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Quoted phrase not found in phrase index: "Spongiform encephalopathy with neuropsychiatric features"
Page 1
Behavioral and psychiatric symptoms in prion disease.
Thompson A, MacKay A, Rudge P, Lukic A, Porter MC, Lowe J, Collinge J, Mead S. Thompson A, et al. Am J Psychiatry. 2014 Mar;171(3):265-74. doi: 10.1176/appi.ajp.2013.12111460. Am J Psychiatry. 2014. PMID: 24585329 Review.
The prion diseases are rare neurodegenerative conditions that cause complex and highly variable neuropsychiatric syndromes, often with remarkably rapid progression. Prominent behavioral and psychiatric symptoms have been recognized since these diseases …
The prion diseases are rare neurodegenerative conditions that cause complex and highly variable neuropsychiatric syndro …
Clinical profiles and ethnic heterogeneity of sporadic fatal insomnia.
Chen Z, Chu M, Zhang J, Kong Y, Xie K, Cui Y, Ye H, Liu L, Li J, Wang L, Wu L. Chen Z, et al. Eur J Neurol. 2023 Apr;30(4):813-822. doi: 10.1111/ene.15676. Epub 2023 Jan 23. Eur J Neurol. 2023. PMID: 36617541
RESULTS: We identified 44 sFI and 157 FFI cases. The prevalence of sleep-related, neuropsychiatric, and autonomic symptoms among the sFI patients were 65.9%, 100.0%, and 43.2%, respectively. ...The Asian sFI patients had a higher proportion of males and positivity for cere …
RESULTS: We identified 44 sFI and 157 FFI cases. The prevalence of sleep-related, neuropsychiatric, and autonomic symptoms among the …
Characteristics of established and proposed sporadic Creutzfeldt-Jakob disease variants.
Appleby BS, Appleby KK, Crain BJ, Onyike CU, Wallin MT, Rabins PV. Appleby BS, et al. Arch Neurol. 2009 Feb;66(2):208-15. doi: 10.1001/archneurol.2008.533. Arch Neurol. 2009. PMID: 19204157
BACKGROUND: The classic Creutzfeldt-Jakob disease (CJD), Heidenhain, and Oppenheimer-Brownell variants are sporadic CJD (sCJD) phenotypes frequently described in the literature, but many cases present with neuropsychiatric symptoms, suggesting that there may be additional …
BACKGROUND: The classic Creutzfeldt-Jakob disease (CJD), Heidenhain, and Oppenheimer-Brownell variants are sporadic CJD (sCJD) phenotypes fr …
Genome-wide association study of behavioural and psychiatric features in human prion disease.
Thompson AG, Uphill J, Lowe J, Porter MC, Lukic A, Carswell C, Rudge P, MacKay A, Collinge J, Mead S. Thompson AG, et al. Transl Psychiatry. 2015 Apr 21;5(4):e552. doi: 10.1038/tp.2015.42. Transl Psychiatry. 2015. PMID: 25897833 Free PMC article.
Prion diseases are rare neurodegenerative conditions causing highly variable clinical syndromes, which often include prominent neuropsychiatric symptoms. ...We would encourage others to acquire phenotype data in independent cohorts of patients with prion …
Prion diseases are rare neurodegenerative conditions causing highly variable clinical syndromes, which often include prominent …
Pellagra encephalopathy as a differential diagnosis for Creutzfeldt-Jakob disease.
Kapas I, Majtenyi K, Törö K, Keller E, Voigtländer T, Kovacs GG. Kapas I, et al. Metab Brain Dis. 2012 Jun;27(2):231-5. doi: 10.1007/s11011-012-9308-8. Epub 2012 Apr 27. Metab Brain Dis. 2012. PMID: 22535301
In the present study we evaluated cases referred as suspected Creutzfeldt-Jakob disease (CJD). Five out of 59 without prion disease showed neuropathological features of pellagra encephalopathy with widespread chromatolytic neurons (age range 40-48 years at de …
In the present study we evaluated cases referred as suspected Creutzfeldt-Jakob disease (CJD). Five out of 59 without prion disease s …
The classic and variant forms of Creutzfeldt-Jakob disease.
Irani DN. Irani DN. Semin Clin Neuropsychiatry. 2003 Jan;8(1):71-9. doi: 10.1053/scnp.2003.50001. Semin Clin Neuropsychiatry. 2003. PMID: 12567334 Review.
Transmissible spongiform encephalopathies (TSEs), also known as prion diseases, are a group of progressive neurodegenerative disorders that affect both animals and humans. These diseases take part of their name from a striking and common neuropathologi …
Transmissible spongiform encephalopathies (TSEs), also known as prion diseases, are a group of progressive neurodegener …
Low mood, visual hallucinations, and falls - heralding the onset of rapidly progressive probable sporadic Creutzfeldt-Jakob disease in a 73-year old: a case report.
Klotz DM, Penfold RS. Klotz DM, et al. J Med Case Rep. 2018 May 8;12(1):128. doi: 10.1186/s13256-018-1649-4. J Med Case Rep. 2018. PMID: 29734943 Free PMC article.
Following admission, she had rapid cognitive decline and developed florid and progressive neurological signs; a diagnosis of prion disease was suspected. A lumbar puncture was performed; cerebrospinal fluid was positive for 14-3-3 protein, real-time quaking-induced …
Following admission, she had rapid cognitive decline and developed florid and progressive neurological signs; a diagnosis of prion di …
Inherited prion disease with an alanine to valine mutation at codon 117 in the prion protein gene.
Mallucci GR, Campbell TA, Dickinson A, Beck J, Holt M, Plant G, de Pauw KW, Hakin RN, Clarke CE, Howell S, Davies-Jones GA, Lawden M, Smith CM, Ince P, Ironside JW, Bridges LR, Dean A, Weeks I, Collinge J. Mallucci GR, et al. Brain. 1999 Oct;122 ( Pt 10):1823-37. doi: 10.1093/brain/122.10.1823. Brain. 1999. PMID: 10506086
Molecular genetic studies have enabled the classification of this disease at the molecular level as one of the group of inherited prion diseases, with the substitution of valine for alanine at codon 117 of the prion protein gene (PRNP). ...Indeed, inhe …
Molecular genetic studies have enabled the classification of this disease at the molecular level as one of the group of inherited prion …