No abstract available
MeSH terms
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Aged
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Brain / metabolism*
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Brain / pathology
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Chromosomes, Human, Pair 3*
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Endosomal Sorting Complexes Required for Transport / genetics*
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Female
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Frontotemporal Dementia / genetics*
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Frontotemporal Dementia / pathology
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Humans
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Inclusion Bodies / metabolism
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Male
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Middle Aged
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Mutation / genetics*
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Nerve Tissue Proteins / genetics*
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Pedigree
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Postmortem Changes
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RNA-Binding Protein FUS / metabolism
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Ubiquitin / metabolism
Substances
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CHMP2B protein, human
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Endosomal Sorting Complexes Required for Transport
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Nerve Tissue Proteins
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RNA-Binding Protein FUS
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Ubiquitin