Similar articles for PMID: 11087738

Year	Number of Results
1990	1
1991	4
1992	6
1993	8
1994	4
1995	6
1996	4
1997	4
1998	4
1999	4
2000	7
2001	3
2002	1
2003	6
2004	3
2005	1
2006	8
2007	4
2008	6
2009	5
2010	5
2011	4
2012	6
2013	5
2014	2
2015	1
2016	7
2017	3
2018	4
2019	4
2020	6
2021	9
2022	4
2024	0

1

A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Sträussler-Scheinker disease A117V.

Tagliavini F, Lievens PM, Tranchant C, Warter JM, Mohr M, Giaccone G, Perini F, Rossi G, Salmona M, Piccardo P, Ghetti B, Beavis RC, Bugiani O, Frangione B, Prelli F. Tagliavini F, et al. J Biol Chem. 2001 Feb 23;276(8):6009-15. doi: 10.1074/jbc.M007062200. Epub 2000 Nov 21. J Biol Chem. 2001. PMID: 11087738 Free article.

2

Prion proteins with different conformations accumulate in Gerstmann-Sträussler-Scheinker disease caused by A117V and F198S mutations.

Piccardo P, Liepnieks JJ, William A, Dlouhy SR, Farlow MR, Young K, Nochlin D, Bird TD, Nixon RR, Ball MJ, DeCarli C, Bugiani O, Tagliavini F, Benson MD, Ghetti B. Piccardo P, et al. Am J Pathol. 2001 Jun;158(6):2201-7. doi: 10.1016/S0002-9440(10)64692-5. Am J Pathol. 2001. PMID: 11395398 Free PMC article.

3

Amyloid fibrils in Gerstmann-Sträussler-Scheinker disease (Indiana and Swedish kindreds) express only PrP peptides encoded by the mutant allele.

Tagliavini F, Prelli F, Porro M, Rossi G, Giaccone G, Farlow MR, Dlouhy SR, Ghetti B, Bugiani O, Frangione B. Tagliavini F, et al. Cell. 1994 Nov 18;79(4):695-703. doi: 10.1016/0092-8674(94)90554-1. Cell. 1994. PMID: 7954833

4

Amyloid protein of Gerstmann-Sträussler-Scheinker disease (Indiana kindred) is an 11 kd fragment of prion protein with an N-terminal glycine at codon 58.

Tagliavini F, Prelli F, Ghiso J, Bugiani O, Serban D, Prusiner SB, Farlow MR, Ghetti B, Frangione B. Tagliavini F, et al. EMBO J. 1991 Mar;10(3):513-9. doi: 10.1002/j.1460-2075.1991.tb07977.x. EMBO J. 1991. PMID: 1672107 Free PMC article.

5

A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP.

Yang W, Cook J, Rassbach B, Lemus A, DeArmond SJ, Mastrianni JA. Yang W, et al. J Neurosci. 2009 Aug 12;29(32):10072-80. doi: 10.1523/JNEUROSCI.2542-09.2009. J Neurosci. 2009. PMID: 19675240 Free PMC article.

6

A novel Gerstmann-Sträussler-Scheinker disease mutation defines a precursor for amyloidogenic 8 kDa PrP fragments and reveals N-terminal structural changes shared by other GSS alleles.

Mercer RCC, Daude N, Dorosh L, Fu ZL, Mays CE, Gapeshina H, Wohlgemuth SL, Acevedo-Morantes CY, Yang J, Cashman NR, Coulthart MB, Pearson DM, Joseph JT, Wille H, Safar JG, Jansen GH, Stepanova M, Sykes BD, Westaway D. Mercer RCC, et al. PLoS Pathog. 2018 Jan 16;14(1):e1006826. doi: 10.1371/journal.ppat.1006826. eCollection 2018 Jan. PLoS Pathog. 2018. PMID: 29338055 Free PMC article.

7

Different patterns of truncated prion protein fragments correlate with distinct phenotypes in P102L Gerstmann-Sträussler-Scheinker disease.

Parchi P, Chen SG, Brown P, Zou W, Capellari S, Budka H, Hainfellner J, Reyes PF, Golden GT, Hauw JJ, Gajdusek DC, Gambetti P. Parchi P, et al. Proc Natl Acad Sci U S A. 1998 Jul 7;95(14):8322-7. doi: 10.1073/pnas.95.14.8322. Proc Natl Acad Sci U S A. 1998. PMID: 9653185 Free PMC article.

8

Isolation of infectious, non-fibrillar and oligomeric prions from a genetic prion disease.

Vanni I, Pirisinu L, Acevedo-Morantes C, Kamali-Jamil R, Rathod V, Di Bari MA, D'Agostino C, Marcon S, Esposito E, Riccardi G, Hornemann S, Senatore A, Aguzzi A, Agrimi U, Wille H, Nonno R. Vanni I, et al. Brain. 2020 May 1;143(5):1512-1524. doi: 10.1093/brain/awaa078. Brain. 2020. PMID: 32303068 Free PMC article.

9

Amyloid fibrils from the N-terminal prion protein fragment are infectious.

Choi JK, Cali I, Surewicz K, Kong Q, Gambetti P, Surewicz WK. Choi JK, et al. Proc Natl Acad Sci U S A. 2016 Nov 29;113(48):13851-13856. doi: 10.1073/pnas.1610716113. Epub 2016 Nov 14. Proc Natl Acad Sci U S A. 2016. PMID: 27849581 Free PMC article.

10

A case of sporadic Creutzfeldt-Jakob disease with a Gerstmann-Sträussler-Scheinker phenotype but no alterations in the PRNP gene.

Liberski PP, Barcikowska M, Cervenakova L, Bratosiewicz J, Marczewska M, Brown P, Gajdusek DC. Liberski PP, et al. Acta Neuropathol. 1998 Oct;96(4):425-30. doi: 10.1007/s004010050915. Acta Neuropathol. 1998. PMID: 9797009

Save citations to file

Email citations

Send citations to clipboard

Add to Collections

Add to My Bibliography

Create a file for external citation management software

Your saved search

Your RSS Feed

My NCBI Filters

Results by year

Text availability

Article attribute

Article type

Publication date

137 results

Results by year