Proia RL - Search Results

1

Kidney sulfatides in mouse models of inherited glycosphingolipid disorders: determination by nano-electrospray ionization tandem mass spectrometry.

Sandhoff R, Hepbildikler ST, Jennemann R, Geyer R, Gieselmann V, Proia RL, Wiegandt H, Grone HJ. Sandhoff R, et al. Among authors: proia rl. J Biol Chem. 2002 Jun 7;277(23):20386-98. doi: 10.1074/jbc.M110641200. Epub 2002 Mar 27. J Biol Chem. 2002. PMID: 11919180 Free article.

2

Physiological substrates for human lysosomal beta -hexosaminidase S.

Hepbildikler ST, Sandhoff R, Kolzer M, Proia RL, Sandhoff K. Hepbildikler ST, et al. Among authors: proia rl. J Biol Chem. 2002 Jan 25;277(4):2562-72. doi: 10.1074/jbc.M105457200. Epub 2001 Nov 13. J Biol Chem. 2002. PMID: 11707436 Free article.

3

Novel class of glycosphingolipids involved in male fertility.

Sandhoff R, Geyer R, Jennemann R, Paret C, Kiss E, Yamashita T, Gorgas K, Sijmonsma TP, Iwamori M, Finaz C, Proia RL, Wiegandt H, Gröne HJ. Sandhoff R, et al. Among authors: proia rl. J Biol Chem. 2005 Jul 22;280(29):27310-8. doi: 10.1074/jbc.M502775200. Epub 2005 May 25. J Biol Chem. 2005. PMID: 15917254 Free article.

4

Evidence for the involvement of Glu-355 in the catalytic action of human beta-hexosaminidase B.

Pennybacker M, Schuette CG, Liessem B, Hepbildikler ST, Kopetka JA, Ellis MR, Myerowitz R, Sandhoff K, Proia RL. Pennybacker M, et al. Among authors: proia rl. J Biol Chem. 1997 Mar 21;272(12):8002-6. doi: 10.1074/jbc.272.12.8002. J Biol Chem. 1997. PMID: 9065471 Free article.

5

Interruption of ganglioside synthesis produces central nervous system degeneration and altered axon-glial interactions.

Yamashita T, Wu YP, Sandhoff R, Werth N, Mizukami H, Ellis JM, Dupree JL, Geyer R, Sandhoff K, Proia RL. Yamashita T, et al. Among authors: proia rl. Proc Natl Acad Sci U S A. 2005 Feb 22;102(8):2725-30. doi: 10.1073/pnas.0407785102. Epub 2005 Feb 14. Proc Natl Acad Sci U S A. 2005. PMID: 15710896 Free PMC article.

6

Combinatorial ganglioside biosynthesis.

Kolter T, Proia RL, Sandhoff K. Kolter T, et al. Among authors: proia rl. J Biol Chem. 2002 Jul 19;277(29):25859-62. doi: 10.1074/jbc.R200001200. Epub 2002 May 13. J Biol Chem. 2002. PMID: 12011101 Free article. Review. No abstract available.

7

Sphingosine kinase 1/S1P receptor signaling axis controls glial proliferation in mice with Sandhoff disease.

Wu YP, Mizugishi K, Bektas M, Sandhoff R, Proia RL. Wu YP, et al. Among authors: proia rl. Hum Mol Genet. 2008 Aug 1;17(15):2257-64. doi: 10.1093/hmg/ddn126. Epub 2008 Apr 17. Hum Mol Genet. 2008. PMID: 18424450 Free PMC article.

8

Depletion of ceramides with very long chain fatty acids causes defective skin permeability barrier function, and neonatal lethality in ELOVL4 deficient mice.

Li W, Sandhoff R, Kono M, Zerfas P, Hoffmann V, Ding BC, Proia RL, Deng CX. Li W, et al. Among authors: proia rl. Int J Biol Sci. 2007 Feb 6;3(2):120-8. doi: 10.7150/ijbs.3.120. Int J Biol Sci. 2007. PMID: 17311087 Free PMC article.

9

Enhanced insulin sensitivity in mice lacking ganglioside GM3.

Yamashita T, Hashiramoto A, Haluzik M, Mizukami H, Beck S, Norton A, Kono M, Tsuji S, Daniotti JL, Werth N, Sandhoff R, Sandhoff K, Proia RL. Yamashita T, et al. Among authors: proia rl. Proc Natl Acad Sci U S A. 2003 Mar 18;100(6):3445-9. doi: 10.1073/pnas.0635898100. Epub 2003 Mar 10. Proc Natl Acad Sci U S A. 2003. PMID: 12629211 Free PMC article.

10

Systemic inflammation in glucocerebrosidase-deficient mice with minimal glucosylceramide storage.

Mizukami H, Mi Y, Wada R, Kono M, Yamashita T, Liu Y, Werth N, Sandhoff R, Sandhoff K, Proia RL. Mizukami H, et al. Among authors: proia rl. J Clin Invest. 2002 May;109(9):1215-21. doi: 10.1172/JCI14530. J Clin Invest. 2002. PMID: 11994410 Free PMC article.

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