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Table representation of search results timeline featuring number of search results per year.

Year Number of Results
2008 1
2009 1
2010 3
2011 2
2012 4
2013 5
2014 12
2015 7
2016 5
2017 4
2018 3
2019 7
2020 11
2021 7
2022 6
2023 1
2024 2

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63 results

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Page 1
Pathophysiology of Eosinophilic Esophagitis.
O'Shea KM, Aceves SS, Dellon ES, Gupta SK, Spergel JM, Furuta GT, Rothenberg ME. O'Shea KM, et al. Gastroenterology. 2018 Jan;154(2):333-345. doi: 10.1053/j.gastro.2017.06.065. Epub 2017 Jul 27. Gastroenterology. 2018. PMID: 28757265 Free PMC article. Review.
Loeys-Dietz syndrome.
Van Laer L, Dietz H, Loeys B. Van Laer L, et al. Adv Exp Med Biol. 2014;802:95-105. doi: 10.1007/978-94-007-7893-1_7. Adv Exp Med Biol. 2014. PMID: 24443023 Review.
Loeys-Dietz syndrome is an autosomal dominant aortic aneurysm syndrome characterized by multisystemic involvement. The most typical clinical triad includes hypertelorism, bifid uvula or cleft palate and aortic aneurysm with tortuosity. ...
Loeys-Dietz syndrome is an autosomal dominant aortic aneurysm syndrome characterized by multisystemic involvement. The …
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T. Skeik N, et al. Ann Vasc Surg. 2019 Oct;60:128-146. doi: 10.1016/j.avsg.2019.04.004. Epub 2019 Jun 12. Ann Vasc Surg. 2019. PMID: 31200053
BACKGROUND: Nonatherosclerotic abdominal arterial vasculopathies (NAVs), including mesenteric or renal artery dissection, aneurysm, stenosis, and vasculitis, are rare but have great clinical significance. Patients may present emergently with life-threatening complications …
BACKGROUND: Nonatherosclerotic abdominal arterial vasculopathies (NAVs), including mesenteric or renal artery dissection, aneurysm, stenosis …
Loeys-Dietz syndrome pathology and aspects of cardiovascular management: A systematic review.
Iqbal R, Alom S, BinSaeid J, Harky A. Iqbal R, et al. Vascular. 2021 Feb;29(1):3-14. doi: 10.1177/1708538120934582. Epub 2020 Jun 19. Vascular. 2021. PMID: 32559129
Loeys-Dietz syndrome is an autosomal dominant genetic disorder which is associated with significant and often crucial vascular manifestations. This review is aimed to examine current evidence on pathophysiology and management of Loeys-Dietz s …
Loeys-Dietz syndrome is an autosomal dominant genetic disorder which is associated with significant and often crucial v …
Surgery for congenital diseases of the aorta.
Cameron D. Cameron D. J Thorac Cardiovasc Surg. 2015 Feb;149(2 Suppl):S14-7. doi: 10.1016/j.jtcvs.2014.10.084. Epub 2014 Oct 23. J Thorac Cardiovasc Surg. 2015. PMID: 25726075 Free article. Review.
The indications for intervention in the aneurysm group are still in evolution but are clearly age- and lesion-dependant. Disorders such as Loeys-Dietz syndrome and Turner syndrome may deserve aggressive prophylactic surgery, as well as Marfan syndrome to a le …
The indications for intervention in the aneurysm group are still in evolution but are clearly age- and lesion-dependant. Disorders such as …
Marfan Syndrome and Related Disorders: 25 Years of Gene Discovery.
Verstraeten A, Alaerts M, Van Laer L, Loeys B. Verstraeten A, et al. Hum Mutat. 2016 Jun;37(6):524-31. doi: 10.1002/humu.22977. Epub 2016 Mar 14. Hum Mutat. 2016. PMID: 26919284 Review.
Marfan syndrome (MFS) is a rare, autosomal-dominant, multisystem disorder, presenting with skeletal, ocular, skin, and cardiovascular symptoms. Significant clinical overlap with other systemic connective tissue diseases, including Loeys-Dietz syndrome …
Marfan syndrome (MFS) is a rare, autosomal-dominant, multisystem disorder, presenting with skeletal, ocular, skin, and cardiovascular sympto …
TGF-β signalopathies as a paradigm for translational medicine.
Cannaerts E, van de Beek G, Verstraeten A, Van Laer L, Loeys B. Cannaerts E, et al. Eur J Med Genet. 2015 Dec;58(12):695-703. doi: 10.1016/j.ejmg.2015.10.010. Epub 2015 Oct 24. Eur J Med Genet. 2015. PMID: 26598797 Review.
The elucidation of the underlying pathogenic mechanisms has led to new treatment strategies, targeting the overactive TGF-beta pathway. Various clinical trials are currently investigating the potential new treatment options. A meta-analysis will contribute to a better unde …
The elucidation of the underlying pathogenic mechanisms has led to new treatment strategies, targeting the overactive TGF-beta pathway. Vari …
Are we ignoring the dilated thoracic aorta?
Castellano JM, Kovacic JC, Sanz J, Fuster V. Castellano JM, et al. Ann N Y Acad Sci. 2012 Apr;1254:164-174. doi: 10.1111/j.1749-6632.2012.06493.x. Ann N Y Acad Sci. 2012. PMID: 22548582 Review.
The extrapolation of data from one aneurysmal disease process to another is still ill-founded and potentially harmful. Clinical trials in TAA are required before medical therapies, such as beta-blockers, angiotensin-converting enzyme inhibitors, angiotensin receptor blocke …
The extrapolation of data from one aneurysmal disease process to another is still ill-founded and potentially harmful. Clinical trial …
Acute aortic dissection: microenvironmental regulation.
Bilfinger TV. Bilfinger TV. Med Sci Monit. 2010 Jul;16(7):RA143-6. Med Sci Monit. 2010. PMID: 20581788 Review.
With the exception of certain genetic connective tissue disorders, acute aortic dissections are still often thought to occur randomly. Very few of these events fall under the genetic category such as Marfan's disease, Ehlers Danlos type IV or Loeys Dietz s …
With the exception of certain genetic connective tissue disorders, acute aortic dissections are still often thought to occur randomly …
Adult surgical experience with Loeys-Dietz syndrome.
Williams JA, Hanna JM, Shah AA, Andersen ND, McDonald MT, Jiang YH, Wechsler SB, Zomorodi A, McCann RL, Hughes GC. Williams JA, et al. Ann Thorac Surg. 2015 Apr;99(4):1275-81. doi: 10.1016/j.athoracsur.2014.11.021. Epub 2015 Feb 10. Ann Thorac Surg. 2015. PMID: 25678502
BACKGROUND: Loeys-Dietz syndrome (LDS) results from mutations in receptors for the cytokine transforming growth factor-beta leading to aggressive aortic pathology sometimes accompanied by specific phenotypic features including bifid uvula, hypertelorism, clef …
BACKGROUND: Loeys-Dietz syndrome (LDS) results from mutations in receptors for the cytokine transforming growth factor- …
63 results