Odds Ratio
  • Risk
  • Sex Factors
  • Sex Ratio*
  • Single-Blind Method
  • Transcription Factors / deficiency
  • Transcription Factors / genetics*

Substances

  • BRCA2 Protein
  • Neoplasm Proteins
  • Transcription Factors