A gain-of-function SNP in TRPC4 cation channel protects against myocardial infarction

Cardiovasc Res. 2011 Aug 1;91(3):465-71. doi: 10.1093/cvr/cvr083. Epub 2011 Mar 22.

Abstract

Aims: The TRPC4 non-selective cation channel is widely expressed in the endothelium, where it generates Ca(2+) signals that participate in the endothelium-mediated vasodilatory response. This study sought to identify single-nucleotide polymorphisms (SNPs) in the TRPC4 gene that are associated with myocardial infarction (MI).

Methods and results: Our candidate-gene association studies identified a missense SNP (TRPC4-I957V) associated with a reduced risk of MI in diabetic patients [odds ratio (OR) = 0.61; confidence interval (CI), 0.40-0.95, P= 0.02]. TRPC4 was also associated with MI in the Wellcome Trust Case-Control Consortium's genome-wide data: an intronic SNP (rs7319926) within the same linkage disequilibrium block as TRPC4-I957V showed an OR of 0.86 (CI, 0.81-0.94; P =10(-4)). Functional studies of the missense SNP were carried out in HEK293 and CHO cells expressing wild-type or mutant channels. Patch-clamp studies and measurement of intracellular [Ca(2+)] in response to muscarinic agonists and direct G-protein activation showed increased channel activity in TRPC4-I957V-transfected cells compared with TRPC4-WT. Site-directed mutagenesis and molecular modelling of TRPC4-I957V suggested that the gain of function was due to the presence of a less bulky Val-957. This permits a firmer interaction between the TRPC4 and the catalytic site of the tyrosine kinase that phosphorylates TRPC4 at Tyr-959 and facilitates channel insertion into the plasma membrane.

Conclusion: We provide evidence for the association of a TRPC4 SNP with MI in population-based genetic studies. The higher Ca(2+) signals generated by TRPC4-I957V may ultimately facilitate the generation of endothelium- and nitric oxide-dependent vasorelaxation, thereby explaining its protective effect at the vasculature.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Analysis of Variance
  • Animals
  • CHO Cells
  • Calcium Signaling
  • Case-Control Studies
  • Chi-Square Distribution
  • Cricetinae
  • Cricetulus
  • Diabetes Complications / genetics*
  • Diabetes Complications / metabolism
  • Diabetes Complications / prevention & control*
  • Exons
  • Female
  • Gene Frequency
  • Genetic Association Studies
  • Genotype
  • HEK293 Cells
  • Humans
  • Linkage Disequilibrium
  • Logistic Models
  • Male
  • Membrane Potentials
  • Middle Aged
  • Models, Molecular
  • Muscarinic Agonists / pharmacology
  • Mutagenesis, Site-Directed
  • Myocardial Infarction / genetics*
  • Myocardial Infarction / metabolism
  • Myocardial Infarction / prevention & control*
  • Odds Ratio
  • Patch-Clamp Techniques
  • Phenotype
  • Phosphorylation
  • Polymorphism, Single Nucleotide*
  • Protein Conformation
  • Risk Assessment
  • Risk Factors
  • Spain
  • Structure-Activity Relationship
  • TRPC Cation Channels / chemistry
  • TRPC Cation Channels / drug effects
  • TRPC Cation Channels / genetics*
  • TRPC Cation Channels / metabolism
  • Transfection

Substances

  • Muscarinic Agonists
  • TRPC Cation Channels
  • TRPC4 ion channel