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Quoted phrase not found in phrase index: "Primary ciliary dyskinesia 22"
Page 1
Current and Future Treatments in Primary Ciliary Dyskinesia.
Paff T, Omran H, Nielsen KG, Haarman EG. Paff T, et al. Int J Mol Sci. 2021 Sep 11;22(18):9834. doi: 10.3390/ijms22189834. Int J Mol Sci. 2021. PMID: 34575997 Free PMC article. Review.
Primary ciliary dyskinesia (PCD) is a rare genetic ciliopathy in which mucociliary clearance is disturbed by the abnormal motion of cilia or there is a severe reduction in the generation of multiple motile cilia. ...Treatment guidelines are largely based on c …
Primary ciliary dyskinesia (PCD) is a rare genetic ciliopathy in which mucociliary clearance is disturbed by the abnorm …
Safety and efficacy of the epithelial sodium channel blocker idrevloride in people with primary ciliary dyskinesia (CLEAN-PCD): a multinational, phase 2, randomised, double-blind, placebo-controlled crossover trial.
Ringshausen FC, Shapiro AJ, Nielsen KG, Mazurek H, Pifferi M, Donn KH, van der Eerden MM, Loebinger MR, Zariwala MA, Leigh MW, Knowles MR, Ferkol TW; CLEAN-PCD investigators and study team. Ringshausen FC, et al. Lancet Respir Med. 2024 Jan;12(1):21-33. doi: 10.1016/S2213-2600(23)00226-6. Epub 2023 Aug 31. Lancet Respir Med. 2024. PMID: 37660715 Clinical Trial.
BACKGROUND: Mucociliary clearance is dysfunctional in people with primary ciliary dyskinesia, resulting in the accumulation of dehydrated mucus in the airways that is difficult to clear. ...Larger, longer clinical studies are warranted to explore the p …
BACKGROUND: Mucociliary clearance is dysfunctional in people with primary ciliary dyskinesia, resulting in the accumula …
Clinical and genetic spectrum of primary ciliary dyskinesia in Chinese patients: a systematic review.
Peng B, Gao YH, Xie JQ, He XW, Wang CC, Xu JF, Zhang GJ. Peng B, et al. Orphanet J Rare Dis. 2022 Jul 19;17(1):283. doi: 10.1186/s13023-022-02427-1. Orphanet J Rare Dis. 2022. PMID: 35854386 Free PMC article. Review.
BACKGROUND: Primary ciliary dyskinesia (PCD) represents a highly heterogenous disorder with extensive clinical and genetic patterns among populations of different geographic location and ethnic origin. However, data about Chinese patients are limited. …
BACKGROUND: Primary ciliary dyskinesia (PCD) represents a highly heterogenous disorder with extensive clinical a …
Primary ciliary dyskinesia: A multicenter survey on clinical practice and patient management in Italy.
Ullmann N, Santamaria F, Allegorico A, Fainardi V, Borrelli M, Ferraro VA, Proietti E, Parisi GF, Romagnoli V, Lucca F, Gallucci M, Mappa L, Lelli M, Amato D, Petrarca L, Cimino G, Sacco O, Calogero C, Patria MF, Acquafredda A, Ferlisi A, Maschio M, Kantar A, Cutrera R. Ullmann N, et al. Pediatr Pulmonol. 2023 Apr;58(4):1127-1135. doi: 10.1002/ppul.26303. Epub 2023 Jan 9. Pediatr Pulmonol. 2023. PMID: 36588099
INTRODUCTION: There are no recent data on primary ciliary dyskinesia (PCD) distribution, diagnosis and treatment in Italy. ...Age at diagnosis was between 4 and 8 years in 45% of the centers, <3 years in three centers. Nasal nitric oxide, transmission elec …
INTRODUCTION: There are no recent data on primary ciliary dyskinesia (PCD) distribution, diagnosis and treatment in Ita …
Treatment response to pulmonary exacerbation in primary ciliary dyskinesia.
Gatt D, Shaw M, Waters V, Kritzinger F, Solomon M, Dell S, Ratjen F. Gatt D, et al. Pediatr Pulmonol. 2023 Oct;58(10):2857-2864. doi: 10.1002/ppul.26599. Epub 2023 Jul 14. Pediatr Pulmonol. 2023. PMID: 37449771
INTRODUCTION: Pulmonary exacerbation (Pex) are common in pediatric primary ciliary dyskinesia (PCD), however changes in forced expiratory volume in 1 s precent predicted (FEV1pp) during Pex are not well described. ...Nonresponse was associated with lower medi …
INTRODUCTION: Pulmonary exacerbation (Pex) are common in pediatric primary ciliary dyskinesia (PCD), however changes in …
Nasal nitric oxide levels in primary ciliary dyskinesia, cystic fibrosis and healthy children.
Güney E, Emiralioğlu N, Cinel G, Yalçın E, Doğru D, Kiper N, Özçelik HU. Güney E, et al. Turk J Pediatr. 2019;61(1):20-25. doi: 10.24953/turkjped.2019.01.004. Turk J Pediatr. 2019. PMID: 31559717 Free article. Clinical Trial.
Guney E, Emiralioglu N, Cinel G, Yalcin E, Dogru D, Kiper N, Ozcelik HU. Nasal nitric oxide levels in primary ciliary dyskinesia, cystic fibrosis and healthy children. Turk J Pediatr 2019; 61: 20-25. Primary ciliary dyskinesia (PCD) is a …
Guney E, Emiralioglu N, Cinel G, Yalcin E, Dogru D, Kiper N, Ozcelik HU. Nasal nitric oxide levels in primary ciliary dyski …
Reducing exacerbations in children and adults with primary ciliary dyskinesia using erdosteine and/or azithromycin therapy (REPEAT trial): study protocol for a multicentre, double-blind, double-dummy, 22 partial factorial, randomised controlled trial.
Chang AB, Morgan LC, Duncan EL, Chatfield MD, Schultz A, Leo PJ, McCallum GB, McInerney-Leo AM, McPhail SM, Zhao Y, Kruljac C, Smith-Vaughan HC, Morris PS, Marchant JM, Yerkovich ST, Cook AL, Wurzel D, Versteegh L, O'Farrell H, McElrea MS, Fletcher S, D'Antoine H, Stroil-Salama E, Robinson PJ, Grimwood K. Chang AB, et al. BMJ Open Respir Res. 2022 May;9(1):e001236. doi: 10.1136/bmjresp-2022-001236. BMJ Open Respir Res. 2022. PMID: 35534039 Free PMC article.
INTRODUCTION: Primary ciliary dyskinesia (PCD) is a rare, progressive, inherited ciliopathic disorder, which is incurable and frequently complicated by the development of bronchiectasis. ...TRIAL REGISTRATION NUMBER: ACTRN12619000564156....
INTRODUCTION: Primary ciliary dyskinesia (PCD) is a rare, progressive, inherited ciliopathic disorder, which is incurab …
Lung clearance index predicts pulmonary exacerbations in individuals with primary ciliary dyskinesia: a multicentre cohort study.
Singer F, Schlegtendal A, Nyilas S, Vermeulen F, Boon M, Koerner-Rettberg C. Singer F, et al. Thorax. 2021 Jul;76(7):681-688. doi: 10.1136/thoraxjnl-2020-215504. Epub 2021 Jan 27. Thorax. 2021. PMID: 33504569
BACKGROUND: Lung clearance index (LCI) is a promising lung function outcome in individuals with primary ciliary dyskinesia (PCD). The impact of events clinically important for individuals with PCD, such as pulmonary exacerbations, on LCI is unknown. ...The as …
BACKGROUND: Lung clearance index (LCI) is a promising lung function outcome in individuals with primary ciliary dyskinesia …
Changing epidemiology of non-cystic fibrosis bronchiectasis.
Bahçeci S, Karaman S, Nacaroğlu HT, Yazıcı S, Girit S, Ünsal-Karkıner Ş, Can D. Bahçeci S, et al. Turk J Pediatr. 2016;58(1):19-26. doi: 10.24953/turkjped.2016.01.003. Turk J Pediatr. 2016. PMID: 27922232 Free article.
Patients who admitted to Behcet Uz Children Hospital between 2005 and 2015 (n=110) were retrospectively examined. The etiology of bronchiectasis was detected as; primary ciliary dyskinesia 26.4%, protracted bacterial bronchitis 22.8%, primary im …
Patients who admitted to Behcet Uz Children Hospital between 2005 and 2015 (n=110) were retrospectively examined. The etiology of bronchiect …
Middle ear ventilation in children with primary ciliary dyskinesia.
Wolter NE, Dell SD, James AL, Campisi P. Wolter NE, et al. Int J Pediatr Otorhinolaryngol. 2012 Nov;76(11):1565-8. doi: 10.1016/j.ijporl.2012.07.011. Epub 2012 Aug 9. Int J Pediatr Otorhinolaryngol. 2012. PMID: 22883987
OBJECTIVE: Otitis media with effusion (OME) in children with primary ciliary dyskinesia (PCD) is recurrent and persistent and presents a complex clinical problem for otolaryngologists. ...Hearing thresholds improved to normal (<25 dB HL) in 80% ears …
OBJECTIVE: Otitis media with effusion (OME) in children with primary ciliary dyskinesia (PCD) is recurrent and persiste …
27 results