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Treatment of Hereditary Angioedema.
Caballero T. Caballero T. J Investig Allergol Clin Immunol. 2021 Feb;31(1):1-16. doi: 10.18176/jiaci.0653. J Investig Allergol Clin Immunol. 2021. PMID: 33602658 Free article. Review.
Hereditary angioedema due to C1-esterase inhibitor deficiency (C1-INH-HAE) is a rare autosomal dominant disease. In the last decade, new drugs and new indications for old drugs have played a role in the management of C1-INH-HAE. ...Increased knowledge of the pathoph …
Hereditary angioedema due to C1-esterase inhibitor deficiency (C1-INH-HAE) is a rare autosomal dominant disease. In the last d …
Novelties in the Diagnosis and Treatment of Angioedema.
Cicardi M, Suffritti C, Perego F, Caccia S. Cicardi M, et al. J Investig Allergol Clin Immunol. 2016;26(4):212-21; quiz two pages after page 221. doi: 10.18176/jiaci.0087. J Investig Allergol Clin Immunol. 2016. PMID: 27470642 Free article. Review.
Histamine is the mediator in acquired angioedema of unknown etiology (idiopathic histaminergic acquired angioedema), whereas in other forms the main mediator is bradykinin. Angioedema can be caused by C1-inhibitor deficiency (C1-INH-hereditary angioedema and C1-INH-acquire …
Histamine is the mediator in acquired angioedema of unknown etiology (idiopathic histaminergic acquired angioedema), whereas in other forms …
Diagnosis and treatment of hereditary angioedema.
Canonica GW, Rossi O. Canonica GW, et al. Panminerva Med. 2012 Sep;54(3):241-53. Panminerva Med. 2012. PMID: 22801442 Review.
A third type of HAE has a similar presentation, but is not due to C1-INH deficiency or impairment. Some patients with type III HAE carry mutations in the coagulation factor XII gene that do not alter factor XII plasma levels but markedly increas …
A third type of HAE has a similar presentation, but is not due to C1-INH deficiency or impairment. Some patients with type III HAE ca …
Current and emerging biologics for the treatment of hereditary angioedema.
Perego F, Wu MA, Valerieva A, Caccia S, Suffritti C, Zanichelli A, Bergamaschini L, Cicardi M. Perego F, et al. Expert Opin Biol Ther. 2019 Jun;19(6):517-526. doi: 10.1080/14712598.2019.1595581. Epub 2019 Mar 26. Expert Opin Biol Ther. 2019. PMID: 30912460 Free article. Review.
INTRODUCTION: Hereditary angioedema due to C1-INH deficiency (C1-INH-HAE) is a rare disease with unpredictable, self-limiting and localized swelling episodes involving the cutaneous and subcutaneous tissues. In the last decade, the spectrum of the possibilities to c …
INTRODUCTION: Hereditary angioedema due to C1-INH deficiency (C1-INH-HAE) is a rare disease with unpredictable, self-limiting …
Hereditary and acquired C1-inhibitor-dependent angioedema: from pathophysiology to treatment.
Zeerleder S, Levi M. Zeerleder S, et al. Ann Med. 2016;48(4):256-67. doi: 10.3109/07853890.2016.1162909. Epub 2016 Mar 26. Ann Med. 2016. PMID: 27018196 Review.
A decreased activity of C1-inhibitor is the hallmark of C1-INH-HAE (types 1 and 2) due to a mutation in the C1-inhibitor gene, whereas the deficiency in C1-inhibitor in C1-INH-AAE is the result of autoimmune phenomena. ...Submucosal edema formation in hereditary and acquir …
A decreased activity of C1-inhibitor is the hallmark of C1-INH-HAE (types 1 and 2) due to a mutation in the C1-inhibitor gene, whereas the …
Hereditary angioedema: an update on causes, manifestations and treatment.
Longhurst HJ, Bork K. Longhurst HJ, et al. Br J Hosp Med (Lond). 2019 Jul 2;80(7):391-398. doi: 10.12968/hmed.2019.80.7.391. Br J Hosp Med (Lond). 2019. PMID: 31283393 Free article. Review.
Hereditary angioedema is a rare genetic disorder caused by deficiency of C1 esterase inhibitor (C1-INH) and characterized by recurrent episodes of severe swelling that affect the limbs, face, intestinal tract and airway. ...Hereditary angioedema attacks are mediated by bra …
Hereditary angioedema is a rare genetic disorder caused by deficiency of C1 esterase inhibitor (C1-INH) and characterized by recurren …
Long-term Prophylaxis with Androgens in the management of Hereditary Angioedema (HAE) in emerging countries.
Guo Y, Zhang H, Lai H, Wang H, Chong-Neto HJ, Valle SOR, Zhu R. Guo Y, et al. Orphanet J Rare Dis. 2022 Nov 2;17(1):399. doi: 10.1186/s13023-022-02536-x. Orphanet J Rare Dis. 2022. PMID: 36324138 Free PMC article. Review.
Hereditary angioedema (HAE) is a rare autosomal dominant genetic disease characterized by repetitive subcutaneous or submucosal angioedema, activation of the kinin system, and increased vascular permeability. C1-inhibitor (C1-INH) deficiency, the main mechanism of H …
Hereditary angioedema (HAE) is a rare autosomal dominant genetic disease characterized by repetitive subcutaneous or submucosal angio …
Hereditary Angioedema with Normal C1 Inhibitor: Update on Evaluation and Treatment.
Magerl M, Germenis AE, Maas C, Maurer M. Magerl M, et al. Immunol Allergy Clin North Am. 2017 Aug;37(3):571-584. doi: 10.1016/j.iac.2017.04.004. Immunol Allergy Clin North Am. 2017. PMID: 28687110 Review.
Its clinical appearance resembles HAE types I and II, which are caused by mutations that result in a deficiency of C1 inhibitor (C1-INH). In patients with the new form of HAE, C1-INH plasma levels and function values are normal, so it's termed HAE with normal C1-INH (HAE-n …
Its clinical appearance resembles HAE types I and II, which are caused by mutations that result in a deficiency of C1 inhibitor (C1-I …
Molecular mechanisms of thrombus formation in ischemic stroke: novel insights and targets for treatment.
Stoll G, Kleinschnitz C, Nieswandt B. Stoll G, et al. Blood. 2008 Nov 1;112(9):3555-62. doi: 10.1182/blood-2008-04-144758. Epub 2008 Aug 1. Blood. 2008. PMID: 18676880 Free article. Review.
In ischemic stroke, treatment options are limited. Therapeutic thrombolysis is restricted to the first few hours after stroke, and the utility of current platelet aggregation inhibitors, including GPIIb/IIIa receptor antagonists, and anticoagulants is counterbalanced by th …
In ischemic stroke, treatment options are limited. Therapeutic thrombolysis is restricted to the first few hours after stroke, and th …
Treatment of hereditary and acquired thrombophilic disorders.
Baker WF Jr, Bick RL. Baker WF Jr, et al. Semin Thromb Hemost. 1999;25(4):387-406. doi: 10.1055/s-2007-994942. Semin Thromb Hemost. 1999. PMID: 10548072 Review.
The treatment of hereditary and acquired thrombophilic disorders is based on an understanding of the disease pathophysiology, prevalence, associated morbidity and mortality, and available therapeutic options. ...The underlying etiologies are less well-defined; howev …
The treatment of hereditary and acquired thrombophilic disorders is based on an understanding of the disease pathophysiology, prevale …
24 results