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220 results

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Quoted phrase not found in phrase index: "Clear cell-sugar-tumor of the lung"
Page 1
Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management.
McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX. McCarthy C, et al. Lancet Respir Med. 2021 Nov;9(11):1313-1327. doi: 10.1016/S2213-2600(21)00228-9. Epub 2021 Aug 27. Lancet Respir Med. 2021. PMID: 34461049 Review.
Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal smooth muscle-like cells, resulting in cystic lung destruction. The invading cell in LAM ari …
Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising neoplasm of women, characterised by infiltration of the …
Single-Cell Transcriptomic Analysis Identifies a Unique Pulmonary Lymphangioleiomyomatosis Cell.
Guo M, Yu JJ, Perl AK, Wikenheiser-Brokamp KA, Riccetti M, Zhang EY, Sudha P, Adam M, Potter A, Kopras EJ, Giannikou K, Potter SS, Sherman S, Hammes SR, Kwiatkowski DJ, Whitsett JA, McCormack FX, Xu Y. Guo M, et al. Am J Respir Crit Care Med. 2020 Nov 15;202(10):1373-1387. doi: 10.1164/rccm.201912-2445OC. Am J Respir Crit Care Med. 2020. PMID: 32603599 Free PMC article.
Rationale: Lymphangioleiomyomatosis (LAM) is a metastatic neoplasm of reproductive-age women associated with mutations in tuberous sclerosis complex genes. LAM causes cystic remodeling of the lung and progressive respiratory failure. The sources and cellular characteristic …
Rationale: Lymphangioleiomyomatosis (LAM) is a metastatic neoplasm of reproductive-age women associated with mutations in tuberous sclerosis …
Lymphangioleiomyomatosis.
Doubková M, Štefániková M, Čan V, Merta Z, Svoboda M. Doubková M, et al. Klin Onkol. 2019 Fall;32(5):367-374. doi: 10.14735/amko2019367. Klin Onkol. 2019. PMID: 31610670 English.
RESULTS: The patients varied in terms of disease stage. The best predictors of prognosis were lung function parameters (forced vital capacity, forced expiratory volume in 1 second, and diffusing capacity for carbon monoxide). Four patients are currently being treate …
RESULTS: The patients varied in terms of disease stage. The best predictors of prognosis were lung function parameters (forced …
Emerging biomarkers of lymphangioleiomyomatosis.
Nijmeh J, El-Chemaly S, Henske EP. Nijmeh J, et al. Expert Rev Respir Med. 2018 Feb;12(2):95-102. doi: 10.1080/17476348.2018.1409622. Epub 2017 Dec 1. Expert Rev Respir Med. 2018. PMID: 29171770 Review.
Lymphangioleiomyomatosis (LAM) is a destructive lung disease affecting primarily women. LAM is caused by inactivating mutations in the tuberous sclerosis complex (TSC) genes, resulting in hyperactivation of mechanistic/mammalian target of rapamycin complex 1 (mTORC1). ...E …
Lymphangioleiomyomatosis (LAM) is a destructive lung disease affecting primarily women. LAM is caused by inactivating mutations in th …
Determinants of Progression and Mortality in Lymphangioleiomyomatosis.
Xu W, Yang C, Cheng C, Wang Y, Hu D, Huang J, He Y, Wang J, Chen K, Yang L, Zhou W, Zhang T, Liu S, Dai J, Meng S, Li X, Yang Y, Wang ST, Feng R, Zhang W, Zhang H, Wang L, Tian X, Xu KF. Xu W, et al. Chest. 2023 Jul;164(1):137-148. doi: 10.1016/j.chest.2023.02.026. Epub 2023 Feb 18. Chest. 2023. PMID: 36801466 Free article.
BACKGROUND: Lymphangioleiomyomatosis is a progressive diffuse cystic lung disease with approximately 85% survival at 10 years. The determinants of disease progression and mortality after the introduction of sirolimus therapy and vascular endothelial growth factor D (VEGF-D …
BACKGROUND: Lymphangioleiomyomatosis is a progressive diffuse cystic lung disease with approximately 85% survival at 10 years. The de …
Safety and Efficacy of Combined Resveratrol and Sirolimus in Lymphangioleiomyomatosis.
Gupta N, Zhang B, Zhou Y, McCormack FX, Ingledue R, Robbins N, Kopras EJ, McMahan S, Singla A, Swigris J, Cole AG, Holz MK. Gupta N, et al. Chest. 2023 May;163(5):1144-1155. doi: 10.1016/j.chest.2023.01.007. Epub 2023 Jan 13. Chest. 2023. PMID: 36642366 Free PMC article.
Secondary objectives included an assessment of the safety profile and the effect on lung function and health-related quality of life (HRQOL). Longitudinal change in outcome measures was assessed using linear mixed models. ...Pulmonary function parameters at study inclusion …
Secondary objectives included an assessment of the safety profile and the effect on lung function and health-related quality of life …
Multiple cystic lung disease.
Ferreira Francisco FA, Soares Souza A Jr, Zanetti G, Marchiori E. Ferreira Francisco FA, et al. Eur Respir Rev. 2015 Dec;24(138):552-64. doi: 10.1183/16000617.0046-2015. Eur Respir Rev. 2015. PMID: 26621970 Free PMC article. Review.
Multiple cystic lung disease represents a diverse group of uncommon disorders that can present a diagnostic challenge due to the increasing number of diseases associated with this presentation. ...The main diseases in this group that are discussed in this review are lympha …
Multiple cystic lung disease represents a diverse group of uncommon disorders that can present a diagnostic challenge due to the incr …
Recent advances in the pathobiology and clinical management of lymphangioleiomyomatosis.
Harari S, Spagnolo P, Cocconcelli E, Luisi F, Cottin V. Harari S, et al. Curr Opin Pulm Med. 2018 Sep;24(5):469-476. doi: 10.1097/MCP.0000000000000502. Curr Opin Pulm Med. 2018. PMID: 29927757 Review.
A randomized, double-blind, multicentre trial has confirmed the efficacy of sirolimus in stabilizing lung function, improving functional performance and quality of life, and reducing lymphatic manifestations in patients with LAM. ...However, additional studies are needed t …
A randomized, double-blind, multicentre trial has confirmed the efficacy of sirolimus in stabilizing lung function, improving functio …
Diffuse cystic lung diseases.
Ryu JH, Tian X, Baqir M, Xu K. Ryu JH, et al. Front Med. 2013 Sep;7(3):316-27. doi: 10.1007/s11684-013-0269-z. Epub 2013 May 11. Front Med. 2013. PMID: 23666611 Review.
Cyst in the lung is defined as a round parenchymal lucency with a well-defined thin wall (< 2 mm thickness). Focal or multifocal cystic lesions include blebs, bullae, pneumatoceles, congenital cystic lesions, traumatic lesions, and several infectious processes such as c …
Cyst in the lung is defined as a round parenchymal lucency with a well-defined thin wall (< 2 mm thickness). Focal or multifocal c …
Current management of lymphangioleiomyomatosis.
Taillé C, Borie R, Crestani B. Taillé C, et al. Curr Opin Pulm Med. 2011 Sep;17(5):374-8. doi: 10.1097/MCP.0b013e328349ac8c. Curr Opin Pulm Med. 2011. PMID: 21760507 Review.
In a recent 12 months controlled trial involving 89 patients with pulmonary LAM, sirolimus stopped lung function decline and improved quality of life and performance score. The protective effect of sirolimus was lost after treatment discontinuation, with a parallel …
In a recent 12 months controlled trial involving 89 patients with pulmonary LAM, sirolimus stopped lung function decline and improved …
220 results