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Quoted phrase not found in phrase index: "Ciliary dyskinesia, primary, 38"
Page 1
Diagnosis and management of children with primary ciliary dyskinesia.
Harris A. Harris A. Nurs Child Young People. 2017 Sep 11;29(7):38-47. doi: 10.7748/ncyp.2017.e936. Nurs Child Young People. 2017. PMID: 29115761
Primary ciliary dyskinesia (PCD) is a rare, genetic disorder of the motile cilia characterised by chronic lung disease, nasal and sinus disease, chronic ear infections with glue ear leading to possible hearing impairment, and subfertility. ...This article see …
Primary ciliary dyskinesia (PCD) is a rare, genetic disorder of the motile cilia characterised by chronic lung disease, …
A retrospective review of Achromobacter species and antibiotic treatments in patients with primary ciliary dyskinesia.
Holgersen MG, Marthin JK, Johansen HK, Nielsen KG. Holgersen MG, et al. Chron Respir Dis. 2021 Jan-Dec;18:14799731211061600. doi: 10.1177/14799731211061600. Chron Respir Dis. 2021. PMID: 34854775 Free PMC article.
Objectives: Primary ciliary dyskinesia (PCD) is a rare congenital disease with defective mucociliary clearance causing frequent and often persistent pulmonary infections. ...On average, 5% of the cohort had at least one annual isolate. Infections became persi …
Objectives: Primary ciliary dyskinesia (PCD) is a rare congenital disease with defective mucociliary clearance causing …
Situs Ambiguus Is Associated With Adverse Clinical Outcomes in Children With Primary Ciliary Dyskinesia.
Kaspy KR, Dell SD, Davis SD, Ferkol TW, Rosenfeld M, Sagel SD, Milla C, Olivier KN, Barber AT, Wee W, Lin FC, Li L, Rampakakis E, Zariwala MA, Knowles MR, Leigh MW, Shapiro AJ. Kaspy KR, et al. Chest. 2024 May;165(5):1070-1081. doi: 10.1016/j.chest.2023.12.005. Epub 2023 Dec 9. Chest. 2024. PMID: 38072392
BACKGROUND: Primary ciliary dyskinesia (PCD) is a rare disorder of motile cilia associated with situs abnormalities. ...RESEARCH QUESTION: Do patients with PCD and SA achieve worse clinical outcomes compared with those with SS or SIT? STUDY DESIGN AND …
BACKGROUND: Primary ciliary dyskinesia (PCD) is a rare disorder of motile cilia associated with situs abnormalities. .. …
Lung structure-function correlation in patients with primary ciliary dyskinesia.
Boon M, Vermeulen FL, Gysemans W, Proesmans M, Jorissen M, De Boeck K. Boon M, et al. Thorax. 2015 Apr;70(4):339-45. doi: 10.1136/thoraxjnl-2014-206578. Epub 2015 Feb 11. Thorax. 2015. PMID: 25673230
BACKGROUND: Primary ciliary dyskinesia (PCD) is a rare disease, characterised by chronic airway infection. ...RESULTS: LCI was abnormal in 28 of 38 patients and a moderate correlation was observed between LCI and FEV1 (r=-0.519, p=0.001). ...
BACKGROUND: Primary ciliary dyskinesia (PCD) is a rare disease, characterised by chronic airway infection. ...RESULTS: …
The secondary nature of ciliary (dis)orientation in secondary and primary ciliary dyskinesia.
Jorissen M, Willems T. Jorissen M, et al. Acta Otolaryngol. 2004 May;124(4):527-31. doi: 10.1080/00016480410016270. Acta Otolaryngol. 2004. PMID: 15224888
OBJECTIVE: Ciliary orientation (COR) is an important parameter of mucociliary clearance and ciliary disorientation has been reported in cases of acquired abnormalities [secondary ciliary dyskinesia (SCD)] and in a very few cases as the single abnormali …
OBJECTIVE: Ciliary orientation (COR) is an important parameter of mucociliary clearance and ciliary disorientation has been re …
Respiratory manifestations in 38 patients with Alstrom syndrome.
Boerwinkle C, Marshall JD, Bryant J, Gahl WA, Olivier KN, Gunay-Aygun M. Boerwinkle C, et al. Pediatr Pulmonol. 2017 Apr;52(4):487-493. doi: 10.1002/ppul.23607. Epub 2016 Dec 28. Pediatr Pulmonol. 2017. PMID: 28029746 Free PMC article.
Prior studies have suggested phenotypic overlap between primary ciliopathies affecting the non-motile, sensory cilia, and primary ciliary dyskinesia (PCD), a motile ciliopathy characterized by respiratory tract disease. METHODS: We describe the burden …
Prior studies have suggested phenotypic overlap between primary ciliopathies affecting the non-motile, sensory cilia, and primary …
A randomised controlled trial on the effect of inhaled hypertonic saline on quality of life in primary ciliary dyskinesia.
Paff T, Daniels JM, Weersink EJ, Lutter R, Vonk Noordegraaf A, Haarman EG. Paff T, et al. Eur Respir J. 2017 Feb 23;49(2):1601770. doi: 10.1183/13993003.01770-2016. Print 2017 Feb. Eur Respir J. 2017. PMID: 28232410 Free article. Clinical Trial.
Increased cough transportability may improve quality of life (QoL) in primary ciliary dyskinesia (PCD).In this randomised controlled trial (RCT), PCD patients received twice-daily inhalations of hypertonic (7%) saline or isotonic (0.9%) saline f …
Increased cough transportability may improve quality of life (QoL) in primary ciliary dyskinesia (PCD).In this rando …
Exploring factors associated with acquisition and chronicity of infection in bronchiectasis: A population-based study.
Shkeiri R, Saliba W, Stein N, Najjar R, Weber G, Dror SK, Mishan PS, Adir Y, Shteinberg M. Shkeiri R, et al. Respir Med. 2021 Aug-Sep;185:106487. doi: 10.1016/j.rmed.2021.106487. Epub 2021 Jun 8. Respir Med. 2021. PMID: 34139580 Free article.
Factors associated with increased risk of a new infection with PA were COPD (HR 1.87 [1.52-2.28], previous isolation of HI (HR 1.38 [1.07-1.78]), and alcohol abuse (HR 2.22 [1.13-4.3]). Younger age was associated with increased risk of HI infection, while COPD was associat …
Factors associated with increased risk of a new infection with PA were COPD (HR 1.87 [1.52-2.28], previous isolation of HI (HR 1.38 [ …
Effect of aerosolized uridine-5'-triphosphate on airway clearance with cough in patients with primary ciliary dyskinesia.
Noone PG, Bennett WD, Regnis JA, Zeman KL, Carson JL, King M, Boucher RC, Knowles MR. Noone PG, et al. Am J Respir Crit Care Med. 1999 Jul;160(1):144-9. doi: 10.1164/ajrccm.160.1.9806146. Am J Respir Crit Care Med. 1999. PMID: 10390392 Clinical Trial.
Primary ciliary dyskinesia (PCD) is a genetic disease characterized by abnormal ciliary structure and function and impaired mucociliary clearance. ...Whole-lung clearance during cough in patients with defective ciliary function is enhanced after …
Primary ciliary dyskinesia (PCD) is a genetic disease characterized by abnormal ciliary structure and function a …
PREFUL MRI for Monitoring Perfusion and Ventilation Changes after Elexacaftor-Tezacaftor-Ivacaftor Therapy for Cystic Fibrosis: A Feasibility Study.
Dohna M, Voskrebenzev A, Klimeš F, Kaireit TF, Glandorf J, Pallenberg ST, Ringshausen FC, Hansen G, Renz DM, Wacker F, Dittrich AM, Vogel-Claussen J. Dohna M, et al. Radiol Cardiothorac Imaging. 2024 Apr;6(2):e230104. doi: 10.1148/ryct.230104. Radiol Cardiothorac Imaging. 2024. PMID: 38573129 Free PMC article.
T1- and T2-weighted MR images and PREFUL perfusion maps were visually assessed for semiquantitative Eichinger scores. Wilcoxon signed rank test compared clinical parameters and PREFUL values before and after ETI therapy. ...Keywords: Pediatrics, MR-Functional Imaging, Pulm …
T1- and T2-weighted MR images and PREFUL perfusion maps were visually assessed for semiquantitative Eichinger scores. Wilcoxon signed rank t …
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