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2001 1
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Page 1
Clinical practice: the management of hyperammonemia.
Häberle J. Häberle J. Eur J Pediatr. 2011 Jan;170(1):21-34. doi: 10.1007/s00431-010-1369-2. Epub 2010 Dec 17. Eur J Pediatr. 2011. PMID: 21165747 Free article. Review.
Hyperammonemia is a life-threatening condition which can affect patients at any age. ...Likewise, the immediate start of appropriate therapy is of utmost importance. This review focuses on a better understanding of factors leading to ammonia elevations and on practi
Hyperammonemia is a life-threatening condition which can affect patients at any age. ...Likewise, the immediate start of appropriate
Initial management of acute hyperammonemia in pediatrics.
Eiroa H, Durand C, Szlago M, Pereyra M, Nuñez M, Guelbert N, Pacheco G, Kleppe S. Eiroa H, et al. Arch Argent Pediatr. 2023 Jun 1;121(3):e202202614. doi: 10.5546/aap.2022-02614.eng. Epub 2022 Oct 27. Arch Argent Pediatr. 2023. PMID: 36287611 Free article. English, Spanish.
Hyperammonemia is a medical emergency. There are no publications regarding the availability of resources, supplies, and knowledge necessary for the initial management of hyperammonemia by pediatricians in Argentina; however, according to the authors' experience, the
Hyperammonemia is a medical emergency. There are no publications regarding the availability of resources, supplies, and knowledge nec
Hereditary hyperferritinemia-cataract syndrome in three Czech families: molecular genetic testing and clinical implications.
Moravikova J, Honzik T, Jadvidzakova E, Zdrahalova K, Kremlikova Pourova R, Korbasova M, Liskova P, Dudakova L. Moravikova J, et al. J AAPOS. 2020 Dec;24(6):352.e1-352.e5. doi: 10.1016/j.jaapos.2020.07.014. Epub 2020 Nov 19. J AAPOS. 2020. PMID: 33221470
One individual, aged 43 years, underwent phlebotomy; another, aged 8.5 years, was treated with the iron chelator deferasirox, leading to life-threatening acute hyperammonemia, without severe liver injury. CONCLUSIONS: Lack of family history does not exclude HHCS, be …
One individual, aged 43 years, underwent phlebotomy; another, aged 8.5 years, was treated with the iron chelator deferasirox, leading to lif …
Extracorporeal treatment for valproic acid poisoning: systematic review and recommendations from the EXTRIP workgroup.
Ghannoum M, Laliberté M, Nolin TD, MacTier R, Lavergne V, Hoffman RS, Gosselin S; EXTRIP Workgroup. Ghannoum M, et al. Clin Toxicol (Phila). 2015 Jun;53(5):454-65. doi: 10.3109/15563650.2015.1035441. Clin Toxicol (Phila). 2015. PMID: 25950372 Review.
The workgroup concluded that VPA is moderately dialyzable (level of evidence = B) and made the following recommendations: ECTR is recommended in severe VPA poisoning (1D); recommendations for ECTR include a VPA concentration > 1300 mg/L (9000 mumol/L)(1D), the presence of cere …
The workgroup concluded that VPA is moderately dialyzable (level of evidence = B) and made the following recommendations: ECTR is recommende …
Peripheral venous route for administration of ammonul infusion for treatment of acute hyperammonemia. An experience from a tertiary center in Saudi Arabia.
Alhashem AM, Salih RM, Al-Aqeel AI, Mohamed S. Alhashem AM, et al. Saudi Med J. 2020 Jan;41(1):98-101. doi: 10.15537/smj.2020.1.24760. Saudi Med J. 2020. PMID: 31915802 Free PMC article.
All children less than 16 years of age admitted between December 2015 and October 2018 with hyperammonemia and received Ammonul infusion for treatment were recruited. Results: Twenty-one patients received the Ammonul infusion. They were admitted 58 times with acute
All children less than 16 years of age admitted between December 2015 and October 2018 with hyperammonemia and received Ammonul infus …
Influence of implementing a protocol for an intravenously administered ammonia scavenger on the management of acute hyperammonemia in a pediatric intensive care unit.
Brossier D, Goyer I, Ziani L, Marquis C, Mitchell G, Ozanne B, Jouvet P. Brossier D, et al. J Inherit Metab Dis. 2019 Jan;42(1):77-85. doi: 10.1002/jimd.12029. J Inherit Metab Dis. 2019. PMID: 30740742
The purpose of the study was to evaluate the influence of establishing a protocol for the use of combined sodium benzoate and sodium phenylacetate (SBSP) (Ammonul) to treat acute hyperammonemia. This was a retrospective, single-center study in a 24-bed medical and s …
The purpose of the study was to evaluate the influence of establishing a protocol for the use of combined sodium benzoate and sodium phenyla …
Gene Therapy for Treatment of Chronic Hyperammonemia in a Rat Model of Hepatic Encephalopathy.
Espíritu-Ramírez P, Ortega-Balderas NY, Sevilla-Tapia L, Montiel-Martínez AG, Pastor-Flores AR, Palomares LA, Torres-Vega MA. Espíritu-Ramírez P, et al. Ann Hepatol. 2018 Oct 16;17(6):1026-1034. doi: 10.5604/01.3001.0012.7203. Ann Hepatol. 2018. PMID: 30600292 Free article.
Existing therapies are deficient and alternative treatments are needed. We have shown that gene therapy with a baculovirus vector containing the glutamine synthetase (Bac-GS) gene is efficient for reducing ammonia levels in an acute hyperammonemia rat …
Existing therapies are deficient and alternative treatments are needed. We have shown that gene therapy with a baculovirus vec …
Feasibility of adjunct therapeutic hypothermia treatment for hyperammonemia and encephalopathy due to urea cycle disorders and organic acidemias.
Lichter-Konecki U, Nadkarni V, Moudgil A, Cook N, Poeschl J, Meyer MT, Dimmock D, Baumgart S. Lichter-Konecki U, et al. Mol Genet Metab. 2013 Aug;109(4):354-9. doi: 10.1016/j.ymgme.2013.05.014. Epub 2013 May 29. Mol Genet Metab. 2013. PMID: 23791307
Nutritional support, intravenous alternative pathway therapy, and dialysis are used to treat severe hyperammonemia associated with UCDs and nutritional support and dialysis are used to treat severe hyperammonemia in OAs. ...Animal experiments and small clinic …
Nutritional support, intravenous alternative pathway therapy, and dialysis are used to treat severe hyperammonemia associated …
Staged transcatheter treatment of portal hypoplasia and congenital portosystemic shunts in children.
Bruckheimer E, Dagan T, Atar E, Schwartz M, Kachko L, Superina R, Amir G, Shapiro R, Birk E. Bruckheimer E, et al. Cardiovasc Intervent Radiol. 2013 Dec;36(6):1580-1585. doi: 10.1007/s00270-013-0581-7. Epub 2013 Feb 22. Cardiovasc Intervent Radiol. 2013. PMID: 23435744
PURPOSE: Congenital portosystemic shunts (CPSS) with portal venous hypoplasia cause hyperammonemia. Acute shunt closure results in portal hypertension. A transcatheter method of staged shunt reduction to afford growth of portal vessels followed by shunt closure is r …
PURPOSE: Congenital portosystemic shunts (CPSS) with portal venous hypoplasia cause hyperammonemia. Acute shunt closure result …
Heliox use in the treatment of acute hyperammonemia.
Barr J, Eshel G, Chen-Levy Z, Lahat E. Barr J, et al. J Child Neurol. 2001 Jun;16(6):456-8. doi: 10.1177/088307380101600616. J Child Neurol. 2001. PMID: 11417617
The objective of this study was to evaluate a new method for the treatment of acute hyperammonemia with a helium-oxygen mixture (heliox). We conducted a prospective, randomized, controlled study of male Sprague-Dawley rats. ...Further studies are required to evaluat …
The objective of this study was to evaluate a new method for the treatment of acute hyperammonemia with a helium-oxygen mixtur …
11 results