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CRN2 binds to TIMP4 and MMP14 and promotes perivascular invasion of glioblastoma cells.
Solga R, Behrens J, Ziemann A, Riou A, Berwanger C, Becker L, Garrett L, de Angelis MH, Fischer L, Coras R, Barkovits K, Marcus K, Mahabir E, Eichinger L, Schröder R, Noegel AA, Clemen CS; German Mouse Clinic Consortium. Solga R, et al. Among authors: schroder r. Eur J Cell Biol. 2019 Dec;98(5-8):151046. doi: 10.1016/j.ejcb.2019.151046. Epub 2019 Oct 11. Eur J Cell Biol. 2019. PMID: 31677819
Structural and functional diversity of novel coronin 1C (CRN2) isoforms in muscle.
Xavier CP, Rastetter RH, Stumpf M, Rosentreter A, Müller R, Reimann J, Cornfine S, Linder S, van Vliet V, Hofmann A, Morgan RO, Fernandez MP, Schröder R, Noegel AA, Clemen CS. Xavier CP, et al. Among authors: schroder r. J Mol Biol. 2009 Oct 23;393(2):287-99. doi: 10.1016/j.jmb.2009.07.079. Epub 2009 Aug 3. J Mol Biol. 2009. PMID: 19651142
N471D WASH complex subunit strumpellin knock-in mice display mild motor and cardiac abnormalities and BPTF and KLHL11 dysregulation in brain tissue.
Clemen CS, Schmidt A, Winter L, Canneva F, Wittig I, Becker L, Coras R, Berwanger C; German Mouse Clinic Consortium; Hofmann A, Eggers B, Marcus K, Gailus-Durner V, Fuchs H, de Angelis MH, Krüger M, von Hörsten S, Eichinger L, Schröder R. Clemen CS, et al. Among authors: schroder r. Neuropathol Appl Neurobiol. 2022 Feb;48(1):e12750. doi: 10.1111/nan.12750. Epub 2021 Aug 12. Neuropathol Appl Neurobiol. 2022. PMID: 34312900
The heterozygous R155C VCP mutation: Toxic in humans! Harmless in mice?
Clemen CS, Winter L, Strucksberg KH, Berwanger C, Türk M, Kornblum C, Florin A, Aguilar-Pimentel JA, Amarie OV, Becker L, Garrett L, Hans W, Moreth K, Neff F, Pingen L, Rathkolb B, Rácz I, Rozman J, Treise I, Fuchs H, Gailus-Durner V, de Angelis MH, Vorgerd M, Eichinger L, Schröder R. Clemen CS, et al. Among authors: schroder r. Biochem Biophys Res Commun. 2018 Sep 18;503(4):2770-2777. doi: 10.1016/j.bbrc.2018.08.038. Epub 2018 Aug 9. Biochem Biophys Res Commun. 2018. PMID: 30100055 Free article.
Desminopathies: pathology and mechanisms.
Clemen CS, Herrmann H, Strelkov SV, Schröder R. Clemen CS, et al. Among authors: schroder r. Acta Neuropathol. 2013 Jan;125(1):47-75. doi: 10.1007/s00401-012-1057-6. Epub 2012 Nov 11. Acta Neuropathol. 2013. PMID: 23143191 Free PMC article. Review.
Mutant desmin substantially perturbs mitochondrial morphology, function and maintenance in skeletal muscle tissue.
Winter L, Wittig I, Peeva V, Eggers B, Heidler J, Chevessier F, Kley RA, Barkovits K, Strecker V, Berwanger C, Herrmann H, Marcus K, Kornblum C, Kunz WS, Schröder R, Clemen CS. Winter L, et al. Among authors: schroder r. Acta Neuropathol. 2016 Sep;132(3):453-73. doi: 10.1007/s00401-016-1592-7. Epub 2016 Jul 8. Acta Neuropathol. 2016. PMID: 27393313 Free PMC article.
Strumpellin is a novel valosin-containing protein binding partner linking hereditary spastic paraplegia to protein aggregation diseases.
Clemen CS, Tangavelou K, Strucksberg KH, Just S, Gaertner L, Regus-Leidig H, Stumpf M, Reimann J, Coras R, Morgan RO, Fernandez MP, Hofmann A, Müller S, Schoser B, Hanisch FG, Rottbauer W, Blümcke I, von Hörsten S, Eichinger L, Schröder R. Clemen CS, et al. Among authors: schroder r. Brain. 2010 Oct;133(10):2920-41. doi: 10.1093/brain/awq222. Epub 2010 Sep 9. Brain. 2010. PMID: 20833645
1,022 results