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Table representation of search results timeline featuring number of search results per year.

Year Number of Results
1968 1
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1985 3
1987 1
1988 1
1990 5
1991 6
1992 3
1993 4
1994 7
1995 6
1996 3
1997 6
1998 8
1999 11
2000 14
2001 23
2002 17
2003 18
2004 19
2005 15
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2007 24
2008 28
2009 17
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2013 56
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798 results

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Quoted phrase not found in phrase index: "Neuropathy with hearing impairment"
Page 1
Auditory neuropathy--neural and synaptic mechanisms.
Moser T, Starr A. Moser T, et al. Nat Rev Neurol. 2016 Mar;12(3):135-49. doi: 10.1038/nrneurol.2016.10. Epub 2016 Feb 19. Nat Rev Neurol. 2016. PMID: 26891769 Free article. Review.
Sensorineural hearing impairment is the most common form of hearing loss, and encompasses pathologies of the cochlea and the auditory nerve. Hearing impairment caused by abnormal neural encoding of sound stimuli despite preservation of se …
Sensorineural hearing impairment is the most common form of hearing loss, and encompasses pathologies of the coc …
Hidden Hearing Loss: A Disorder with Multiple Etiologies and Mechanisms.
C Kohrman D, Wan G, Cassinotti L, Corfas G. C Kohrman D, et al. Cold Spring Harb Perspect Med. 2020 Jan 2;10(1):a035493. doi: 10.1101/cshperspect.a035493. Cold Spring Harb Perspect Med. 2020. PMID: 30617057 Free PMC article. Review.
Hidden hearing loss (HHL), a recently described auditory disorder, has been proposed to affect auditory neural processing and hearing acuity in subjects with normal audiometric thresholds, particularly in noisy environments. In contrast to central auditory pr …
Hidden hearing loss (HHL), a recently described auditory disorder, has been proposed to affect auditory neural processing and …
Delineating Wolfram-like syndrome: A systematic review and discussion of the WFS1-associated disease spectrum.
de Muijnck C, Brink JBT, Bergen AA, Boon CJF, van Genderen MM. de Muijnck C, et al. Surv Ophthalmol. 2023 Jul-Aug;68(4):641-654. doi: 10.1016/j.survophthal.2023.01.012. Epub 2023 Feb 9. Surv Ophthalmol. 2023. PMID: 36764396 Free article. Review.
The most common phenotype consisted of the combination of optic atrophy (87%) and hearing impairment (94%). Diabetes mellitus was seen in 44% of the patients. ...Patients with missense mutations in WFS1 had a lower number of clinical manifestations, less chance of d …
The most common phenotype consisted of the combination of optic atrophy (87%) and hearing impairment (94%). Diabetes mellitus …
Auditory Neuropathy/Auditory Synaptopathy.
Hood LJ. Hood LJ. Otolaryngol Clin North Am. 2021 Dec;54(6):1093-1100. doi: 10.1016/j.otc.2021.07.004. Epub 2021 Sep 15. Otolaryngol Clin North Am. 2021. PMID: 34535280 Review.
Patients with auditory neuropathy (AN)/auditory synaptopathy (AS) present unique evaluation and management challenges. ...
Patients with auditory neuropathy (AN)/auditory synaptopathy (AS) present unique evaluation and management challenges. ...
Auditory neuropathy.
Starr A, Rance G. Starr A, et al. Handb Clin Neurol. 2015;129:495-508. doi: 10.1016/B978-0-444-62630-1.00028-7. Handb Clin Neurol. 2015. PMID: 25726287 Review.
These include: (1) speech perception; (2) localizing a sound's origin in space; and (3) identifying sounds in background noise. Auditory neuropathy (AN) is a consequence of: (1) presynaptic disorders affecting inner hair cell ribbon synapses; (2) postsynaptic disorders of …
These include: (1) speech perception; (2) localizing a sound's origin in space; and (3) identifying sounds in background noise. Auditory …
Audiometry and other hearing tests.
Davies RA. Davies RA. Handb Clin Neurol. 2016;137:157-76. doi: 10.1016/B978-0-444-63437-5.00011-X. Handb Clin Neurol. 2016. PMID: 27638069 Review.
Hearing tests of the peripheral auditory system are well established and the pure-tone audiogram is generally regarded as the screening test of choice in adults. It allows the distinction to be made between conductive, i.e., outer- and middle-ear, and sensorineural, i.e., …
Hearing tests of the peripheral auditory system are well established and the pure-tone audiogram is generally regarded as the screeni …
Cochlea and auditory nerve.
Eggermont JJ. Eggermont JJ. Handb Clin Neurol. 2019;160:437-449. doi: 10.1016/B978-0-444-64032-1.00029-1. Handb Clin Neurol. 2019. PMID: 31277867 Review.
Presence of CM and absence of CAPs are the diagnostic hallmarks of auditory neuropathy. Increased and prolonged SPs are often found in Meniere's disease but are too often in the normal range to be diagnostic. When including NAP waveforms, Meniere's disease can be different …
Presence of CM and absence of CAPs are the diagnostic hallmarks of auditory neuropathy. Increased and prolonged SPs are often found i …
A Review of Posterior Fossa Lesions.
Bray HN, Sappington JM. Bray HN, et al. Mo Med. 2022 Nov-Dec;119(6):553-558. Mo Med. 2022. PMID: 36588644 Free PMC article. Review.
Posterior fossa lesions can occur in patients of all ages. Patients present with subtle findings of hearing loss, tinnitus, headache, cranial neuropathies, imbalance, vertigo, nausea, and vomiting depending on the location and type of lesion. The presentation …
Posterior fossa lesions can occur in patients of all ages. Patients present with subtle findings of hearing loss, tinnitus, he …
Endolymphatic sac tumors.
Wick CC, Manzoor NF, Semaan MT, Megerian CA. Wick CC, et al. Otolaryngol Clin North Am. 2015 Apr;48(2):317-30. doi: 10.1016/j.otc.2014.12.006. Epub 2015 Jan 31. Otolaryngol Clin North Am. 2015. PMID: 25650230 Review.
Endolymphatic sac tumors (ELST) are slow-growing, locally aggressive, low-grade malignancies that originate from the epithelium of the endolymphatic duct and sac. ELST often present with sensorineural hearing loss, tinnitus, and vertigo, which may mimic Meniere dise …
Endolymphatic sac tumors (ELST) are slow-growing, locally aggressive, low-grade malignancies that originate from the epithelium of the endol …
Auditory neuropathy/dyssynchrony revisited.
Menten K, Van Eynde C, Desloovere C, Wouters J. Menten K, et al. B-ENT. 2014;10(2):105-12. B-ENT. 2014. PMID: 25090808 Review.
Auditory neuropathy/dyssynchrony (AN/AD) is a relatively, recently described diagnostic term. ...
Auditory neuropathy/dyssynchrony (AN/AD) is a relatively, recently described diagnostic term. ...
798 results