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231 results

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Quoted phrase not found in phrase index: "Central Nervous System Paraganglioma"
Page 1
Hypoxia-Inducible Factor 2 Alpha (HIF2α) Inhibitors: Targeting Genetically Driven Tumor Hypoxia.
Toledo RA, Jimenez C, Armaiz-Pena G, Arenillas C, Capdevila J, Dahia PLM. Toledo RA, et al. Endocr Rev. 2023 Mar 4;44(2):312-322. doi: 10.1210/endrev/bnac025. Endocr Rev. 2023. PMID: 36301191 Free PMC article.
Belzutifan, a highly specific and well-tolerated HIF2alpha inhibitor, recently received FDA approval for the treatment of nonmetastatic renal cell carcinomas, pancreatic neuroendocrine tumors, and central nervous system hemangioblastomas from patients with vo …
Belzutifan, a highly specific and well-tolerated HIF2alpha inhibitor, recently received FDA approval for the treatment of nonmetastatic rena …
Familial pheochromocytoma.
Erlic Z, Neumann HP. Erlic Z, et al. Hormones (Athens). 2009 Jan-Mar;8(1):29-38. doi: 10.14310/horm.2002.1219. Hormones (Athens). 2009. PMID: 19269919 Free article.
Other important components of VHL are hemangioblastomas of the eye and Central Nervous System (CNS), renal clear cell carcinoma, multiple pancreatic cysts and islet cell carcinoma. PGL syndromes have been genetically characterized as PGL 1, 3 and 4 and are ca …
Other important components of VHL are hemangioblastomas of the eye and Central Nervous System (CNS), renal clear cell c …
Cerebellar paraganglioma.
Prayson RA, Chahlavi A, Luciano M. Prayson RA, et al. Ann Diagn Pathol. 2004 Aug;8(4):219-23. doi: 10.1053/j.anndiagpath.2004.04.005. Ann Diagn Pathol. 2004. PMID: 15290673
Paragangliomas arising as primary neoplasms in the intracranial portion of the central nervous system are relatively uncommon and only have been rarely reported. ...Morphologic and immunohistochemical features of the neoplasm are discussed and literatu …
Paragangliomas arising as primary neoplasms in the intracranial portion of the central nervous system are relati …
Management recommendations for pancreatic manifestations of von Hippel-Lindau disease.
Laks S, van Leeuwaarde R, Patel D, Keutgen XM, Hammel P, Nilubol N, Links TP, Halfdanarson TR, Daniels AB, Tirosh A; Pancreatic Manifestations Recommendations Development Subcommittee of the VHL Alliance. Laks S, et al. Cancer. 2022 Feb 1;128(3):435-446. doi: 10.1002/cncr.33978. Epub 2021 Nov 4. Cancer. 2022. PMID: 34735022 Free article. Review.
Von Hippel-Lindau disease (VHL) is a multineoplasm inherited disease manifesting with hemangioblastoma of the central nervous system and retina, adrenal pheochromocytoma, renal cell carcinoma, pancreatic neuroendocrine tumors and cysts, and neoplasms/cysts of …
Von Hippel-Lindau disease (VHL) is a multineoplasm inherited disease manifesting with hemangioblastoma of the central nervous …
Severe paroxysmal hypertension (pseudopheochromocytoma).
Mann SJ. Mann SJ. Curr Hypertens Rep. 2008 Feb;10(1):12-8. doi: 10.1007/s11906-008-0005-2. Curr Hypertens Rep. 2008. PMID: 18367021 Review.
Patients experience symptomatic blood pressure surges likely linked to sympathetic nervous system stimulation. A specific personality profile associated with this disorder suggests a psychological basis, attributable to repressed emotion related to prior emotional t …
Patients experience symptomatic blood pressure surges likely linked to sympathetic nervous system stimulation. A specific pers …
Temporal paragangliomas.
Suárez C, Sevilla MA, Llorente JL. Suárez C, et al. Eur Arch Otorhinolaryngol. 2007 Jul;264(7):719-31. doi: 10.1007/s00405-007-0267-3. Epub 2007 Mar 2. Eur Arch Otorhinolaryngol. 2007. PMID: 17333230 Review.
Temporal paragangliomas (PGL) are usually limited to the paraganglionar system with a sporadic or familial origin. ...
Temporal paragangliomas (PGL) are usually limited to the paraganglionar system with a sporadic or familial origin. ...
Hemangioblastomas and Other Vascular Origating Tumors of Brain or Spinal Cord.
Vetrano IG, Gioppo A, Faragò G, Pinzi V, Pollo B, Broggi M, Schiariti M, Ferroli P, Acerbi F. Vetrano IG, et al. Adv Exp Med Biol. 2023;1405:377-403. doi: 10.1007/978-3-031-23705-8_14. Adv Exp Med Biol. 2023. PMID: 37452946 Review.
The median age of patients with sporadic HBS is about 40 years. More than two-third of VHL patients develop one or more central nervous system HBs during their lifetime; in case of VHL, patients at first diagnosis are usually younger than the patients with sp …
The median age of patients with sporadic HBS is about 40 years. More than two-third of VHL patients develop one or more central ne …
The clinical aspects of pituitary tumour genetics.
Dénes J, Korbonits M. Dénes J, et al. Endocrine. 2021 Mar;71(3):663-674. doi: 10.1007/s12020-021-02633-0. Epub 2021 Feb 4. Endocrine. 2021. PMID: 33543431 Free PMC article. Review.
While most pituitary tumours are sporadic, around 5% of the cases arise in a familial setting, either isolated [familial isolated pituitary adenoma, related to AIP or X-linked acrogigantism], or in a syndromic disorder, such as multiple endocrine neoplasia type 1 or 4, Carney com …
While most pituitary tumours are sporadic, around 5% of the cases arise in a familial setting, either isolated [familial isolated pituitary …
Von Hippel-Lindau and Hereditary Pheochromocytoma/Paraganglioma Syndromes: Clinical Features, Genetics, and Surveillance Recommendations in Childhood.
Rednam SP, Erez A, Druker H, Janeway KA, Kamihara J, Kohlmann WK, Nathanson KL, States LJ, Tomlinson GE, Villani A, Voss SD, Schiffman JD, Wasserman JD. Rednam SP, et al. Clin Cancer Res. 2017 Jun 15;23(12):e68-e75. doi: 10.1158/1078-0432.CCR-17-0547. Clin Cancer Res. 2017. PMID: 28620007 Review.
Von Hippel-Lindau disease (vHL) is a hereditary tumor predisposition syndrome that places affected individuals at risk for multiple tumors, which are predominantly benign and generally occur in the central nervous system or abdomen. Although the majority of t …
Von Hippel-Lindau disease (vHL) is a hereditary tumor predisposition syndrome that places affected individuals at risk for multiple tumors, …
von Hippel-Lindau disease.
Maher ER, Kaelin WG Jr. Maher ER, et al. Medicine (Baltimore). 1997 Nov;76(6):381-91. doi: 10.1097/00005792-199711000-00001. Medicine (Baltimore). 1997. PMID: 9413424 Free article. Review.
von Hippel-Lindau disease is a hereditary cancer syndrome characterized by the development of vascular tumors of the central nervous system and retina, clear cell renal carcinomas, pheochromocytomas, pancreatic islet cell tumors, endolymphatic sac tumors, and …
von Hippel-Lindau disease is a hereditary cancer syndrome characterized by the development of vascular tumors of the central nervo …
231 results