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Quoted phrase not found in phrase index: "Abnormal pyramidal sign"
Page 1
Mitochondrial membrane protein-associated neurodegeneration (MPAN).
Hartig M, Prokisch H, Meitinger T, Klopstock T. Hartig M, et al. Int Rev Neurobiol. 2013;110:73-84. doi: 10.1016/B978-0-12-410502-7.00004-1. Int Rev Neurobiol. 2013. PMID: 24209434 Review.
The C19orf12 gene product is an orphan mitochondrial membrane protein, and most mutations are predicted to cause loss of function. From 67 MPAN cases so far reported, we describe here the clinical, radiological, and genetic features. Key clinical features are pyramidal …
The C19orf12 gene product is an orphan mitochondrial membrane protein, and most mutations are predicted to cause loss of function. Fr …
Spinocerebellar ataxia in a cohort of patients from Rio de Janeiro.
Alvarenga MP, Siciliani LC, Carvalho RS, Ganimi MC, Penna PS. Alvarenga MP, et al. Neurol Sci. 2022 Aug;43(8):4997-5005. doi: 10.1007/s10072-022-06084-x. Epub 2022 Apr 25. Neurol Sci. 2022. PMID: 35469073 Review.
Mobility assistance was required in 75% after 11 years and wheelchair in 25%. The Scale for the Assessment and Rating of Ataxia scores at the last follow-up varied from 2 to 37 (median = 14.50) and correlated positively with duration of the disease. ...African ethnicity wa …
Mobility assistance was required in 75% after 11 years and wheelchair in 25%. The Scale for the Assessment and Rating of Ataxia scores …
Analysis of Chinese patients with sporadic Creutzfeldt-Jakob disease.
Yang J, Kuang H, Wang Q, Liu J, Chen X, Shang H. Yang J, et al. Prion. 2020 Dec;14(1):137-142. doi: 10.1080/19336896.2020.1761515. Prion. 2020. PMID: 32378453 Free PMC article.
With the progression of the disease, the four main clinical symptoms and signs were developed, including myoclonus, visual or cerebella disturbance, pyramidal or extrapyramidal dysfunction, and akinetic mutism. Extrapyramidal symptoms were more frequently observed. …
With the progression of the disease, the four main clinical symptoms and signs were developed, including myoclonus, visual or cerebella dist …
PLA2G6-associated neurodegeneration: New insights into brain abnormalities and disease progression.
Darling A, Aguilera-Albesa S, Tello CA, Serrano M, Tomás M, Camino-León R, Fernández-Ramos J, Jiménez-Escrig A, Poó P, O'Callaghan M, Ortez C, Nascimento A, Fernández Mesaque RC, Madruga M, Arrabal L, Roldan S, Gómez-Martín H, Garrido C, Temudo T, Jou-Muñoz C, Muchart J, Huisman TAGM, Poretti A, Lupo V, Espinós C, Pérez-Dueñas B. Darling A, et al. Parkinsonism Relat Disord. 2019 Apr;61:179-186. doi: 10.1016/j.parkreldis.2018.10.013. Epub 2018 Oct 13. Parkinsonism Relat Disord. 2019. PMID: 30340910
We performed qualitative and quantitative assessment of MRI abnormalities and searched for clinical and radiological phenotype and genotype correlations. ...CONCLUSIONS: Cerebellar atrophy was a universal radiological sign in infantile and childhood onset PLAN, and …
We performed qualitative and quantitative assessment of MRI abnormalities and searched for clinical and radiological phenotype and ge …
FDG-PET in Creutzfeldt-Jakob disease: Analysis of clinical-PET correlation.
Renard D, Castelnovo G, Collombier L, Thouvenot E, Boudousq V. Renard D, et al. Prion. 2017 Nov 2;11(6):440-453. doi: 10.1080/19336896.2017.1387348. Epub 2017 Nov 13. Prion. 2017. PMID: 29099286 Free PMC article.

Two types of statistical parametric mapping (SPM) analyses, using stringent level of significance p < 0.001 and extent threshold of 100 voxels, were performed: one comparing CJD patients presenting specific sign against CJD patients without this specific sign (in

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Two types of statistical parametric mapping (SPM) analyses, using stringent level of significance p < 0.001 and extent threshold of 100 v

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Characterization of the central motor conduction time in a large cohort of spinocerebellar ataxia type 3 patients.
Shi Y, Peng L, Zou G, Chen Z, Wan L, Tang Z, Hou X, Peng H, Wang C, Shen L, Xia K, Qiu R, Tang B, Jiang H. Shi Y, et al. Parkinsonism Relat Disord. 2022 Nov;104:58-63. doi: 10.1016/j.parkreldis.2022.10.006. Epub 2022 Oct 8. Parkinsonism Relat Disord. 2022. PMID: 36244162
Moreover, SCA3 patients with Babinski signs did not necessarily have abnormal CMCT, and vice versa. Our study demonstrated that PMS is a reliable method as F wave for detecting CMCT in SCA3. ...CONCLUSIONS: A small proportion of SCA3 patients had a slight prolongation of C …
Moreover, SCA3 patients with Babinski signs did not necessarily have abnormal CMCT, and vice versa. Our study demonstrated that PMS i …
Electrophysiological Assessment and Classification of Motor Pathway Function in Patients With Spinal Dural Arteriovenous Fistula.
Nakanishi K, Tanaka N, Fujimoto Y, Nishikawa K, Kamei N, Nakamae T, Kotaka S, Adachi N. Nakanishi K, et al. J Clin Neurophysiol. 2019 Jan;36(1):45-51. doi: 10.1097/WNP.0000000000000526. J Clin Neurophysiol. 2019. PMID: 30308550
PCT-AH in the SDAVF group was significantly longer than that in the control and CMT groups. Twelve patients in the SDAVF group showed abnormal CMCT-AH and/or PCT-AH. Abnormal CMCT-AH and PCT-AH were detected in five cases that exhibited UMN sign and/or LMN …
PCT-AH in the SDAVF group was significantly longer than that in the control and CMT groups. Twelve patients in the SDAVF group showed abn …
Biallelic MYORG mutation carriers exhibit primary brain calcification with a distinct phenotype.
Grangeon L, Wallon D, Charbonnier C, Quenez O, Richard AC, Rousseau S, Budowski C, Lebouvier T, Corbille AG, Vidailhet M, Méneret A, Roze E, Anheim M, Tranchant C, Favrole P, Antoine JC, Defebvre L, Ayrignac X, Labauge P, Pariente J, Clanet M, Maltête D, Rovelet-Lecrux A, Boland A, Deleuze JF; French PFBC study group; Frebourg T, Hannequin D, Campion D, Nicolas G. Grangeon L, et al. Brain. 2019 Jun 1;142(6):1573-1586. doi: 10.1093/brain/awz095. Brain. 2019. PMID: 31009047
We found that MYORG patients exhibited a high clinical penetrance with a median age of onset of 52 years (range: 21-62) with motor impairment at the forefront. In particular, dysarthria was the presenting sign in 11/16 patients. In contrast to patients with autosomal domin …
We found that MYORG patients exhibited a high clinical penetrance with a median age of onset of 52 years (range: 21-62) with motor impairmen …
Correlation between pyramidal signs and the severity of cervical myelopathy.
Chikuda H, Seichi A, Takeshita K, Shoda N, Ono T, Matsudaira K, Kawaguchi H, Nakamura K. Chikuda H, et al. Eur Spine J. 2010 Oct;19(10):1684-9. doi: 10.1007/s00586-010-1364-3. Epub 2010 Mar 13. Eur Spine J. 2010. PMID: 20229121 Free PMC article.

The most prevalent signs were hyperreflexia (94%), Hoffmann reflex (81%), Babinski sign (53%), and ankle clonus (35%). Babinski sign (P < 0.001), ankle clonus, and Hoffmann reflex showed significant association with the lower m-JOA score. Conversely, no as

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The most prevalent signs were hyperreflexia (94%), Hoffmann reflex (81%), Babinski sign (53%), and ankle clonus (35%). Babinski si …
Efficacy and safety of intravenous high-dose immunoglobulin in treatment of the severe form of Japanese encephalitis.
Chen D, Peng X, Zhan Y, Wu P, Jiang L, Hu Y. Chen D, et al. Neurol Sci. 2022 Jun;43(6):3911-3918. doi: 10.1007/s10072-022-05891-6. Epub 2022 Jan 19. Neurol Sci. 2022. PMID: 35044559

The duration of unconsciousness and the number of days of seizures, a dull response to light, the pyramidal sign, and meningeal-irritation sign in the IVIG group were shorter than those in the control group (p < 0.05). ...The Liverpool Outcome Score

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The duration of unconsciousness and the number of days of seizures, a dull response to light, the pyramidal sign, and meningea …
27 results