Normalization of intracellular lysosomal hydrolases in I-cell disease fibroblasts with sucrose loading.
Kato T, Okada S, Ohshima T, Inui K, Yutaka T, Yabuuchi H.
Kato T, et al. Among authors: okada s.
J Biol Chem. 1982 Jul 10;257(13):7814-9.
J Biol Chem. 1982.
PMID: 7085649
Free article.
We recently reported that the addition of 88 mM sucrose to the medium of cultured human skin fibroblasts from normal subjects induced several lysosomal hydrolases, but did not induce deficient hydrolases in lysosomal enzyme deficiencies (Kato, T., Okada, S., Ohshima …
We recently reported that the addition of 88 mM sucrose to the medium of cultured human skin fibroblasts from normal subjects induced severa …