Pilewski JM - Search Results

1

The effect of discontinuing hypertonic saline or dornase alfa on mucociliary clearance in elexacaftor/tezacaftor/ivacaftor treated people with cystic fibrosis: The SIMPLIFY-MCC Study.

Donaldson SH, Corcoran TE, Pilewski JM, Laube BL, Mogayzel P, Ceppe A, Wu J, Zeman K, Rowe SM, Nichols DP, Gifford AH, Bennett WD, Mayer-Hamblett N; SIMPLIFY MCC Study teams. Donaldson SH, et al. Among authors: pilewski jm. J Cyst Fibros. 2024 Feb 13:S1569-1993(24)00018-3. doi: 10.1016/j.jcf.2024.02.003. Online ahead of print. J Cyst Fibros. 2024. PMID: 38355350

2

Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR.

Donaldson SH, Pilewski JM, Griese M, Cooke J, Viswanathan L, Tullis E, Davies JC, Lekstrom-Himes JA, Wang LT; VX11-661-101 Study Group. Donaldson SH, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2018 Jan 15;197(2):214-224. doi: 10.1164/rccm.201704-0717OC. Am J Respir Crit Care Med. 2018. PMID: 28930490 Free PMC article. Clinical Trial.

3

VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

Davies JC, Moskowitz SM, Brown C, Horsley A, Mall MA, McKone EF, Plant BJ, Prais D, Ramsey BW, Taylor-Cousar JL, Tullis E, Uluer A, McKee CM, Robertson S, Shilling RA, Simard C, Van Goor F, Waltz D, Xuan F, Young T, Rowe SM; VX16-659-101 Study Group. Davies JC, et al. N Engl J Med. 2018 Oct 25;379(17):1599-1611. doi: 10.1056/NEJMoa1807119. Epub 2018 Oct 18. N Engl J Med. 2018. PMID: 30334693 Free PMC article. Clinical Trial.

4

Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax.

Flume PA, Mogayzel PJ Jr, Robinson KA, Rosenblatt RL, Quittell L, Marshall BC; Clinical Practice Guidelines for Pulmonary Therapies Committee; Cystic Fibrosis Foundation Pulmonary Therapies Committee. Flume PA, et al. Am J Respir Crit Care Med. 2010 Aug 1;182(3):298-306. doi: 10.1164/rccm.201002-0157OC. Am J Respir Crit Care Med. 2010. PMID: 20675678

5

A longitudinal analysis of respiratory symptoms in people with cystic fibrosis with advanced lung disease on and off ETI.

Gill ER, Bartlett LE, Milinic T, Burdis N, Pilewski JM, Dunitz JM, Kapnadak SG, Goss CH, Ramos KJ. Gill ER, et al. Among authors: pilewski jm. J Cyst Fibros. 2024 Jan;23(1):161-164. doi: 10.1016/j.jcf.2023.11.008. Epub 2023 Nov 25. J Cyst Fibros. 2024. PMID: 38008684

6

Systems serology in cystic fibrosis: Anti-Pseudomonas IgG1 responses and reduced lung function.

Lu S, Chen K, Song K, Pilewski JM, Gunn BM, Poch KR, Rysavy NM, Vestal BE, Saavedra MT, Kolls JK. Lu S, et al. Among authors: pilewski jm. Cell Rep Med. 2023 Oct 17;4(10):101210. doi: 10.1016/j.xcrm.2023.101210. Cell Rep Med. 2023. PMID: 37852181 Free PMC article.

7

Effect of elexacaftor/tezacaftor/ivacaftor on mucus and mucociliary clearance in cystic fibrosis.

Donaldson SH, Corcoran TE, Pilewski JM, Mogayzel P, Laube BL, Boitet ER, Harris ES, Ceppe A, Edwards LJ, Zeman K, Wu J, Esther CR Jr, Nichols DP, Bennett WD, Rowe SM. Donaldson SH, et al. Among authors: pilewski jm. J Cyst Fibros. 2024 Jan;23(1):155-160. doi: 10.1016/j.jcf.2023.10.010. Epub 2023 Oct 14. J Cyst Fibros. 2024. PMID: 37845149

8

Elexacaftor-tezacaftor-ivacaftor decreases pseudomonas abundance in the sinonasal microbiome in cystic fibrosis.

Zemke AC, Hilliam Y, Stapleton AL, Kimple AJ, Goralski JL, Shaffer AD, Pilewski JM, Senior BA, Lee SE, Cooper VS. Zemke AC, et al. Among authors: pilewski jm. Int Forum Allergy Rhinol. 2024 May;14(5):928-938. doi: 10.1002/alr.23288. Epub 2023 Oct 14. Int Forum Allergy Rhinol. 2024. PMID: 37837613

9

Feasibility Testing of a Web-Based Reproductive Decision Support Tool for Cystic Fibrosis.

Kazmerski TM, Stransky OM, Wright CE, Albanowski M, Pilewski JM, Talabi MB, Callegari LS, Chang JC, Abebe KZ, Miller E, Deal A, O'Leary R, Borrero S. Kazmerski TM, et al. Among authors: pilewski jm. J Cyst Fibros. 2023 Oct 11:S1569-1993(23)00924-4. doi: 10.1016/j.jcf.2023.10.003. Online ahead of print. J Cyst Fibros. 2023. PMID: 37833123

10

Advancing the pipeline of cystic fibrosis clinical trials: a new roadmap with a global trial network perspective.

Mayer-Hamblett N, Clancy JP, Jain R, Donaldson SH, Fajac I, Goss CH, Polineni D, Ratjen F, Quon BS, Zemanick ET, Bell SC, Davies JC, Jain M, Konstan MW, Kerper NR, LaRosa T, Mall MA, McKone E, Pearson K, Pilewski JM, Quittell L, Rayment JH, Rowe SM, Taylor-Cousar JL, Retsch-Bogart G, Downey DG. Mayer-Hamblett N, et al. Among authors: pilewski jm. Lancet Respir Med. 2023 Oct;11(10):932-944. doi: 10.1016/S2213-2600(23)00297-7. Epub 2023 Sep 9. Lancet Respir Med. 2023. PMID: 37699421 Review.

11

Lung transplant recipients with telomere-mediated pulmonary fibrosis have increased risk for hematologic complications.

Hannan SJ, Iasella CJ, Sutton RM, Popescu ID, Koshy R, Burke R, Chen X, Zhang Y, Pilewski JM, Hage CA, Sanchez PG, Im A, Farah R, Alder JK, McDyer JF. Hannan SJ, et al. Among authors: pilewski jm. Am J Transplant. 2023 Oct;23(10):1590-1602. doi: 10.1016/j.ajt.2023.06.014. Epub 2023 Jun 29. Am J Transplant. 2023. PMID: 37392813 Free PMC article.

12

Role of Extracellular Vesicles in the Propagation of Lung Fibrosis in Systemic Sclerosis.

Mouawad JE, Sanderson M, Sharma S, Helke KL, Pilewski JM, Nadig SN, Feghali-Bostwick C. Mouawad JE, et al. Among authors: pilewski jm. Arthritis Rheumatol. 2023 Dec;75(12):2228-2239. doi: 10.1002/art.42638. Epub 2023 Sep 21. Arthritis Rheumatol. 2023. PMID: 37390364

13

Incidence of Acute Cellular Rejection After Granulocyte Colony-Stimulating Factor in Lung Transplant Recipients.

Fredrick SR, Iasella CJ, Sacha LM, Rivosecchi RM, Morrell MR, Sanchez PG, Pilewski JM, Snyder ME, McDyer JF, Moore CA. Fredrick SR, et al. Among authors: pilewski jm. J Pharm Pract. 2023 Jun 21:8971900231184308. doi: 10.1177/08971900231184308. Online ahead of print. J Pharm Pract. 2023. PMID: 37345293

14

Sequential redo-bilateral lung transplantation in recipient with prior heart-lung transplantation with tracheal anastomosis.

Coster JN, Chan EG, Furukawa M, Pilewski JM, Nguyen MHT, Sanchez PG. Coster JN, et al. Among authors: pilewski jm. JTCVS Tech. 2023 Apr 8;19:160-163. doi: 10.1016/j.xjtc.2023.03.017. eCollection 2023 Jun. JTCVS Tech. 2023. PMID: 37324355 Free PMC article. No abstract available.

15

Rabbit Antithymocyte Globulin for Treatment of Corticosteroid Refractory Acute Cellular Rejection After Lung Transplantation.

Rudzik KN, Moore CA, Sacha LM, Rivosecchi RM, Saul M, Pilewski JM, Kilaru SD, Snyder ME, McDyer JF, Iasella CJ. Rudzik KN, et al. Among authors: pilewski jm. Transplantation. 2023 Aug 1;107(8):1828-1834. doi: 10.1097/TP.0000000000004617. Epub 2023 Jul 20. Transplantation. 2023. PMID: 37143198

16

Position paper: Models of post-transplant care for individuals with cystic fibrosis.

McKone E, Ramos KJ, Chaparro C, Blatter J, Hachem R, Anstead M, Vlahos F, Thaxton A, Hempstead S, Daniels T, Murray M, Sole A, Vos R, Tallarico E, Faro A, Pilewski JM. McKone E, et al. Among authors: pilewski jm. J Cyst Fibros. 2023 May;22(3):374-380. doi: 10.1016/j.jcf.2023.02.011. Epub 2023 Mar 5. J Cyst Fibros. 2023. PMID: 36882349 Free article.

17

Phage therapy in a lung transplant recipient with cystic fibrosis infected with multidrug-resistant Burkholderia multivorans.

Haidar G, Chan BK, Cho ST, Hughes Kramer K, Nordstrom HR, Wallace NR, Stellfox ME, Holland M, Kline EG, Kozar JM, Kilaru SD, Pilewski JM, LiPuma JJ, Cooper VS, Shields RK, Van Tyne D. Haidar G, et al. Among authors: pilewski jm. Transpl Infect Dis. 2023 Apr;25(2):e14041. doi: 10.1111/tid.14041. Epub 2023 Mar 2. Transpl Infect Dis. 2023. PMID: 36864824 Free PMC article.

18

First Characterization of the Transcriptome of Lung Fibroblasts of SSc Patients and Healthy Donors of African Ancestry.

Renaud L, Waldrep KM, da Silveira WA, Pilewski JM, Feghali-Bostwick CA. Renaud L, et al. Among authors: pilewski jm. Int J Mol Sci. 2023 Feb 11;24(4):3645. doi: 10.3390/ijms24043645. Int J Mol Sci. 2023. PMID: 36835058 Free PMC article.

19

Nasal epithelial cell culture fluorescence recovery after photobleaching predicts cystic fibrosis therapeutic response.

Corcoran TE, Bertrand CA, Myerburg MM, Weiner DJ, Frizzell SA, Li A, Agostini B, Parker RS, Shapiro ME, Muthukrishnan A, Hages ND, Mulhern BP, Pilewski JM. Corcoran TE, et al. Among authors: pilewski jm. ERJ Open Res. 2022 Dec 12;8(4):00382-2022. doi: 10.1183/23120541.00382-2022. eCollection 2022 Oct. ERJ Open Res. 2022. PMID: 36655223 Free PMC article.

20

Ameliorating Fibrosis in Murine and Human Tissues with END55, an Endostatin-Derived Fusion Protein Made in Plants.

Mlakar L, Garrett SM, Watanabe T, Sanderson M, Nishimoto T, Heywood J, Helke KL, Pilewski JM, Herzog EL, Feghali-Bostwick C. Mlakar L, et al. Among authors: pilewski jm. Biomedicines. 2022 Nov 9;10(11):2861. doi: 10.3390/biomedicines10112861. Biomedicines. 2022. PMID: 36359382 Free PMC article.

21

Embedded Specialist Palliative Care in Cystic Fibrosis: Results of a Randomized Feasibility Clinical Trial.

Kavalieratos D, Lowers J, Moreines LT, Hoydich ZP, Arnold RM, Yabes JG, Richless C, Ikejiani DZ, Teuteberg W, Pilewski JM. Kavalieratos D, et al. Among authors: pilewski jm. J Palliat Med. 2023 Apr;26(4):489-496. doi: 10.1089/jpm.2022.0349. Epub 2022 Nov 9. J Palliat Med. 2023. PMID: 36350712 Free PMC article. Clinical Trial.

22

Update on Lung Transplantation for Cystic Fibrosis.

Pilewski JM. Pilewski JM. Clin Chest Med. 2022 Dec;43(4):821-840. doi: 10.1016/j.ccm.2022.07.002. Clin Chest Med. 2022. PMID: 36344083 Review.

23

Take on transplant: human-centered design of a patient education tool to facilitate informed discussions about lung transplant among people with cystic fibrosis.

Hartzler AL, Bartlett LE, Hobler MR, Reid N, Pryor JB, Kapnadak SG, Berry DL, Lober WB, Goss CH, Ramos KJ; Take on Transplant Study Group. Hartzler AL, et al. J Am Med Inform Assoc. 2022 Dec 13;30(1):26-37. doi: 10.1093/jamia/ocac176. J Am Med Inform Assoc. 2022. PMID: 36173364 Free PMC article.

24

Cross-Regulation of F-Box Protein FBXL2 with T-bet and TNF-α during Acute and Chronic Lung Allograft Rejection.

Das A, Wang X, Wei J, Hoji A, Coon TA, Popescu I, Brown M, Frizzell S, Iasella CJ, Noda K, Sembrat JC, Devonshire K, Hannan SJ, Snyder ME, Pilewski JM, Sanchez PG, Chandra D, Mallampalli RK, Alder JK, Chen BB, McDyer JF. Das A, et al. Among authors: pilewski jm. J Immunol. 2022 Nov 1;209(9):1788-1795. doi: 10.4049/jimmunol.2200245. Epub 2022 Sep 16. J Immunol. 2022. PMID: 36113884 Free PMC article.

25

Reduced Cathepsin L expression and secretion into the extracellular milieu contribute to lung fibrosis in systemic sclerosis.

Mouawad JE, Sharma S, Renaud L, Pilewski JM, Nadig SN, Feghali-Bostwick C. Mouawad JE, et al. Among authors: pilewski jm. Rheumatology (Oxford). 2023 Mar 1;62(3):1306-1316. doi: 10.1093/rheumatology/keac411. Rheumatology (Oxford). 2023. PMID: 35900152 Free PMC article.

26

Induction Strategies in Lung Transplantation: Alemtuzumab vs. Basiliximab a Single-Center Experience.

Furukawa M, Chan EG, Ryan JP, Hyzny EJ, Sacha LM, Coster JN, Pilewski JM, Lendermon EA, Kilaru SD, McDyer JF, Sanchez PG. Furukawa M, et al. Among authors: pilewski jm. Front Immunol. 2022 Jun 1;13:864545. doi: 10.3389/fimmu.2022.864545. eCollection 2022. Front Immunol. 2022. PMID: 35720296 Free PMC article.

27

Outpatient Pharmacologic Management of Lung Transplant Candidates on the Waiting List.

Sayah DM, Pilewski JM. Sayah DM, et al. Among authors: pilewski jm. Thorac Surg Clin. 2022 May;32(2):111-119. doi: 10.1016/j.thorsurg.2022.01.002. Thorac Surg Clin. 2022. PMID: 35512930 Review.

28

Use of elexacaftor/tezacaftor/ivacaftor among cystic fibrosis lung transplant recipients.

Ramos KJ, Guimbellot JS, Valapour M, Bartlett LE, Wai TH, Goss CH, Pilewski JM, Faro A, Diamond JM; CFLTC Study Group. Ramos KJ, et al. Among authors: pilewski jm. J Cyst Fibros. 2022 Sep;21(5):745-752. doi: 10.1016/j.jcf.2022.04.009. Epub 2022 Apr 23. J Cyst Fibros. 2022. PMID: 35474016 Free PMC article.

29

CD4⁺ T-Cell Dysfunction in Severe COVID-19 Disease Is Tumor Necrosis Factor-α/Tumor Necrosis Factor Receptor 1-Dependent.

Popescu I, Snyder ME, Iasella CJ, Hannan SJ, Koshy R, Burke R, Das A, Brown MJ, Lyons EJ, Lieber SC, Chen X, Sembrat JC, Bhatt P, Deng E, An X, Linstrum K, Kitsios G, Konstantinidis I, Saul M, Kass DJ, Alder JK, Chen BB, Lendermon EA, Kilaru S, Johnson B, Pilewski JM, Kiss JE, Wells AH, Morris A, McVerry BJ, McMahon DK, Triulzi DJ, Chen K, Sanchez PG, McDyer JF. Popescu I, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2022 Jun 15;205(12):1403-1418. doi: 10.1164/rccm.202111-2493OC. Am J Respir Crit Care Med. 2022. PMID: 35348444 Free PMC article.

30

Elexacaftor-Tezacaftor- Ivacaftor improves sinonasal outcomes in cystic fibrosis.

Stapleton AL, Kimple AJ, Goralski JL, Nouraie SM, Branstetter BF, Shaffer AD, Pilewski JM, Senior BA, Lee SE, Zemke AC. Stapleton AL, et al. Among authors: pilewski jm. J Cyst Fibros. 2022 Sep;21(5):792-799. doi: 10.1016/j.jcf.2022.03.002. Epub 2022 Mar 14. J Cyst Fibros. 2022. PMID: 35300931 Free PMC article.

31

Cystic fibrosis: candidate selection and impact of the cystic fibrosis transmembrane conductance regulator therapy.

Lehr CJ, Pilewski JM. Lehr CJ, et al. Among authors: pilewski jm. Curr Opin Organ Transplant. 2022 Jun 1;27(3):198-203. doi: 10.1097/MOT.0000000000000975. Curr Opin Organ Transplant. 2022. PMID: 35184094 Review.

32

Prospective Evaluation of Coronavirus Disease 2019 (COVID-19) Vaccine Responses Across a Broad Spectrum of Immunocompromising Conditions: the COVID-19 Vaccination in the Immunocompromised Study (COVICS).

Haidar G, Agha M, Bilderback A, Lukanski A, Linstrum K, Troyan R, Rothenberger S, McMahon DK, Crandall MD, Sobolewksi MD, Nathan Enick P, Jacobs JL, Collins K, Klamar-Blain C, Macatangay BJC, Parikh UM, Heaps A, Coughenour L, Schwartz MB, Dueker JM, Silveira FP, Keebler ME, Humar A, Luketich JD, Morrell MR, Pilewski JM, McDyer JF, Pappu B, Ferris RL, Marks SM, Mahon J, Mulvey K, Hariharan S, Updike GM, Brock L, Edwards R, Beigi RH, Kip PL, Wells A, Minnier T, Angus DC, Mellors JW. Haidar G, et al. Among authors: pilewski jm. Clin Infect Dis. 2022 Aug 24;75(1):e630-e644. doi: 10.1093/cid/ciac103. Clin Infect Dis. 2022. PMID: 35179197 Free PMC article.

33

Risk factors of bronchial dehiscence after primary lung transplantation.

Furukawa M, Chan EG, Morrell MR, Ryan JP, Rivosecchi RM, Iasella CJ, Lendermon EA, Pilewski JM, Sanchez PG. Furukawa M, et al. Among authors: pilewski jm. J Card Surg. 2022 Apr;37(4):950-957. doi: 10.1111/jocs.16291. Epub 2022 Feb 8. J Card Surg. 2022. PMID: 35133655

34

Body Mass Index Recovery after Lung Transplant for Cystic Fibrosis.

Pryor JB, Bradford MC, Jennerich AL, Wai TYH, Pilewski JM, Kapnadak SG, Aitken ML, Goss CH, Ramos KJ. Pryor JB, et al. Among authors: pilewski jm. Ann Am Thorac Soc. 2022 Jul;19(7):1130-1138. doi: 10.1513/AnnalsATS.202108-969OC. Ann Am Thorac Soc. 2022. PMID: 35044894 Free PMC article.

35

Lung transplantation for idiopathic pulmonary fibrosis enriches for individuals with telomere-mediated disease.

Alder JK, Sutton RM, Iasella CJ, Nouraie M, Koshy R, Hannan SJ, Chan EG, Chen X, Zhang Y, Brown M, Popescu I, Veatch M, Saul M, Berndt A, Methé BA, Morris A, Pilewski JM, Sanchez PG, Morrell MR, Shapiro SD, Lindell KO, Gibson KF, Kass DJ, McDyer JF. Alder JK, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2022 May;41(5):654-663. doi: 10.1016/j.healun.2021.11.008. Epub 2021 Nov 15. J Heart Lung Transplant. 2022. PMID: 34933798 Free PMC article.

36

Acidic Microenvironment Determines Antibiotic Susceptibility and Biofilm Formation of Pseudomonas aeruginosa.

Lin Q, Pilewski JM, Di YP. Lin Q, et al. Among authors: pilewski jm. Front Microbiol. 2021 Nov 19;12:747834. doi: 10.3389/fmicb.2021.747834. eCollection 2021. Front Microbiol. 2021. PMID: 34867864 Free PMC article.

37

HLA-C and KIR permutations influence chronic obstructive pulmonary disease risk.

Mkorombindo T, Tran-Nguyen TK, Yuan K, Zhang Y, Xue J, Criner GJ, Kim YI, Pilewski JM, Gaggar A, Cho MH, Sciurba FC, Duncan SR. Mkorombindo T, et al. Among authors: pilewski jm. JCI Insight. 2021 Oct 8;6(19):e150187. doi: 10.1172/jci.insight.150187. JCI Insight. 2021. PMID: 34464355 Free PMC article.

38

Rapid postmortem ventilation improves donor lung viability by extending the tolerable warm ischemic time after cardiac death in mice.

Yu J, Xu C, Lee JS, Alder JK, Wen Z, Wang G, Gil Silva AA, Sanchez PG, Pilewski JM, McDyer JF, Wang X. Yu J, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2021 Oct 1;321(4):L653-L662. doi: 10.1152/ajplung.00011.2021. Epub 2021 Jul 28. Am J Physiol Lung Cell Mol Physiol. 2021. PMID: 34318693 Free article.

39

CFTR Modulators to the Rescue of Individuals with Cystic Fibrosis and Advanced Lung Disease.

Myerburg M, Pilewski JM. Myerburg M, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2021 Jul 1;204(1):7-9. doi: 10.1164/rccm.202103-0674ED. Am J Respir Crit Care Med. 2021. PMID: 34161195 Free PMC article. No abstract available.

40

Cystic fibrosis foundation consensus statements for the care of cystic fibrosis lung transplant recipients.

Shah P, Lowery E, Chaparro C, Visner G, Hempstead SE, Abraham J, Bhakta Z, Carroll M, Christon L, Danziger-Isakov L, Diamond JM, Lease E, Leonard J, Litvin M, Poole R, Vlahos F, Werchan C, Murray MA, Tallarico E, Faro A, Pilewski JM, Hachem RR. Shah P, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2021 Jul;40(7):539-556. doi: 10.1016/j.healun.2021.04.011. Epub 2021 Apr 22. J Heart Lung Transplant. 2021. PMID: 34103223 Free article. Review.

41

Effect of lumacaftor-ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis: Results from the PROSPECT MCC sub-study.

Donaldson SH, Laube BL, Mogayzel P, Corcoran TE, Pilewski JM, Ceppe A, Wu J, Bhambhvani PG, Ratjen F, Sagel SD, Clancy JP, Rowe SM, Bennett WD. Donaldson SH, et al. Among authors: pilewski jm. J Cyst Fibros. 2022 Jan;21(1):143-145. doi: 10.1016/j.jcf.2021.05.004. Epub 2021 May 31. J Cyst Fibros. 2022. PMID: 34083123 Free PMC article.

42

Long-term safety and efficacy of tezacaftor-ivacaftor in individuals with cystic fibrosis aged 12 years or older who are homozygous or heterozygous for Phe508del CFTR (EXTEND): an open-label extension study.

Flume PA, Biner RF, Downey DG, Brown C, Jain M, Fischer R, De Boeck K, Sawicki GS, Chang P, Paz-Diaz H, Rubin JL, Yang Y, Hu X, Pasta DJ, Millar SJ, Campbell D, Wang X, Ahluwalia N, Owen CA, Wainwright CE; VX14-661-110 study group. Flume PA, et al. Lancet Respir Med. 2021 Jul;9(7):733-746. doi: 10.1016/S2213-2600(20)30510-5. Epub 2021 Feb 10. Lancet Respir Med. 2021. PMID: 33581080

43

Challenges in the use of highly effective modulator treatment for cystic fibrosis.

Ramos KJ, Pilewski JM, Taylor-Cousar JL. Ramos KJ, et al. Among authors: pilewski jm. J Cyst Fibros. 2021 May;20(3):381-387. doi: 10.1016/j.jcf.2021.01.007. Epub 2021 Jan 30. J Cyst Fibros. 2021. PMID: 33531206 Free PMC article. Review.

44

Type-1 immunity and endogenous immune regulators predominate in the airway transcriptome during chronic lung allograft dysfunction.

Iasella CJ, Hoji A, Popescu I, Wei J, Snyder ME, Zhang Y, Xu W, Iouchmanov V, Koshy R, Brown M, Fung M, Langelier C, Lendermon EA, Dugger D, Shah R, Lee J, Johnson B, Golden J, Leard LE, Ellen Kleinhenz M, Kilaru S, Hays SR, Singer JP, Sanchez PG, Morrell MR, Pilewski JM, Greenland JR, Chen K, McDyer JF. Iasella CJ, et al. Among authors: pilewski jm. Am J Transplant. 2021 Jun;21(6):2145-2160. doi: 10.1111/ajt.16360. Epub 2020 Nov 20. Am J Transplant. 2021. PMID: 33078555 Free PMC article.

45

Donor-specific antibody characteristics, including persistence and complement-binding capacity, increase risk for chronic lung allograft dysfunction.

Iasella CJ, Ensor CR, Marrari M, Mangiola M, Xu Q, Nolley E, Moore CA, Morrell MR, Pilewski JM, Sanchez PG, McDyer JF, Zeevi A. Iasella CJ, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2020 Dec;39(12):1417-1425. doi: 10.1016/j.healun.2020.09.003. Epub 2020 Sep 10. J Heart Lung Transplant. 2020. PMID: 32981841

46

Long-Term Ivacaftor in People Aged 6 Years and Older with Cystic Fibrosis with Ivacaftor-Responsive Mutations.

Pilewski JM, De Boeck K, Nick JA, Tian S, DeSouza C, Higgins M, Moss RB. Pilewski JM, et al. Pulm Ther. 2020 Dec;6(2):303-313. doi: 10.1007/s41030-020-00129-2. Epub 2020 Sep 23. Pulm Ther. 2020. PMID: 32965659 Free PMC article.

47

Incorporating patient and caregiver feedback into lung transplant referral guidelines for individuals with cystic fibrosis-Preliminary findings from a novel paradigm.

Smith PJ, Dunitz JM, Lucy A, Hempstead SE, Tallarico E, Faro A, Pilewski JM, Ramos KJ. Smith PJ, et al. Among authors: pilewski jm. Clin Transplant. 2020 Oct;34(10):e14038. doi: 10.1111/ctr.14038. Epub 2020 Aug 17. Clin Transplant. 2020. PMID: 32654238 Free PMC article.

48

Interleukin-22 Inhibits Respiratory Syncytial Virus Production by Blocking Virus-Mediated Subversion of Cellular Autophagy.

Das S, St Croix C, Good M, Chen J, Zhao J, Hu S, Ross M, Myerburg MM, Pilewski JM, Williams J, Wenzel SE, Kolls JK, Ray A, Ray P. Das S, et al. Among authors: pilewski jm. iScience. 2020 Jul 24;23(7):101256. doi: 10.1016/j.isci.2020.101256. Epub 2020 Jun 10. iScience. 2020. PMID: 32580124 Free PMC article.

49

Improved Prognosis in Cystic Fibrosis: Consideration for Intensive Care during the COVID-19 Pandemic.

Ramos KJ, Pilewski JM, Faro A, Marshall BC. Ramos KJ, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2020 Jun 1;201(11):1434-1435. doi: 10.1164/rccm.202004-0999LE. Am J Respir Crit Care Med. 2020. PMID: 32289235 Free PMC article. No abstract available.

50

Cystic Fibrosis Foundation consensus guidelines for the care of individuals with advanced cystic fibrosis lung disease.

Kapnadak SG, Dimango E, Hadjiliadis D, Hempstead SE, Tallarico E, Pilewski JM, Faro A, Albright J, Benden C, Blair S, Dellon EP, Gochenour D, Michelson P, Moshiree B, Neuringer I, Riedy C, Schindler T, Singer LG, Young D, Vignola L, Zukosky J, Simon RH. Kapnadak SG, et al. Among authors: pilewski jm. J Cyst Fibros. 2020 May;19(3):344-354. doi: 10.1016/j.jcf.2020.02.015. Epub 2020 Feb 27. J Cyst Fibros. 2020. PMID: 32115388 Free article.

51

Evaluation of humoral immunity in end-stage lung disease.

Traister RS, Coffey K, Xie M, Van Meerbeke S, Pilewski JM, Sorensen RU, Petrov AA. Traister RS, et al. Among authors: pilewski jm. J Allergy Clin Immunol Pract. 2020 Jun;8(6):2104-2106. doi: 10.1016/j.jaip.2020.01.063. Epub 2020 Feb 26. J Allergy Clin Immunol Pract. 2020. PMID: 32112921 No abstract available.

52

Underweight Patients With Cystic Fibrosis Have Acceptable Survival Following Lung Transplantation: A United Network for Organ Sharing Registry Study.

Ramos KJ, Kapnadak SG, Bradford MC, Somayaji R, Morrell ED, Pilewski JM, Lease ED, Mulligan MS, Aitken ML, Gries CJ, Goss CH. Ramos KJ, et al. Among authors: pilewski jm. Chest. 2020 Apr;157(4):898-906. doi: 10.1016/j.chest.2019.11.043. Epub 2020 Jan 17. Chest. 2020. PMID: 31958441 Free PMC article.

53

Organ Transplantation for Cystic Fibrosis.

Morrell MR, Kiel SC, Pilewski JM. Morrell MR, et al. Among authors: pilewski jm. Semin Respir Crit Care Med. 2019 Dec;40(6):842-856. doi: 10.1055/s-0039-3399554. Epub 2019 Dec 30. Semin Respir Crit Care Med. 2019. PMID: 31887769 Review.

54

Idiopathic pulmonary fibrosis lung transplant recipients are at increased risk for EBV-associated posttransplant lymphoproliferative disorder and worse survival.

Iasella CJ, Winters SA, Kois A, Cho J, Hannan SJ, Koshy R, Moore CA, Ensor CR, Lendermon EA, Morrell MR, Pilewski JM, Sanchez PG, Kass DJ, Alder JK, Nouraie SM, McDyer JF. Iasella CJ, et al. Among authors: pilewski jm. Am J Transplant. 2020 May;20(5):1439-1446. doi: 10.1111/ajt.15756. Epub 2020 Jan 22. Am J Transplant. 2020. PMID: 31874120 Free PMC article.

55

Prevalence of unmet palliative care needs in adults with cystic fibrosis.

Trandel ET, Pilewski JM, Dellon EP, Jeong K, Yabes JG, Moreines LT, Arnold RM, Hoydich ZP, Kavalieratos D. Trandel ET, et al. Among authors: pilewski jm. J Cyst Fibros. 2020 May;19(3):394-401. doi: 10.1016/j.jcf.2019.11.010. Epub 2019 Dec 18. J Cyst Fibros. 2020. PMID: 31862306 Free PMC article.

56

Routine deep vein thrombosis screening after lung transplantation: Incidence and risk factors.

Jorge A, Sanchez PG, Hayanga JWA, Pilewski JM, Morrell M, Tuft M, Ryan J, D'Cunha J. Jorge A, et al. Among authors: pilewski jm. J Thorac Cardiovasc Surg. 2020 Mar;159(3):1142-1150. doi: 10.1016/j.jtcvs.2019.08.030. Epub 2019 Sep 25. J Thorac Cardiovasc Surg. 2020. PMID: 31839224 Free article.

57

Insulin-like growth factor (IGF)-II- mediated fibrosis in pathogenic lung conditions.

Garrett SM, Hsu E, Thomas JM, Pilewski JM, Feghali-Bostwick C. Garrett SM, et al. Among authors: pilewski jm. PLoS One. 2019 Nov 25;14(11):e0225422. doi: 10.1371/journal.pone.0225422. eCollection 2019. PLoS One. 2019. PMID: 31765403 Free PMC article.

58

Targeting the IL-22/IL-22BP axis enhances tight junctions and reduces inflammation during influenza infection.

Hebert KD, Mclaughlin N, Galeas-Pena M, Zhang Z, Eddens T, Govero A, Pilewski JM, Kolls JK, Pociask DA. Hebert KD, et al. Among authors: pilewski jm. Mucosal Immunol. 2020 Jan;13(1):64-74. doi: 10.1038/s41385-019-0206-9. Epub 2019 Oct 9. Mucosal Immunol. 2020. PMID: 31597930 Free PMC article.

59

Insulin-like growth factor binding protein-4 exerts antifibrotic activity by reducing levels of connective tissue growth factor and the C-X-C chemokine receptor 4.

Su Y, Nishimoto T, Hoffman S, Nguyen XX, Pilewski JM, Feghali-Bostwick C. Su Y, et al. Among authors: pilewski jm. FASEB Bioadv. 2019 Mar;1(3):167-179. doi: 10.1096/fba.2018-00015. Epub 2018 Nov 14. FASEB Bioadv. 2019. PMID: 31482149 Free PMC article.

60

Call for Changes in Lung Allocation to Reduce Transplant Wait-List Mortality for Cystic Fibrosis.

Nolley EP, Pilewski JM. Nolley EP, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2019 Oct 15;200(8):956-957. doi: 10.1164/rccm.201907-1385ED. Am J Respir Crit Care Med. 2019. PMID: 31356757 Free PMC article. No abstract available.

61

Impact of a Mobile Health Intervention on Long-term Nonadherence After Lung Transplantation: Follow-up After a Randomized Controlled Trial.

Geramita EM, DeVito Dabbs AJ, DiMartini AF, Pilewski JM, Switzer GE, Posluszny DM, Myaskovsky L, Dew MA. Geramita EM, et al. Among authors: pilewski jm. Transplantation. 2020 Mar;104(3):640-651. doi: 10.1097/TP.0000000000002872. Transplantation. 2020. PMID: 31335759 Free PMC article. Clinical Trial.

62

Outcomes in Lung Transplant Recipients With Mycobacterium abscessus Infection: A 15-Year Experience From a Large Tertiary Care Center.

Hamad Y, Pilewski JM, Morrell M, D'Cunha J, Kwak EJ. Hamad Y, et al. Among authors: pilewski jm. Transplant Proc. 2019 Jul-Aug;51(6):2035-2042. doi: 10.1016/j.transproceed.2019.02.028. Epub 2019 Jul 11. Transplant Proc. 2019. PMID: 31303416

63

Symptom Burden and Unmet Existential Needs in Adults With Cystic Fibrosis.

Trandel ET, Pilewski JM, Dellon EP, Moreines LT, Yabes JG, Jeong K, Arnold RM, Kavalieratos D. Trandel ET, et al. Among authors: pilewski jm. West J Nurs Res. 2019 Oct;41(10):1448-1464. doi: 10.1177/0193945919852585. Epub 2019 Jul 3. West J Nurs Res. 2019. PMID: 31267835

64

Successful lung transplantation from a hepatitis C RNA-positive donor to a hepatitis C treatment-experienced recipient with cystic fibrosis.

Harano T, Haidar G, Schaheen L, Morrell MR, Pilewski JM, D'Cunha J. Harano T, et al. Among authors: pilewski jm. J Thorac Cardiovasc Surg. 2019 Oct;158(4):e155-e157. doi: 10.1016/j.jtcvs.2019.05.010. Epub 2019 May 24. J Thorac Cardiovasc Surg. 2019. PMID: 31229293 Free article. No abstract available.

65

Clinical predictors of cystic fibrosis chronic rhinosinusitis severity.

Zemke AC, Nouraie SM, Moore J, Gaston JR, Rowan NR, Pilewski JM, Bomberger JM, Lee SE. Zemke AC, et al. Among authors: pilewski jm. Int Forum Allergy Rhinol. 2019 Jul;9(7):759-765. doi: 10.1002/alr.22332. Epub 2019 Jun 4. Int Forum Allergy Rhinol. 2019. PMID: 31162888 Free PMC article.

66

Successful Lung Transplantation in a Patient with Chronic Granulomatous Disease.

Xie M, Lee J, Crespo M, Fajt ML, Shigemura N, Pilewski JM, Petrov AA. Xie M, et al. Among authors: pilewski jm. J Clin Immunol. 2019 May;39(4):347-349. doi: 10.1007/s10875-019-00623-6. Epub 2019 Apr 23. J Clin Immunol. 2019. PMID: 31016643 No abstract available.

67

Transcriptomic Responses to Ivacaftor and Prediction of Ivacaftor Clinical Responsiveness.

Sun T, Sun Z, Jiang Y, Ferguson AA, Pilewski JM, Kolls JK, Chen W, Chen K. Sun T, et al. Among authors: pilewski jm. Am J Respir Cell Mol Biol. 2019 Nov;61(5):643-652. doi: 10.1165/rcmb.2019-0032OC. Am J Respir Cell Mol Biol. 2019. PMID: 30995102 Free PMC article.

68

Multiprobe Nuclear Imaging of the Cystic Fibrosis Lung as a Biomarker of Therapeutic Effect.

Corcoran TE, Huber AS, Myerburg MM, Weiner DJ, Locke LW, Lacy RT, Weber L, Czachowski MR, Johnston DJ, Muthukrishnan A, Lennox AT, Pilewski JM. Corcoran TE, et al. Among authors: pilewski jm. J Aerosol Med Pulm Drug Deliv. 2019 Aug;32(4):242-249. doi: 10.1089/jamp.2018.1491. Epub 2019 Apr 10. J Aerosol Med Pulm Drug Deliv. 2019. PMID: 30969149 Free PMC article.

69

Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines.

Ramos KJ, Smith PJ, McKone EF, Pilewski JM, Lucy A, Hempstead SE, Tallarico E, Faro A, Rosenbluth DB, Gray AL, Dunitz JM; CF Lung Transplant Referral Guidelines Committee. Ramos KJ, et al. Among authors: pilewski jm. J Cyst Fibros. 2019 May;18(3):321-333. doi: 10.1016/j.jcf.2019.03.002. Epub 2019 Mar 27. J Cyst Fibros. 2019. PMID: 30926322 Free PMC article. Review.

70

Closing the Loop: Engaging Leaders and Front-Line Physicians to Promote Physician Wellness.

Barbash IJ, Pilewski JM, McVerry BJ. Barbash IJ, et al. Among authors: pilewski jm. Ann Am Thorac Soc. 2019 Aug;16(8):970-973. doi: 10.1513/AnnalsATS.201812-866PS. Ann Am Thorac Soc. 2019. PMID: 30874450 No abstract available.

71

Effect of ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis patients with G551D-CFTR.

Donaldson SH, Laube BL, Corcoran TE, Bhambhvani P, Zeman K, Ceppe A, Zeitlin PL, Mogayzel PJ Jr, Boyle M, Locke LW, Myerburg MM, Pilewski JM, Flanagan B, Rowe SM, Bennett WD. Donaldson SH, et al. Among authors: pilewski jm. JCI Insight. 2018 Dec 20;3(24):e122695. doi: 10.1172/jci.insight.122695. JCI Insight. 2018. PMID: 30568035 Free PMC article.

72

Intracellular Heat Shock Protein 70 Deficiency in Pulmonary Fibrosis.

Sellares J, Veraldi KL, Thiel KJ, Cárdenes N, Alvarez D, Schneider F, Pilewski JM, Rojas M, Feghali-Bostwick CA. Sellares J, et al. Among authors: pilewski jm. Am J Respir Cell Mol Biol. 2019 Jun;60(6):629-636. doi: 10.1165/rcmb.2017-0268OC. Am J Respir Cell Mol Biol. 2019. PMID: 30543447 Free PMC article.

73

Detrimental Association of Hypogammaglobulinemia With Chronic Lung Allograft Dysfunction and Death Is Not Mitigated by On-Demand Immunoglobulin G Replacement After Lung Transplantation.

Lichvar AB, Ensor CR, Zeevi A, Morrell MR, Pilewski JM, Hayanga JWA, D'Cunha J, McDyer JF, Petrov AA. Lichvar AB, et al. Among authors: pilewski jm. Prog Transplant. 2018 Dec 11:1526924818817028. doi: 10.1177/1526924818817028. Online ahead of print. Prog Transplant. 2018. PMID: 30537897

74

A Prospective Observational Study of Hypogammaglobulinemia in the First Year After Lung Transplantation.

Petrov AA, Traister RS, Crespo MM, Silveira FP, Xie M, Coffey K, Ensor CR, Landsittel D, Pilewski JM. Petrov AA, et al. Among authors: pilewski jm. Transplant Direct. 2018 Jul 12;4(8):e372. doi: 10.1097/TXD.0000000000000811. eCollection 2018 Aug. Transplant Direct. 2018. PMID: 30255132 Free PMC article.

75

Pseudomonas aeruginosa utilizes host polyunsaturated phosphatidylethanolamines to trigger theft-ferroptosis in bronchial epithelium.

Dar HH, Tyurina YY, Mikulska-Ruminska K, Shrivastava I, Ting HC, Tyurin VA, Krieger J, St Croix CM, Watkins S, Bayir E, Mao G, Armbruster CR, Kapralov A, Wang H, Parsek MR, Anthonymuthu TS, Ogunsola AF, Flitter BA, Freedman CJ, Gaston JR, Holman TR, Pilewski JM, Greenberger JS, Mallampalli RK, Doi Y, Lee JS, Bahar I, Bomberger JM, Bayır H, Kagan VE. Dar HH, et al. Among authors: pilewski jm. J Clin Invest. 2018 Oct 1;128(10):4639-4653. doi: 10.1172/JCI99490. Epub 2018 Sep 10. J Clin Invest. 2018. PMID: 30198910 Free PMC article.

76

Staphylococcus aureus Biofilm Growth on Cystic Fibrosis Airway Epithelial Cells Is Enhanced during Respiratory Syncytial Virus Coinfection.

Kiedrowski MR, Gaston JR, Kocak BR, Coburn SL, Lee S, Pilewski JM, Myerburg MM, Bomberger JM. Kiedrowski MR, et al. Among authors: pilewski jm. mSphere. 2018 Aug 15;3(4):e00341-18. doi: 10.1128/mSphere.00341-18. mSphere. 2018. PMID: 30111629 Free PMC article.

77

Impaired Cytomegalovirus Immunity in Idiopathic Pulmonary Fibrosis Lung Transplant Recipients with Short Telomeres.

Popescu I, Mannem H, Winters SA, Hoji A, Silveira F, McNally E, Pipeling MR, Lendermon EA, Morrell MR, Pilewski JM, Hanumanthu VS, Zhang Y, Gulati S, Shah PD, Iasella CJ, Ensor CR, Armanios M, McDyer JF. Popescu I, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2019 Feb 1;199(3):362-376. doi: 10.1164/rccm.201805-0825OC. Am J Respir Crit Care Med. 2019. PMID: 30088779 Free PMC article.

78

Optical or Transbronchial Biopsy to Diagnose Acute Cellular Rejection.

Petrov AA, Pilewski JM. Petrov AA, et al. Among authors: pilewski jm. Transplantation. 2019 Feb;103(2):235-236. doi: 10.1097/TP.0000000000002307. Transplantation. 2019. PMID: 29847503 No abstract available.

79

ATP12A promotes mucus dysfunction during Type 2 airway inflammation.

Lennox AT, Coburn SL, Leech JA, Heidrich EM, Kleyman TR, Wenzel SE, Pilewski JM, Corcoran TE, Myerburg MM. Lennox AT, et al. Among authors: pilewski jm. Sci Rep. 2018 Feb 1;8(1):2109. doi: 10.1038/s41598-018-20444-8. Sci Rep. 2018. PMID: 29391451 Free PMC article.

80

Sexual and reproductive health care utilization and preferences reported by young women with cystic fibrosis.

Kazmerski TM, Sawicki GS, Miller E, Jones KA, Abebe KZ, Tuchman LK, Ladores S, Rubenstein RC, Sagel SD, Weiner DJ, Pilewski JM, Orenstein DM, Borrero S. Kazmerski TM, et al. Among authors: pilewski jm. J Cyst Fibros. 2018 Jan;17(1):64-70. doi: 10.1016/j.jcf.2017.08.009. Epub 2017 Sep 1. J Cyst Fibros. 2018. PMID: 28866451 Free article.

81

Microbiome in lung explants of idiopathic pulmonary fibrosis: a case-control study in patients with end-stage fibrosis.

Kitsios GD, Rojas M, Kass DJ, Fitch A, Sembrat JC, Qin S, Veraldi KL, Gibson KF, Lindell K, Pilewski JM, Methe B, Li K, McDyer J, McVerry BJ, Morris A. Kitsios GD, et al. Among authors: pilewski jm. Thorax. 2018 May;73(5):481-484. doi: 10.1136/thoraxjnl-2017-210537. Epub 2017 Aug 11. Thorax. 2018. PMID: 28802277 Free PMC article.

82

Sexual and reproductive health behaviors and experiences reported by young women with cystic fibrosis.

Kazmerski TM, Sawicki GS, Miller E, Jones KA, Abebe KZ, Tuchman LK, Ladores S, Rubenstein RC, Sagel SD, Weiner DJ, Pilewski JM, Orenstein DM, Borrero S. Kazmerski TM, et al. Among authors: pilewski jm. J Cyst Fibros. 2018 Jan;17(1):57-63. doi: 10.1016/j.jcf.2017.07.017. Epub 2017 Aug 1. J Cyst Fibros. 2018. PMID: 28774749 Free article.

83

Overnight delivery of hypertonic saline by nasal cannula aerosol for cystic fibrosis.

Corcoran TE, Godovchik JE, Donn KH, Busick DR, Goralski J, Locke LW, Markovetz MR, Myerburg MM, Muthukrishnan A, Weber L, Lacy RT, Pilewski JM. Corcoran TE, et al. Among authors: pilewski jm. Pediatr Pulmonol. 2017 Sep;52(9):1142-1149. doi: 10.1002/ppul.23749. Epub 2017 Jul 24. Pediatr Pulmonol. 2017. PMID: 28737262 Free PMC article. Clinical Trial.

84

The CFTR trafficking mutation F508del inhibits the constitutive activity of SLC26A9.

Bertrand CA, Mitra S, Mishra SK, Wang X, Zhao Y, Pilewski JM, Madden DR, Frizzell RA. Bertrand CA, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2017 Jun 1;312(6):L912-L925. doi: 10.1152/ajplung.00178.2016. Epub 2017 Mar 30. Am J Physiol Lung Cell Mol Physiol. 2017. PMID: 28360110 Free PMC article.

85

Effect of aerosolized antipseudomonals on Pseudomonas positivity and bronchiolitis obliterans syndrome after lung transplantation.

Moore CA, Pilewski JM, Venkataramanan R, Robinson KM, Morrell MR, Wisniewski SR, Zeevi A, McDyer JF, Ensor CR. Moore CA, et al. Among authors: pilewski jm. Transpl Infect Dis. 2017 Jun;19(3). doi: 10.1111/tid.12688. Epub 2017 Apr 17. Transpl Infect Dis. 2017. PMID: 28273385

86

Proteasome Inhibitor Carfilzomib-Based Therapy for Antibody-Mediated Rejection of the Pulmonary Allograft: Use and Short-Term Findings.

Ensor CR, Yousem SA, Marrari M, Morrell MR, Mangiola M, Pilewski JM, D'Cunha J, Wisniewski SR, Venkataramanan R, Zeevi A, McDyer JF. Ensor CR, et al. Among authors: pilewski jm. Am J Transplant. 2017 May;17(5):1380-1388. doi: 10.1111/ajt.14222. Epub 2017 Mar 9. Am J Transplant. 2017. PMID: 28173620 Free article.

87

Provider Attitudes and Practices toward Sexual and Reproductive Health Care for Young Women with Cystic Fibrosis.

Kazmerski TM, Borrero S, Sawicki GS, Abebe KZ, Jones KA, Tuchman LK, Weiner DJ, Pilewski JM, Orenstein DM, Miller E. Kazmerski TM, et al. Among authors: pilewski jm. J Pediatr Adolesc Gynecol. 2017 Oct;30(5):546-552. doi: 10.1016/j.jpag.2017.01.009. Epub 2017 Feb 3. J Pediatr Adolesc Gynecol. 2017. PMID: 28163120

88

Rescue alemtuzumab for refractory acute cellular rejection and bronchiolitis obliterans syndrome after lung transplantation.

Ensor CR, Rihtarchik LC, Morrell MR, Hayanga JW, Lichvar AB, Pilewski JM, Wisniewski S, Johnson BA, D'Cunha J, Zeevi A, McDyer JF. Ensor CR, et al. Among authors: pilewski jm. Clin Transplant. 2017 Apr;31(4). doi: 10.1111/ctr.12899. Epub 2017 Feb 22. Clin Transplant. 2017. PMID: 28008661

89

Long-Term Follow-up of a Randomized Controlled Trial Evaluating a Mobile Health Intervention for Self-Management in Lung Transplant Recipients.

Rosenberger EM, DeVito Dabbs AJ, DiMartini AF, Landsittel DP, Pilewski JM, Dew MA. Rosenberger EM, et al. Among authors: pilewski jm. Am J Transplant. 2017 May;17(5):1286-1293. doi: 10.1111/ajt.14062. Epub 2016 Oct 31. Am J Transplant. 2017. PMID: 27664940 Free PMC article. Clinical Trial.

90

Pattern and Predictors of Hospital Readmission During the First Year After Lung Transplantation.

Alrawashdeh M, Zomak R, Dew MA, Sereika S, Song MK, Pilewski JM, DeVito Dabbs A. Alrawashdeh M, et al. Among authors: pilewski jm. Am J Transplant. 2017 May;17(5):1325-1333. doi: 10.1111/ajt.14064. Epub 2016 Oct 27. Am J Transplant. 2017. PMID: 27676226 Free PMC article. Clinical Trial.

91

Antiinflammatory effects of bromodomain and extraterminal domain inhibition in cystic fibrosis lung inflammation.

Chen K, Campfield BT, Wenzel SE, McAleer JP, Kreindler JL, Kurland G, Gopal R, Wang T, Chen W, Eddens T, Quinn KM, Myerburg MM, Horne WT, Lora JM, Albrecht BK, Pilewski JM, Kolls JK. Chen K, et al. Among authors: pilewski jm. JCI Insight. 2016 Jul 21;1(11):e87168. doi: 10.1172/jci.insight.87168. JCI Insight. 2016. PMID: 27517095 Free PMC article.

92

Provider and Patient Attitudes Regarding Sexual Health in Young Women With Cystic Fibrosis.

Kazmerski TM, Borrero S, Tuchman LK, Weiner DJ, Pilewski JM, Orenstein DM, Miller E. Kazmerski TM, et al. Among authors: pilewski jm. Pediatrics. 2016 Jun;137(6):e20154452. doi: 10.1542/peds.2015-4452. Epub 2016 May 2. Pediatrics. 2016. PMID: 27244858

93

Engineered cationic antimicrobial peptide (eCAP) prevents Pseudomonas aeruginosa biofilm growth on airway epithelial cells.

Lashua LP, Melvin JA, Deslouches B, Pilewski JM, Montelaro RC, Bomberger JM. Lashua LP, et al. Among authors: pilewski jm. J Antimicrob Chemother. 2016 Aug;71(8):2200-7. doi: 10.1093/jac/dkw143. Epub 2016 May 26. J Antimicrob Chemother. 2016. PMID: 27231279 Free PMC article.

94

Vitamin D supplementation decreases Aspergillus fumigatus specific Th2 responses in CF patients with aspergillus sensitization: a phase one open-label study.

Nguyen NL, Pilewski JM, Celedón JC, Mandalapu S, Blanchard ML, DeRicco A, Hartigan E, Alcorn JF, Kolls JK. Nguyen NL, et al. Among authors: pilewski jm. Asthma Res Pract. 2015;1:3. doi: 10.1186/s40733-015-0003-5. Epub 2015 Jun 4. Asthma Res Pract. 2015. PMID: 27011794 Free PMC article.

95

Pseudomonas infection and mucociliary and absorptive clearance in the cystic fibrosis lung.

Locke LW, Myerburg MM, Weiner DJ, Markovetz MR, Parker RS, Muthukrishnan A, Weber L, Czachowski MR, Lacy RT, Pilewski JM, Corcoran TE. Locke LW, et al. Among authors: pilewski jm. Eur Respir J. 2016 May;47(5):1392-401. doi: 10.1183/13993003.01880-2015. Epub 2016 Mar 23. Eur Respir J. 2016. PMID: 27009167 Free PMC article.

96

Lung Transplantation for Cystic Fibrosis.

Morrell MR, Pilewski JM. Morrell MR, et al. Among authors: pilewski jm. Clin Chest Med. 2016 Mar;37(1):127-38. doi: 10.1016/j.ccm.2015.11.008. Clin Chest Med. 2016. PMID: 26857774 Review.

97

Surgical Strategy for Lung Transplantation in Adults With Small Chests: Lobar Transplant Versus a Pediatric Donor.

Mahesh B, Bhama JK, Odell DD, Hayanga AJ, Bermudez CA, Morrell MR, Crespo MM, Pilewski JM, Johnson BA, Luketich JD, D'Cunha J, Shigemura N. Mahesh B, et al. Among authors: pilewski jm. Transplantation. 2016 Dec;100(12):2693-2698. doi: 10.1097/TP.0000000000001048. Transplantation. 2016. PMID: 26760568

98

A Randomized Controlled Trial of a Mobile Health Intervention to Promote Self-Management After Lung Transplantation.

DeVito Dabbs A, Song MK, Myers BA, Li R, Hawkins RP, Pilewski JM, Bermudez CA, Aubrecht J, Begey A, Connolly M, Alrawashdeh M, Dew MA. DeVito Dabbs A, et al. Among authors: pilewski jm. Am J Transplant. 2016 Jul;16(7):2172-80. doi: 10.1111/ajt.13701. Epub 2016 Mar 14. Am J Transplant. 2016. PMID: 26729617 Free PMC article. Clinical Trial.

99

Looking Beyond Respiratory Cultures: Microbiome-Cytokine Signatures of Bacterial Pneumonia and Tracheobronchitis in Lung Transplant Recipients.

Shankar J, Nguyen MH, Crespo MM, Kwak EJ, Lucas SK, McHugh KJ, Mounaud S, Alcorn JF, Pilewski JM, Shigemura N, Kolls JK, Nierman WC, Clancy CJ. Shankar J, et al. Among authors: pilewski jm. Am J Transplant. 2016 Jun;16(6):1766-78. doi: 10.1111/ajt.13676. Epub 2016 Feb 10. Am J Transplant. 2016. PMID: 26693965 Free article.

100

Lung Transplant in Patients with Scleroderma Compared with Pulmonary Fibrosis. Short- and Long-Term Outcomes.

Crespo MM, Bermudez CA, Dew MA, Johnson BA, George MP, Bhama J, Morrell M, D'Cunha J, Shigemura N, Richards TJ, Pilewski JM. Crespo MM, et al. Among authors: pilewski jm. Ann Am Thorac Soc. 2016 Jun;13(6):784-92. doi: 10.1513/AnnalsATS.201503-177OC. Ann Am Thorac Soc. 2016. PMID: 26669584

101

Prolonged Use of the Hemolung Respiratory Assist System as a Bridge to Redo Lung Transplantation.

Bermudez CA, Zaldonis D, Fan MH, Pilewski JM, Crespo MM. Bermudez CA, et al. Among authors: pilewski jm. Ann Thorac Surg. 2015 Dec;100(6):2330-3. doi: 10.1016/j.athoracsur.2015.02.104. Ann Thorac Surg. 2015. PMID: 26652524

102

Cystic fibrosis program directors' attitudes toward sexual and reproductive health in young women with CF.

Kazmerski TM, Tuchman LK, Borrero S, Weiner D, Pilewski JM, Orenstein DM, Miller E. Kazmerski TM, et al. Among authors: pilewski jm. Pediatr Pulmonol. 2016 Jan;51(1):22-7. doi: 10.1002/ppul.23321. Epub 2015 Nov 9. Pediatr Pulmonol. 2016. PMID: 26551521

103

Psychiatric Predictors of Long-term Transplant-Related Outcomes in Lung Transplant Recipients.

Rosenberger EM, DiMartini AF, DeVito Dabbs AJ, Bermudez CA, Pilewski JM, Toyoda Y, Dew MA. Rosenberger EM, et al. Among authors: pilewski jm. Transplantation. 2016 Jan;100(1):239-47. doi: 10.1097/TP.0000000000000824. Transplantation. 2016. PMID: 26177087 Free PMC article.

104

Simkania negevensis and acute cellular rejection in lung transplant recipients.

Jamal AJ, Resende MR, Prochnow T, McGilvray I, Pilewski JM, Crespo MM, Singer LG, McCurry KR, Kolls JK, Keshavjee S, Liles WC, Husain S. Jamal AJ, et al. Among authors: pilewski jm. Clin Transplant. 2015 Aug;29(8):705-11. doi: 10.1111/ctr.12571. Epub 2015 Jul 20. Clin Transplant. 2015. PMID: 26009941

105

Intracellular Na+ regulates epithelial Na+ channel maturation.

Heidrich E, Carattino MD, Hughey RP, Pilewski JM, Kleyman TR, Myerburg MM. Heidrich E, et al. Among authors: pilewski jm. J Biol Chem. 2015 May 1;290(18):11569-77. doi: 10.1074/jbc.M115.640763. Epub 2015 Mar 12. J Biol Chem. 2015. PMID: 25767115 Free PMC article.

106

Effect of ivacaftor in patients with advanced cystic fibrosis and a G551D-CFTR mutation: Safety and efficacy in an expanded access program in the United States.

Taylor-Cousar J, Niknian M, Gilmartin G, Pilewski JM; VX11-770-901 investigators. Taylor-Cousar J, et al. Among authors: pilewski jm. J Cyst Fibros. 2016 Jan;15(1):116-22. doi: 10.1016/j.jcf.2015.01.008. Epub 2015 Feb 11. J Cyst Fibros. 2016. PMID: 25682022 Free article. Clinical Trial.

107

De novo donor-specific HLA antibodies are associated with early and high-grade bronchiolitis obliterans syndrome and death after lung transplantation.

Morrell MR, Pilewski JM, Gries CJ, Pipeling MR, Crespo MM, Ensor CR, Yousem SA, D'Cunha J, Shigemura N, Bermudez CA, McDyer JF, Zeevi A. Morrell MR, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2014 Dec;33(12):1288-94. doi: 10.1016/j.healun.2014.07.018. Epub 2014 Aug 23. J Heart Lung Transplant. 2014. PMID: 25443870

108

Outcomes of intraoperative venoarterial extracorporeal membrane oxygenation versus cardiopulmonary bypass during lung transplantation.

Bermudez CA, Shiose A, Esper SA, Shigemura N, D'Cunha J, Bhama JK, Richards TJ, Arlia P, Crespo MM, Pilewski JM. Bermudez CA, et al. Among authors: pilewski jm. Ann Thorac Surg. 2014 Dec;98(6):1936-42; discussion 1942-3. doi: 10.1016/j.athoracsur.2014.06.072. Epub 2014 Oct 22. Ann Thorac Surg. 2014. PMID: 25443002

109

A physiologically-motivated compartment-based model of the effect of inhaled hypertonic saline on mucociliary clearance and liquid transport in cystic fibrosis.

Markovetz MR, Corcoran TE, Locke LW, Myerburg MM, Pilewski JM, Parker RS. Markovetz MR, et al. Among authors: pilewski jm. PLoS One. 2014 Nov 10;9(11):e111972. doi: 10.1371/journal.pone.0111972. eCollection 2014. PLoS One. 2014. PMID: 25383714 Free PMC article.

110

Nitrite modulates bacterial antibiotic susceptibility and biofilm formation in association with airway epithelial cells.

Zemke AC, Shiva S, Burns JL, Moskowitz SM, Pilewski JM, Gladwin MT, Bomberger JM. Zemke AC, et al. Among authors: pilewski jm. Free Radic Biol Med. 2014 Dec;77:307-16. doi: 10.1016/j.freeradbiomed.2014.08.011. Epub 2014 Sep 16. Free Radic Biol Med. 2014. PMID: 25229185 Free PMC article.

111

Autoreactivity to glucose regulated protein 78 links emphysema and osteoporosis in smokers.

Bon J, Kahloon R, Zhang Y, Xue J, Fuhrman CR, Tan J, Burger M, Kass DJ, Csizmadia E, Otterbein L, Chandra D, Bhargava A, Pilewski JM, Roodman GD, Sciurba FC, Duncan SR. Bon J, et al. Among authors: pilewski jm. PLoS One. 2014 Sep 12;9(9):e105066. doi: 10.1371/journal.pone.0105066. eCollection 2014. PLoS One. 2014. PMID: 25216103 Free PMC article.

112

Palliative care and location of death in decedents with idiopathic pulmonary fibrosis.

Lindell KO, Liang Z, Hoffman LA, Rosenzweig MQ, Saul MI, Pilewski JM, Gibson KF, Kaminski N. Lindell KO, et al. Among authors: pilewski jm. Chest. 2015 Feb;147(2):423-429. doi: 10.1378/chest.14-1127. Chest. 2015. PMID: 25187973 Free PMC article.

113

Cystic fibrosis: recent successes present new challenges.

Pilewski JM, Taichman DB. Pilewski JM, et al. Ann Intern Med. 2014 Aug 19;161(4):298-9. doi: 10.7326/M14-1534. Ann Intern Med. 2014. PMID: 25133363 No abstract available.

114

Highly effective cystic fibrosis clinical research teams: critical success factors.

Retsch-Bogart GZ, Van Dalfsen JM, Marshall BC, George C, Pilewski JM, Nelson EC, Goss CH, Ramsey BW. Retsch-Bogart GZ, et al. Among authors: pilewski jm. J Gen Intern Med. 2014 Aug;29 Suppl 3(Suppl 3):S714-23. doi: 10.1007/s11606-014-2896-8. J Gen Intern Med. 2014. PMID: 25029977 Free PMC article.

115

First successful lung transplantation for sickle cell disease with severe pulmonary arterial hypertension and pulmonary veno-occlusive disease.

George MP, Novelli EM, Shigemura N, Simon MA, Feingold B, Krishnamurti L, Morrell MR, Gries CG, Haider S, Johnson BA, Crespo MM, Bhama JK, Bermudez C, Yousem SA, Toyoda Y, Champion HC, Pilewski JM, Gladwin MT. George MP, et al. Among authors: pilewski jm. Pulm Circ. 2013 Dec;3(4):952-8. doi: 10.1086/674749. Pulm Circ. 2013. PMID: 25006411 Free PMC article.

116

Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis.

Rowe SM, Heltshe SL, Gonska T, Donaldson SH, Borowitz D, Gelfond D, Sagel SD, Khan U, Mayer-Hamblett N, Van Dalfsen JM, Joseloff E, Ramsey BW; GOAL Investigators of the Cystic Fibrosis Foundation Therapeutics Development Network. Rowe SM, et al. Am J Respir Crit Care Med. 2014 Jul 15;190(2):175-84. doi: 10.1164/rccm.201404-0703OC. Am J Respir Crit Care Med. 2014. PMID: 24927234 Free PMC article.

117

Lung transplantation with lungs from older donors: recipient and surgical factors affect outcomes.

Shigemura N, Horai T, Bhama JK, D'Cunha J, Zaldonis D, Toyoda Y, Pilewski JM, Luketich JD, Bermudez CA. Shigemura N, et al. Among authors: pilewski jm. Transplantation. 2014 Oct 27;98(8):903-8. doi: 10.1097/TP.0000000000000134. Transplantation. 2014. PMID: 24825527

118

Quantitative imaging of airway liquid absorption in cystic fibrosis.

Locke LW, Myerburg MM, Markovetz MR, Parker RS, Weber L, Czachowski MR, Harding TJ, Brown SL, Nero JA, Pilewski JM, Corcoran TE. Locke LW, et al. Among authors: pilewski jm. Eur Respir J. 2014 Sep;44(3):675-84. doi: 10.1183/09031936.00220513. Epub 2014 Apr 17. Eur Respir J. 2014. PMID: 24743971 Free PMC article. Clinical Trial.

119

Delayed chest closure after lung transplantation: techniques, outcomes, and strategies.

Shigemura N, Orhan Y, Bhama JK, D'Cunha J, Zaldonis D, Pilewski JM, Luketich JD, Bermudez CA. Shigemura N, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2014 Jul;33(7):741-8. doi: 10.1016/j.healun.2014.03.003. Epub 2014 Mar 12. J Heart Lung Transplant. 2014. PMID: 24726683

120

E3 ligase subunit Fbxo15 and PINK1 kinase regulate cardiolipin synthase 1 stability and mitochondrial function in pneumonia.

Chen BB, Coon TA, Glasser JR, Zou C, Ellis B, Das T, McKelvey AC, Rajbhandari S, Lear T, Kamga C, Shiva S, Li C, Pilewski JM, Callio J, Chu CT, Ray A, Ray P, Tyurina YY, Kagan VE, Mallampalli RK. Chen BB, et al. Among authors: pilewski jm. Cell Rep. 2014 Apr 24;7(2):476-487. doi: 10.1016/j.celrep.2014.02.048. Epub 2014 Apr 3. Cell Rep. 2014. PMID: 24703837 Free PMC article.

121

Ganciclovir-resistant cytomegalovirus infections among lung transplant recipients are associated with poor outcomes despite treatment with foscarnet-containing regimens.

Minces LR, Nguyen MH, Mitsani D, Shields RK, Kwak EJ, Silveira FP, Abdel-Massih R, Pilewski JM, Crespo MM, Bermudez C, Bhama JK, Toyoda Y, Clancy CJ. Minces LR, et al. Among authors: pilewski jm. Antimicrob Agents Chemother. 2014;58(1):128-35. doi: 10.1128/AAC.00561-13. Epub 2013 Oct 21. Antimicrob Agents Chemother. 2014. PMID: 24145525 Free PMC article.

122

Elevated CXCL10 (IP-10) in bronchoalveolar lavage fluid is associated with acute cellular rejection after human lung transplantation.

Husain S, Resende MR, Rajwans N, Zamel R, Pilewski JM, Crespo MM, Singer LG, McCurry KR, Kolls JK, Keshavjee S, Liles WC. Husain S, et al. Among authors: pilewski jm. Transplantation. 2014 Jan 15;97(1):90-7. doi: 10.1097/TP.0b013e3182a6ee0a. Transplantation. 2014. PMID: 24025324 Free PMC article.

123

Anti-PcrV antibody in cystic fibrosis: a novel approach targeting Pseudomonas aeruginosa airway infection.

Milla CE, Chmiel JF, Accurso FJ, VanDevanter DR, Konstan MW, Yarranton G, Geller DE; KB001 Study Group. Milla CE, et al. Pediatr Pulmonol. 2014 Jul;49(7):650-8. doi: 10.1002/ppul.22890. Epub 2013 Sep 9. Pediatr Pulmonol. 2014. PMID: 24019259 Free PMC article. Clinical Trial.

124

Effect of apical hyperosmotic sodium challenge and amiloride on sodium transport in human bronchial epithelial cells from cystic fibrosis donors.

Rasgado-Flores H, Krishna Mandava V, Siman H, Van Driessche W, Pilewski JM, Randell SH, Bridges RJ. Rasgado-Flores H, et al. Among authors: pilewski jm. Am J Physiol Cell Physiol. 2013 Dec 1;305(11):C1114-22. doi: 10.1152/ajpcell.00166.2013. Epub 2013 Aug 28. Am J Physiol Cell Physiol. 2013. PMID: 23986197 Free PMC article.

125

Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation.

Rowe SM, Liu B, Hill A, Hathorne H, Cohen M, Beamer JR, Accurso FJ, Dong Q, Ordoñez CL, Stone AJ, Olson ER, Clancy JP; VX06-770-101 Study Group. Rowe SM, et al. PLoS One. 2013 Jul 26;8(7):e66955. doi: 10.1371/journal.pone.0066955. Print 2013. PLoS One. 2013. PMID: 23922647 Free PMC article. Clinical Trial.

126

Plasma B lymphocyte stimulator and B cell differentiation in idiopathic pulmonary fibrosis patients.

Xue J, Kass DJ, Bon J, Vuga L, Tan J, Csizmadia E, Otterbein L, Soejima M, Levesque MC, Gibson KF, Kaminski N, Pilewski JM, Donahoe M, Sciurba FC, Duncan SR. Xue J, et al. Among authors: pilewski jm. J Immunol. 2013 Sep 1;191(5):2089-95. doi: 10.4049/jimmunol.1203476. Epub 2013 Jul 19. J Immunol. 2013. PMID: 23872052 Free PMC article.

127

Clinical trials of health information technology interventions intended for patient use: unique issues and considerations.

DeVito Dabbs A, Song MK, Myers B, Hawkins RP, Aubrecht J, Begey A, Connolly M, Li R, Pilewski JM, Bermudez CA, Dew MA. DeVito Dabbs A, et al. Among authors: pilewski jm. Clin Trials. 2013;10(6):896-906. doi: 10.1177/1740774513493149. Epub 2013 Jul 18. Clin Trials. 2013. PMID: 23867222 Free PMC article. Clinical Trial.

128

Lobar lung transplantation: a relevant surgical option in the current era of lung allocation score.

Shigemura N, D'Cunha J, Bhama JK, Shiose A, Abou El Ela A, Hackmann A, Zaldonis D, Toyoda Y, Pilewski JM, Luketich JD, Bermudez CA. Shigemura N, et al. Among authors: pilewski jm. Ann Thorac Surg. 2013 Aug;96(2):451-6. doi: 10.1016/j.athoracsur.2013.04.030. Epub 2013 Jun 15. Ann Thorac Surg. 2013. PMID: 23773735

129

Lung transplantation after lung volume reduction surgery.

Shigemura N, Gilbert S, Bhama JK, Crespo MM, Zaldonis D, Pilewski JM, Bermudez CA. Shigemura N, et al. Among authors: pilewski jm. Transplantation. 2013 Aug 27;96(4):421-5. doi: 10.1097/TP.0b013e31829853ac. Transplantation. 2013. PMID: 23736352

130

Epidemiology and outcomes of deep surgical site infections following lung transplantation.

Shields RK, Clancy CJ, Minces LR, Shigemura N, Kwak EJ, Silveira FP, Abdel-Massih RC, Bhama JK, Bermudez CA, Pilewski JM, Crespo M, Toyoda Y, Nguyen MH. Shields RK, et al. Among authors: pilewski jm. Am J Transplant. 2013 Aug;13(8):2137-45. doi: 10.1111/ajt.12292. Epub 2013 May 24. Am J Transplant. 2013. PMID: 23710593 Free article. Clinical Trial.

131

Nature and correlates of post-traumatic stress symptomatology in lung transplant recipients.

Gries CJ, Dew MA, Curtis JR, Edelman JD, DeVito Dabbs A, Pilewski JM, Goss CH, Mulligan MS, White DB. Gries CJ, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2013 May;32(5):525-32. doi: 10.1016/j.healun.2013.01.1046. J Heart Lung Transplant. 2013. PMID: 23570741 Free PMC article.

132

Liquid hyper-absorption as a cause of increased DTPA clearance in the cystic fibrosis airway.

Corcoran TE, Thomas KM, Brown S, Myerburg MM, Locke LW, Pilewski JM. Corcoran TE, et al. Among authors: pilewski jm. EJNMMI Res. 2013 Feb 27;3(1):14. doi: 10.1186/2191-219X-3-14. EJNMMI Res. 2013. PMID: 23446051 Free PMC article.

133

Early major neurologic complications after lung transplantation: incidence, risk factors, and outcome.

Shigemura N, Sclabassi RJ, Bhama JK, Gries CJ, Crespo MM, Johnson B, Pilewski JM, Bermudez CA. Shigemura N, et al. Among authors: pilewski jm. Transplantation. 2013 Mar 27;95(6):866-71. doi: 10.1097/TP.0b013e318280b359. Transplantation. 2013. PMID: 23354301

134

Patients with idiopathic pulmonary fibrosis with antibodies to heat shock protein 70 have poor prognoses.

Kahloon RA, Xue J, Bhargava A, Csizmadia E, Otterbein L, Kass DJ, Bon J, Soejima M, Levesque MC, Lindell KO, Gibson KF, Kaminski N, Banga G, Oddis CV, Pilewski JM, Sciurba FC, Donahoe M, Zhang Y, Duncan SR. Kahloon RA, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2013 Apr 1;187(7):768-75. doi: 10.1164/rccm.201203-0506OC. Am J Respir Crit Care Med. 2013. PMID: 23262513 Free PMC article.

135

Donor smoking history and age in lung transplantation: a revisit.

Shigemura N, Toyoda Y, Bhama JK, Gries CJ, Crespo M, Johnson B, Zaldonis D, Pilewski JM, Bermudez CA. Shigemura N, et al. Among authors: pilewski jm. Transplantation. 2013 Feb 15;95(3):513-8. doi: 10.1097/TP.0b013e3182751f1f. Transplantation. 2013. PMID: 23202531

136

Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis.

Moss RB, Mistry SJ, Konstan MW, Pilewski JM, Kerem E, Tal-Singer R, Lazaar AL; CF2110399 Investigators. Moss RB, et al. Among authors: pilewski jm. J Cyst Fibros. 2013 May;12(3):241-8. doi: 10.1016/j.jcf.2012.08.016. Epub 2012 Sep 17. J Cyst Fibros. 2013. PMID: 22995323 Free article. Clinical Trial.

137

Staphylococcus aureus infections in the early period after lung transplantation: epidemiology, risk factors, and outcomes.

Shields RK, Clancy CJ, Minces LR, Kwak EJ, Silveira FP, Abdel Massih RC, Toyoda Y, Bermudez C, Bhama JK, Shigemura N, Pilewski JM, Crespo M, Hong Nguyen M. Shields RK, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2012 Nov;31(11):1199-206. doi: 10.1016/j.healun.2012.08.012. Epub 2012 Sep 15. J Heart Lung Transplant. 2012. PMID: 22986156

138

Syndecan-2 is a novel target of insulin-like growth factor binding protein-3 and is over-expressed in fibrosis.

Ruiz XD, Mlakar LR, Yamaguchi Y, Su Y, Larregina AT, Pilewski JM, Feghali-Bostwick CA. Ruiz XD, et al. Among authors: pilewski jm. PLoS One. 2012;7(8):e43049. doi: 10.1371/journal.pone.0043049. Epub 2012 Aug 10. PLoS One. 2012. PMID: 22900087 Free PMC article.

139

Patients with cystic fibrosis have inducible IL-17+IL-22+ memory cells in lung draining lymph nodes.

Chan YR, Chen K, Duncan SR, Lathrop KL, Latoche JD, Logar AJ, Pociask DA, Wahlberg BJ, Ray P, Ray A, Pilewski JM, Kolls JK. Chan YR, et al. Among authors: pilewski jm. J Allergy Clin Immunol. 2013 Apr;131(4):1117-29, 1129.e1-5. doi: 10.1016/j.jaci.2012.05.036. Epub 2012 Jul 11. J Allergy Clin Immunol. 2013. PMID: 22795370 Free PMC article.

140

Imaging the postdeposition dispersion of an inhaled surfactant aerosol.

Corcoran TE, Thomas KM, Garoff S, Tilton RD, Przybycien TM, Pilewski JM. Corcoran TE, et al. Among authors: pilewski jm. J Aerosol Med Pulm Drug Deliv. 2012 Oct;25(5):290-6. doi: 10.1089/jamp.2011.0920. Epub 2012 Mar 6. J Aerosol Med Pulm Drug Deliv. 2012. PMID: 22393908 Free PMC article. Clinical Trial.

141

Prospective, observational study of voriconazole therapeutic drug monitoring among lung transplant recipients receiving prophylaxis: factors impacting levels of and associations between serum troughs, efficacy, and toxicity.

Mitsani D, Nguyen MH, Shields RK, Toyoda Y, Kwak EJ, Silveira FP, Pilewski JM, Crespo MM, Bermudez C, Bhama JK, Clancy CJ. Mitsani D, et al. Among authors: pilewski jm. Antimicrob Agents Chemother. 2012 May;56(5):2371-7. doi: 10.1128/AAC.05219-11. Epub 2012 Feb 13. Antimicrob Agents Chemother. 2012. PMID: 22330924 Free PMC article.

142

Gastrin-releasing peptide receptor expression in non-cancerous bronchial epithelia is associated with lung cancer: a case-control study.

Egloff AM, Gaither Davis A, Shuai Y, Land S, Pilewski JM, Luketich JD, Landreneau R, Miller YE, Grandis JR, Siegfried JM. Egloff AM, et al. Among authors: pilewski jm. Respir Res. 2012 Feb 1;13(1):9. doi: 10.1186/1465-9921-13-9. Respir Res. 2012. PMID: 22296774 Free PMC article.

143

Activated CD47 promotes pulmonary arterial hypertension through targeting caveolin-1.

Bauer PM, Bauer EM, Rogers NM, Yao M, Feijoo-Cuaresma M, Pilewski JM, Champion HC, Zuckerbraun BS, Calzada MJ, Isenberg JS. Bauer PM, et al. Among authors: pilewski jm. Cardiovasc Res. 2012 Mar 15;93(4):682-93. doi: 10.1093/cvr/cvr356. Epub 2012 Jan 2. Cardiovasc Res. 2012. PMID: 22215724 Free PMC article.

144

Lung transplantation for pulmonary hypertension.

George MP, Champion HC, Pilewski JM. George MP, et al. Among authors: pilewski jm. Pulm Circ. 2011 Apr-Jun;1(2):182-91. doi: 10.4103/2045-8932.83455. Pulm Circ. 2011. PMID: 22034605 Free PMC article.

145

Localized expression of tenascin in systemic sclerosis-associated pulmonary fibrosis and its regulation by insulin-like growth factor binding protein 3.

Brissett M, Veraldi KL, Pilewski JM, Medsger TA Jr, Feghali-Bostwick CA. Brissett M, et al. Among authors: pilewski jm. Arthritis Rheum. 2012 Jan;64(1):272-80. doi: 10.1002/art.30647. Arthritis Rheum. 2012. PMID: 21898349 Free PMC article.

146

Extracorporeal membrane oxygenation as a bridge to lung transplant: midterm outcomes.

Bermudez CA, Rocha RV, Zaldonis D, Bhama JK, Crespo MM, Shigemura N, Pilewski JM, Sappington PL, Boujoukos AJ, Toyoda Y. Bermudez CA, et al. Among authors: pilewski jm. Ann Thorac Surg. 2011 Oct;92(4):1226-31; discussion 1231-2. doi: 10.1016/j.athoracsur.2011.04.122. Epub 2011 Aug 26. Ann Thorac Surg. 2011. PMID: 21872213

147

Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation.

Clancy JP, Rowe SM, Accurso FJ, Aitken ML, Amin RS, Ashlock MA, Ballmann M, Boyle MP, Bronsveld I, Campbell PW, De Boeck K, Donaldson SH, Dorkin HL, Dunitz JM, Durie PR, Jain M, Leonard A, McCoy KS, Moss RB, Pilewski JM, Rosenbluth DB, Rubenstein RC, Schechter MS, Botfield M, Ordoñez CL, Spencer-Green GT, Vernillet L, Wisseh S, Yen K, Konstan MW. Clancy JP, et al. Among authors: pilewski jm. Thorax. 2012 Jan;67(1):12-8. doi: 10.1136/thoraxjnl-2011-200393. Epub 2011 Aug 8. Thorax. 2012. PMID: 21825083 Free PMC article. Clinical Trial.

148

Does simultaneous lung-liver transplantation provide an immunologic advantage compared with isolated lung transplantation?

Bhama JK, Pilewski JM, Zaldonis D, Fontes PA, DeVera ME, Shullo MA, Shigemura N, Bermudez CA, Toyoda Y, McCurry KR. Bhama JK, et al. Among authors: pilewski jm. J Thorac Cardiovasc Surg. 2011 May;141(5):e36-8. doi: 10.1016/j.jtcvs.2011.01.056. J Thorac Cardiovasc Surg. 2011. PMID: 21497229 Free article. No abstract available.

149

Five-year outcomes with alemtuzumab induction after lung transplantation.

Shyu S, Dew MA, Pilewski JM, DeVito Dabbs AJ, Zaldonis DB, Studer SM, Crespo MM, Toyoda Y, Bermudez CA, McCurry KR. Shyu S, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2011 Jul;30(7):743-54. doi: 10.1016/j.healun.2011.01.714. Epub 2011 Mar 21. J Heart Lung Transplant. 2011. PMID: 21420318 Free PMC article.

150

The HLA class II Allele DRB1*1501 is over-represented in patients with idiopathic pulmonary fibrosis.

Xue J, Gochuico BR, Alawad AS, Feghali-Bostwick CA, Noth I, Nathan SD, Rosen GD, Rosas IO, Dacic S, Ocak I, Fuhrman CR, Cuenco KT, Smith MA, Jacobs SS, Zeevi A, Morel PA, Pilewski JM, Valentine VG, Gibson KF, Kaminski N, Sciurba FC, Zhang Y, Duncan SR. Xue J, et al. Among authors: pilewski jm. PLoS One. 2011 Feb 23;6(2):e14715. doi: 10.1371/journal.pone.0014715. PLoS One. 2011. PMID: 21373184 Free PMC article.

151

Lung tissues in patients with systemic sclerosis have gene expression patterns unique to pulmonary fibrosis and pulmonary hypertension.

Hsu E, Shi H, Jordan RM, Lyons-Weiler J, Pilewski JM, Feghali-Bostwick CA. Hsu E, et al. Among authors: pilewski jm. Arthritis Rheum. 2011 Mar;63(3):783-94. doi: 10.1002/art.30159. Arthritis Rheum. 2011. PMID: 21360508 Free PMC article.

152

High mortality rates among solid organ transplant recipients infected with extensively drug-resistant Acinetobacter baumannii: using in vitro antibiotic combination testing to identify the combination of a carbapenem and colistin as an effective treatment regimen.

Shields RK, Kwak EJ, Potoski BA, Doi Y, Adams-Haduch JM, Silviera FP, Toyoda Y, Pilewski JM, Crespo M, Pasculle AW, Clancy CJ, Nguyen MH. Shields RK, et al. Among authors: pilewski jm. Diagn Microbiol Infect Dis. 2011 Jun;70(2):246-52. doi: 10.1016/j.diagmicrobio.2010.12.023. Epub 2011 Feb 25. Diagn Microbiol Infect Dis. 2011. PMID: 21353436

153

A polymorphism linked to elevated levels of interferon-γ is associated with an increased risk of cytomegalovirus disease among Caucasian lung transplant recipients at a single center.

Mitsani D, Nguyen MH, Girnita DM, Spichty K, Kwak EJ, Silveira FP, Toyoda Y, Pilewski JM, Crespo M, Bhama JK, Abdel-Massih R, Zaldonis D, Zeevi A, Clancy CJ. Mitsani D, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2011 May;30(5):523-9. doi: 10.1016/j.healun.2010.11.008. Epub 2011 Jan 15. J Heart Lung Transplant. 2011. PMID: 21239188

154

Posaconazole serum concentrations among cardiothoracic transplant recipients: factors impacting trough levels and correlation with clinical response to therapy.

Shields RK, Clancy CJ, Vadnerkar A, Kwak EJ, Silveira FP, Massih RC, Pilewski JM, Crespo M, Toyoda Y, Bhama JK, Bermudez C, Nguyen MH. Shields RK, et al. Among authors: pilewski jm. Antimicrob Agents Chemother. 2011 Mar;55(3):1308-11. doi: 10.1128/AAC.01325-10. Epub 2010 Dec 28. Antimicrob Agents Chemother. 2011. PMID: 21189337 Free PMC article.

155

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation.

Accurso FJ, Rowe SM, Clancy JP, Boyle MP, Dunitz JM, Durie PR, Sagel SD, Hornick DB, Konstan MW, Donaldson SH, Moss RB, Pilewski JM, Rubenstein RC, Uluer AZ, Aitken ML, Freedman SD, Rose LM, Mayer-Hamblett N, Dong Q, Zha J, Stone AJ, Olson ER, Ordoñez CL, Campbell PW, Ashlock MA, Ramsey BW. Accurso FJ, et al. Among authors: pilewski jm. N Engl J Med. 2010 Nov 18;363(21):1991-2003. doi: 10.1056/NEJMoa0909825. N Engl J Med. 2010. PMID: 21083385 Free PMC article. Clinical Trial.

156

Intrapulmonary disposition of amphotericin B after aerosolized delivery of amphotericin B lipid complex (Abelcet; ABLC) in lung transplant recipients.

Husain S, Capitano B, Corcoran T, Studer SM, Crespo M, Johnson B, Pilewski JM, Shutt K, Pakstis DL, Zhang S, Carey ME, Paterson DL, McCurry KR, Venkataramanan R. Husain S, et al. Among authors: pilewski jm. Transplantation. 2010 Dec 15;90(11):1215-9. doi: 10.1097/TP.0b013e3181f995ea. Transplantation. 2010. PMID: 20881664 Clinical Trial.

157

Vitamin D3 attenuates Th2 responses to Aspergillus fumigatus mounted by CD4+ T cells from cystic fibrosis patients with allergic bronchopulmonary aspergillosis.

Kreindler JL, Steele C, Nguyen N, Chan YR, Pilewski JM, Alcorn JF, Vyas YM, Aujla SJ, Finelli P, Blanchard M, Zeigler SF, Logar A, Hartigan E, Kurs-Lasky M, Rockette H, Ray A, Kolls JK. Kreindler JL, et al. Among authors: pilewski jm. J Clin Invest. 2010 Sep;120(9):3242-54. doi: 10.1172/JCI42388. Epub 2010 Aug 16. J Clin Invest. 2010. PMID: 20714107 Free PMC article.

158

Exploring the meaning of chronic rejection after lung transplantation and its impact on clinical management and caregiving.

Song MK, Devito Dabbs AJ, Studer SM, Arnold RM, Pilewski JM. Song MK, et al. Among authors: pilewski jm. J Pain Symptom Manage. 2010 Aug;40(2):246-55. doi: 10.1016/j.jpainsymman.2009.12.014. Epub 2010 Jun 11. J Pain Symptom Manage. 2010. PMID: 20541897 Free article.

159

c-Cbl facilitates endocytosis and lysosomal degradation of cystic fibrosis transmembrane conductance regulator in human airway epithelial cells.

Ye S, Cihil K, Stolz DB, Pilewski JM, Stanton BA, Swiatecka-Urban A. Ye S, et al. Among authors: pilewski jm. J Biol Chem. 2010 Aug 27;285(35):27008-27018. doi: 10.1074/jbc.M110.139881. Epub 2010 Jun 4. J Biol Chem. 2010. PMID: 20525683 Free PMC article.

160

Plasma inflammatory mediators associated with bone metabolism in COPD.

Bon JM, Zhang Y, Duncan SR, Pilewski JM, Zaldonis D, Zeevi A, McCurry KR, Greenspan SL, Sciurba FC. Bon JM, et al. Among authors: pilewski jm. COPD. 2010 Jun;7(3):186-91. doi: 10.3109/15412555.2010.482114. COPD. 2010. PMID: 20486817 Free PMC article.

161

Acute regulation of the epithelial sodium channel in airway epithelia by proteases and trafficking.

Myerburg MM, Harvey PR, Heidrich EM, Pilewski JM, Butterworth MB. Myerburg MM, et al. Among authors: pilewski jm. Am J Respir Cell Mol Biol. 2010 Dec;43(6):712-9. doi: 10.1165/rcmb.2009-0348OC. Epub 2010 Jan 22. Am J Respir Cell Mol Biol. 2010. PMID: 20097829 Free PMC article.

162

Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis.

Hutt DM, Herman D, Rodrigues AP, Noel S, Pilewski JM, Matteson J, Hoch B, Kellner W, Kelly JW, Schmidt A, Thomas PJ, Matsumura Y, Skach WR, Gentzsch M, Riordan JR, Sorscher EJ, Okiyoneda T, Yates JR 3rd, Lukacs GL, Frizzell RA, Manning G, Gottesfeld JM, Balch WE. Hutt DM, et al. Among authors: pilewski jm. Nat Chem Biol. 2010 Jan;6(1):25-33. doi: 10.1038/nchembio.275. Epub 2009 Dec 6. Nat Chem Biol. 2010. PMID: 19966789 Free PMC article.

163

Absorptive clearance of DTPA as an aerosol-based biomarker in the cystic fibrosis airway.

Corcoran TE, Thomas KM, Myerburg MM, Muthukrishnan A, Weber L, Frizzell R, Pilewski JM. Corcoran TE, et al. Among authors: pilewski jm. Eur Respir J. 2010 Apr;35(4):781-6. doi: 10.1183/09031936.00059009. Epub 2009 Aug 28. Eur Respir J. 2010. PMID: 19717485 Free PMC article. Clinical Trial.

164

AMPK agonists ameliorate sodium and fluid transport and inflammation in cystic fibrosis airway epithelial cells.

Myerburg MM, King JD Jr, Oyster NM, Fitch AC, Magill A, Baty CJ, Watkins SC, Kolls JK, Pilewski JM, Hallows KR. Myerburg MM, et al. Among authors: pilewski jm. Am J Respir Cell Mol Biol. 2010 Jun;42(6):676-84. doi: 10.1165/2009-0147OC. Epub 2009 Jul 17. Am J Respir Cell Mol Biol. 2010. PMID: 19617399 Free PMC article.

165

Role of insulin-like growth factor binding protein-3 in allergic airway remodeling.

Veraldi KL, Gibson BT, Yasuoka H, Myerburg MM, Kelly EA, Balzar S, Jarjour NN, Pilewski JM, Wenzel SE, Feghali-Bostwick CA. Veraldi KL, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2009 Oct 1;180(7):611-7. doi: 10.1164/rccm.200810-1555OC. Epub 2009 Jul 16. Am J Respir Crit Care Med. 2009. PMID: 19608721 Free PMC article.

166

Experience with immune monitoring in lung transplant recipients: correlation of low immune function with infection.

Husain S, Raza K, Pilewski JM, Zaldonis D, Crespo M, Toyoda Y, Shutt K, Spichty K, Bentlejewski C, Pakstis DL, Carey ME, McCurry KR, Zeevi A. Husain S, et al. Among authors: pilewski jm. Transplantation. 2009 Jun 27;87(12):1852-7. doi: 10.1097/TP.0b013e3181a75ad2. Transplantation. 2009. PMID: 19543064

167

SLC26A9 is a constitutively active, CFTR-regulated anion conductance in human bronchial epithelia.

Bertrand CA, Zhang R, Pilewski JM, Frizzell RA. Bertrand CA, et al. Among authors: pilewski jm. J Gen Physiol. 2009 Apr;133(4):421-38. doi: 10.1085/jgp.200810097. Epub 2009 Mar 16. J Gen Physiol. 2009. PMID: 19289574 Free PMC article.

168

Extracorporeal membrane oxygenation for primary graft dysfunction after lung transplantation: long-term survival.

Bermudez CA, Adusumilli PS, McCurry KR, Zaldonis D, Crespo MM, Pilewski JM, Toyoda Y. Bermudez CA, et al. Among authors: pilewski jm. Ann Thorac Surg. 2009 Mar;87(3):854-60. doi: 10.1016/j.athoracsur.2008.11.036. Ann Thorac Surg. 2009. PMID: 19231405

169

Interleukin-17A induces bicarbonate secretion in normal human bronchial epithelial cells.

Kreindler JL, Bertrand CA, Lee RJ, Karasic T, Aujla S, Pilewski JM, Frizzell RA, Kolls JK. Kreindler JL, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2009 Feb;296(2):L257-66. doi: 10.1152/ajplung.00344.2007. Epub 2008 Dec 12. Am J Physiol Lung Cell Mol Physiol. 2009. PMID: 19074559 Free PMC article.

170

Egr-1 regulates autophagy in cigarette smoke-induced chronic obstructive pulmonary disease.

Chen ZH, Kim HP, Sciurba FC, Lee SJ, Feghali-Bostwick C, Stolz DB, Dhir R, Landreneau RJ, Schuchert MJ, Yousem SA, Nakahira K, Pilewski JM, Lee JS, Zhang Y, Ryter SW, Choi AM. Chen ZH, et al. Among authors: pilewski jm. PLoS One. 2008 Oct 2;3(10):e3316. doi: 10.1371/journal.pone.0003316. PLoS One. 2008. PMID: 18830406 Free PMC article.

171

Postdeposition dispersion of aerosol medications using surfactant carriers.

Marcinkowski AL, Garoff S, Tilton RD, Pilewski JM, Corcoran TE. Marcinkowski AL, et al. Among authors: pilewski jm. J Aerosol Med Pulm Drug Deliv. 2008 Dec;21(4):361-70. doi: 10.1089/jamp.2008.0699. J Aerosol Med Pulm Drug Deliv. 2008. PMID: 18800882

172

CX3CL1 up-regulation is associated with recruitment of CX3CR1+ mononuclear phagocytes and T lymphocytes in the lungs during cigarette smoke-induced emphysema.

McComb JG, Ranganathan M, Liu XH, Pilewski JM, Ray P, Watkins SC, Choi AM, Lee JS. McComb JG, et al. Among authors: pilewski jm. Am J Pathol. 2008 Oct;173(4):949-61. doi: 10.2353/ajpath.2008.071034. Epub 2008 Sep 4. Am J Pathol. 2008. PMID: 18772344 Free PMC article.

173

Post-transplant colonization with non-Aspergillus molds and risk of development of invasive fungal disease in lung transplant recipients.

Silveira FP, Kwak EJ, Paterson DL, Pilewski JM, McCurry KR, Husain S. Silveira FP, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2008 Aug;27(8):850-5. doi: 10.1016/j.healun.2008.05.021. J Heart Lung Transplant. 2008. PMID: 18656797

174

Chaperone displacement from mutant cystic fibrosis transmembrane conductance regulator restores its function in human airway epithelia.

Sun F, Mi Z, Condliffe SB, Bertrand CA, Gong X, Lu X, Zhang R, Latoche JD, Pilewski JM, Robbins PD, Frizzell RA. Sun F, et al. Among authors: pilewski jm. FASEB J. 2008 Sep;22(9):3255-63. doi: 10.1096/fj.07-105338. Epub 2008 Jun 12. FASEB J. 2008. PMID: 18556464 Free PMC article.

175

Prostasin expression is regulated by airway surface liquid volume and is increased in cystic fibrosis.

Myerburg MM, McKenna EE, Luke CJ, Frizzell RA, Kleyman TR, Pilewski JM. Myerburg MM, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2008 May;294(5):L932-41. doi: 10.1152/ajplung.00437.2007. Epub 2008 Feb 29. Am J Physiol Lung Cell Mol Physiol. 2008. PMID: 18310226 Free PMC article.

176

IL-22 mediates mucosal host defense against Gram-negative bacterial pneumonia.

Aujla SJ, Chan YR, Zheng M, Fei M, Askew DJ, Pociask DA, Reinhart TA, McAllister F, Edeal J, Gaus K, Husain S, Kreindler JL, Dubin PJ, Pilewski JM, Myerburg MM, Mason CA, Iwakura Y, Kolls JK. Aujla SJ, et al. Among authors: pilewski jm. Nat Med. 2008 Mar;14(3):275-81. doi: 10.1038/nm1710. Epub 2008 Feb 10. Nat Med. 2008. PMID: 18264110 Free PMC article.

177

Defining an inhibitory domain in the alpha-subunit of the epithelial sodium channel.

Carattino MD, Passero CJ, Steren CA, Maarouf AB, Pilewski JM, Myerburg MM, Hughey RP, Kleyman TR. Carattino MD, et al. Among authors: pilewski jm. Am J Physiol Renal Physiol. 2008 Jan;294(1):F47-52. doi: 10.1152/ajprenal.00399.2007. Epub 2007 Nov 21. Am J Physiol Renal Physiol. 2008. PMID: 18032549 Free article.

178

Autoantibodies in patients with chronic obstructive pulmonary disease.

Feghali-Bostwick CA, Gadgil AS, Otterbein LE, Pilewski JM, Stoner MW, Csizmadia E, Zhang Y, Sciurba FC, Duncan SR. Feghali-Bostwick CA, et al. Among authors: pilewski jm. Am J Respir Crit Care Med. 2008 Jan 15;177(2):156-63. doi: 10.1164/rccm.200701-014OC. Epub 2007 Nov 1. Am J Respir Crit Care Med. 2008. PMID: 17975205 Free PMC article.

179

Successful outcome of human metapneumovirus (hMPV) pneumonia in a lung transplant recipient treated with intravenous ribavirin.

Raza K, Ismailjee SB, Crespo M, Studer SM, Sanghavi S, Paterson DL, Kwak EJ, Rinaldo CR Jr, Pilewski JM, McCurry KR, Husain S. Raza K, et al. Among authors: pilewski jm. J Heart Lung Transplant. 2007 Aug;26(8):862-4. doi: 10.1016/j.healun.2007.05.020. Epub 2007 Jul 12. J Heart Lung Transplant. 2007. PMID: 17692793 Free PMC article.

180

Cellular and humoral autoreactivity in idiopathic pulmonary fibrosis.

Feghali-Bostwick CA, Tsai CG, Valentine VG, Kantrow S, Stoner MW, Pilewski JM, Gadgil A, George MP, Gibson KF, Choi AM, Kaminski N, Zhang Y, Duncan SR. Feghali-Bostwick CA, et al. Among authors: pilewski jm. J Immunol. 2007 Aug 15;179(4):2592-9. doi: 10.4049/jimmunol.179.4.2592. J Immunol. 2007. PMID: 17675522 Clinical Trial.

181

Hepatocyte growth factor and other fibroblast secretions modulate the phenotype of human bronchial epithelial cells.

Myerburg MM, Latoche JD, McKenna EE, Stabile LP, Siegfried JS, Feghali-Bostwick CA, Pilewski JM. Myerburg MM, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2007 Jun;292(6):L1352-60. doi: 10.1152/ajplung.00328.2006. Epub 2007 Feb 16. Am J Physiol Lung Cell Mol Physiol. 2007. PMID: 17307814 Free article.

182

Epithelial Na+ channels are fully activated by furin- and prostasin-dependent release of an inhibitory peptide from the gamma-subunit.

Bruns JB, Carattino MD, Sheng S, Maarouf AB, Weisz OA, Pilewski JM, Hughey RP, Kleyman TR. Bruns JB, et al. Among authors: pilewski jm. J Biol Chem. 2007 Mar 2;282(9):6153-60. doi: 10.1074/jbc.M610636200. Epub 2007 Jan 1. J Biol Chem. 2007. PMID: 17199078 Free article.

183

Molecular and functional properties of lung SP cells.

Reynolds SD, Shen H, Reynolds PR, Betsuyaku T, Pilewski JM, Gambelli F, Di Giuseppe M, Ortiz LA, Stripp BR. Reynolds SD, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2007 Apr;292(4):L972-83. doi: 10.1152/ajplung.00090.2006. Epub 2006 Dec 1. Am J Physiol Lung Cell Mol Physiol. 2007. PMID: 17142352 Free article.

184

Insulin-like growth factor-binding protein-5 induces pulmonary fibrosis and triggers mononuclear cellular infiltration.

Yasuoka H, Zhou Z, Pilewski JM, Oury TD, Choi AM, Feghali-Bostwick CA. Yasuoka H, et al. Among authors: pilewski jm. Am J Pathol. 2006 Nov;169(5):1633-42. doi: 10.2353/ajpath.2006.060501. Am J Pathol. 2006. PMID: 17071587 Free PMC article.

185

Aerosol deposition of lipid complex amphotericin-B (Abelcet) in lung transplant recipients.

Corcoran TE, Venkataramanan R, Mihelc KM, Marcinkowski AL, Ou J, McCook BM, Weber L, Carey ME, Paterson DL, Pilewski JM, McCurry KR, Husain S. Corcoran TE, et al. Among authors: pilewski jm. Am J Transplant. 2006 Nov;6(11):2765-73. doi: 10.1111/j.1600-6143.2006.01529.x. Am J Transplant. 2006. PMID: 17049064 Free article.

186

Comprehensive analysis of gene expression on GOLD-2 Versus GOLD-0 smokers reveals novel genes important in the pathogenesis of COPD.

Ning W, Lee J, Kaminski N, Feghali-Bostwick CA, Watkins SC, Pilewski JM, Peters DG, Hogg JC, Choi AM. Ning W, et al. Among authors: pilewski jm. Proc Am Thorac Soc. 2006 Aug;3(6):466. doi: 10.1513/pats.200603-031MS. Proc Am Thorac Soc. 2006. PMID: 16921106 No abstract available.

187

Airway surface liquid volume regulates ENaC by altering the serine protease-protease inhibitor balance: a mechanism for sodium hyperabsorption in cystic fibrosis.

Myerburg MM, Butterworth MB, McKenna EE, Peters KW, Frizzell RA, Kleyman TR, Pilewski JM. Myerburg MM, et al. Among authors: pilewski jm. J Biol Chem. 2006 Sep 22;281(38):27942-9. doi: 10.1074/jbc.M606449200. Epub 2006 Jul 26. J Biol Chem. 2006. PMID: 16873367 Free article.

188

The epithelial Na+ channel is inhibited by a peptide derived from proteolytic processing of its alpha subunit.

Carattino MD, Sheng S, Bruns JB, Pilewski JM, Hughey RP, Kleyman TR. Carattino MD, et al. Among authors: pilewski jm. J Biol Chem. 2006 Jul 7;281(27):18901-7. doi: 10.1074/jbc.M604109200. Epub 2006 May 11. J Biol Chem. 2006. PMID: 16690613 Free article.

189

Up-regulation of AMP-activated kinase by dysfunctional cystic fibrosis transmembrane conductance regulator in cystic fibrosis airway epithelial cells mitigates excessive inflammation.

Hallows KR, Fitch AC, Richardson CA, Reynolds PR, Clancy JP, Dagher PC, Witters LA, Kolls JK, Pilewski JM. Hallows KR, et al. Among authors: pilewski jm. J Biol Chem. 2006 Feb 17;281(7):4231-41. doi: 10.1074/jbc.M511029200. Epub 2005 Dec 18. J Biol Chem. 2006. PMID: 16361706 Free article.

190

The status of gene therapy for cystic fibrosis.

Weiss DJ, Pilewski JM. Weiss DJ, et al. Among authors: pilewski jm. Semin Respir Crit Care Med. 2003 Dec;24(6):749-70. doi: 10.1055/s-2004-815670. Semin Respir Crit Care Med. 2003. PMID: 16088590

191

Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth-related oncogene-alpha and granulocyte colony-stimulating factor in bronchial epithelium: implications for airway inflammation in cystic fibrosis.

McAllister F, Henry A, Kreindler JL, Dubin PJ, Ulrich L, Steele C, Finder JD, Pilewski JM, Carreno BM, Goldman SJ, Pirhonen J, Kolls JK. McAllister F, et al. Among authors: pilewski jm. J Immunol. 2005 Jul 1;175(1):404-12. doi: 10.4049/jimmunol.175.1.404. J Immunol. 2005. PMID: 15972674 Free PMC article.

192

Insulin-like growth factor binding proteins 3 and 5 are overexpressed in idiopathic pulmonary fibrosis and contribute to extracellular matrix deposition.

Pilewski JM, Liu L, Henry AC, Knauer AV, Feghali-Bostwick CA. Pilewski JM, et al. Am J Pathol. 2005 Feb;166(2):399-407. doi: 10.1016/S0002-9440(10)62263-8. Am J Pathol. 2005. PMID: 15681824 Free PMC article.

193

Comprehensive gene expression profiles reveal pathways related to the pathogenesis of chronic obstructive pulmonary disease.

Ning W, Li CJ, Kaminski N, Feghali-Bostwick CA, Alber SM, Di YP, Otterbein SL, Song R, Hayashi S, Zhou Z, Pinsky DJ, Watkins SC, Pilewski JM, Sciurba FC, Peters DG, Hogg JC, Choi AM. Ning W, et al. Among authors: pilewski jm. Proc Natl Acad Sci U S A. 2004 Oct 12;101(41):14895-900. doi: 10.1073/pnas.0401168101. Epub 2004 Oct 5. Proc Natl Acad Sci U S A. 2004. PMID: 15469929 Free PMC article.

194

Finally, mice with CF lung disease.

Frizzell RA, Pilewski JM. Frizzell RA, et al. Among authors: pilewski jm. Nat Med. 2004 May;10(5):452-4. doi: 10.1038/nm0504-452. Nat Med. 2004. PMID: 15122239 No abstract available.

195

Selective toxicity of engineered lentivirus lytic peptides in a CF airway cell model.

Phadke SM, Islam K, Deslouches B, Kapoor SA, Beer Stolz D, Watkins SC, Montelaro RC, Pilewski JM, Mietzner TA. Phadke SM, et al. Among authors: pilewski jm. Peptides. 2003 Aug;24(8):1099-107. doi: 10.1016/j.peptides.2003.07.001. Peptides. 2003. PMID: 14612179

196

Gene therapy for airway diseases: continued progress toward identifying and overcoming barriers to efficiency.

Pilewski JM. Pilewski JM. Am J Respir Cell Mol Biol. 2002 Aug;27(2):117-21. doi: 10.1165/ajrcmb.27.2.f244. Am J Respir Cell Mol Biol. 2002. PMID: 12151301 Review. No abstract available.

197

Secreted and transmembrane mucins inhibit gene transfer with AAV4 more efficiently than AAV5.

Walters RW, Pilewski JM, Chiorini JA, Zabner J. Walters RW, et al. Among authors: pilewski jm. J Biol Chem. 2002 Jun 28;277(26):23709-13. doi: 10.1074/jbc.M200292200. Epub 2002 Mar 29. J Biol Chem. 2002. PMID: 11925433 Free article.

198

Na+ transport in normal and CF human bronchial epithelial cells is inhibited by BAY 39-9437.

Bridges RJ, Newton BB, Pilewski JM, Devor DC, Poll CT, Hall RL. Bridges RJ, et al. Among authors: pilewski jm. Am J Physiol Lung Cell Mol Physiol. 2001 Jul;281(1):L16-23. doi: 10.1152/ajplung.2001.281.1.L16. Am J Physiol Lung Cell Mol Physiol. 2001. PMID: 11404240 Free article.

199

Hepatocyte growth factor promotes tumor growth in a novel in vivo model of human lung cancer.

Pilewski JM, Bumbalo TS 3rd, Davis AG, Siegfried JM. Pilewski JM, et al. Am J Respir Cell Mol Biol. 2001 May;24(5):556-62. doi: 10.1165/ajrcmb.24.5.4074. Am J Respir Cell Mol Biol. 2001. PMID: 11350824

200

Pharmacological modulation of ion transport across wild-type and DeltaF508 CFTR-expressing human bronchial epithelia.

Devor DC, Bridges RJ, Pilewski JM. Devor DC, et al. Among authors: pilewski jm. Am J Physiol Cell Physiol. 2000 Aug;279(2):C461-79. doi: 10.1152/ajpcell.2000.279.2.C461. Am J Physiol Cell Physiol. 2000. PMID: 10913013 Free article.

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