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Page 1
Novel CFTR mutations in black cystic fibrosis patients.
Feuillet-Fieux MN, Ferrec M, Gigarel N, Thuillier L, Sermet I, Steffann J, Lenoir G, Bonnefont JP. Feuillet-Fieux MN, et al. Among authors: sermet i. Clin Genet. 2004 Apr;65(4):284-7. doi: 10.1111/j.1399-0004.2004.00230.x. Clin Genet. 2004. PMID: 15025720
[Potential nasal transepithelial difference].
Fajac I, Sermet I. Fajac I, et al. Among authors: sermet i. Rev Pneumol Clin. 2008 Feb;64(1):34-7. doi: 10.1016/j.pneumo.2008.06.001. Rev Pneumol Clin. 2008. PMID: 18613347 Review. French. No abstract available.
New clinical diagnostic procedures for cystic fibrosis in Europe.
De Boeck K, Derichs N, Fajac I, de Jonge HR, Bronsveld I, Sermet I, Vermeulen F, Sheppard DN, Cuppens H, Hug M, Melotti P, Middleton PG, Wilschanski M; ECFS Diagnostic Network Working Group; EuroCareCF WP3 Group on CF diagnosis. De Boeck K, et al. Among authors: sermet i. J Cyst Fibros. 2011 Jun;10 Suppl 2:S53-66. doi: 10.1016/S1569-1993(11)60009-X. J Cyst Fibros. 2011. PMID: 21658643 Free article. Review.
Guideline on the design and conduct of cystic fibrosis clinical trials: the European Cystic Fibrosis Society-Clinical Trials Network (ECFS-CTN).
De Boeck K, Bulteel V, Tiddens H, Wagner T, Fajac I, Conway S, Dufour F, Smyth AR, Lee T, Sermet I, Kassai B, Elborn S; ECFS-CTN network partners. De Boeck K, et al. Among authors: sermet i. J Cyst Fibros. 2011 Jun;10 Suppl 2:S67-74. doi: 10.1016/S1569-1993(11)60010-6. J Cyst Fibros. 2011. PMID: 21658644 Free article.
Nasal polyposis and cystic fibrosis(CF): review of the literature.
Feuillet-Fieux MN, Lenoir G, Sermet I, Elie C, Djadi-Prat J, Ferrec M, Magen M, Couloigner V, Manach Y, Lacour B, Bonnefont JP. Feuillet-Fieux MN, et al. Among authors: sermet i. Rhinology. 2011 Aug;49(3):347-55. doi: 10.4193/Rhino10.225. Rhinology. 2011. PMID: 21858268 Review.
Amikacin liposome inhalation suspension for chronic Pseudomonas aeruginosa infection in cystic fibrosis.
Bilton D, Pressler T, Fajac I, Clancy JP, Sands D, Minic P, Cipolli M, Galeva I, Solé A, Quittner AL, Liu K, McGinnis JP 2nd, Eagle G, Gupta R, Konstan MW; CLEAR-108 Study Group. Bilton D, et al. J Cyst Fibros. 2020 Mar;19(2):284-291. doi: 10.1016/j.jcf.2019.08.001. Epub 2019 Aug 23. J Cyst Fibros. 2020. PMID: 31451351 Free PMC article. Clinical Trial.
Standards of care for CFTR variant-specific therapy (including modulators) for people with cystic fibrosis.
Southern KW, Castellani C, Lammertyn E, Smyth A, VanDevanter D, van Koningsbruggen-Rietschel S, Barben J, Bevan A, Brokaar E, Collins S, Connett GJ, Daniels TWV, Davies J, Declercq D, Gartner S, Gramegna A, Hamilton N, Hauser J, Kashirskaya N, Kessler L, Lowdon J, Makukh H, Martin C, Morrison L, Nazareth D, Noordhoek J, O'Neill C, Owen E, Oxley H, Raraigh KS, Raynal C, Robinson K, Roehmel J, Schwarz C, Sermet I, Shteinberg M, Sinha I, Takawira C, van Mourik P, Verkleij M, Waller MD, Duff A. Southern KW, et al. Among authors: sermet i. J Cyst Fibros. 2023 Jan;22(1):17-30. doi: 10.1016/j.jcf.2022.10.002. Epub 2022 Oct 28. J Cyst Fibros. 2023. PMID: 36916675 Free article.
[Cervical tumefaction in a teenager with cystic fibrosis].
Vrielynck S, Roques C, Sermet I, Emond S, Lenoir G. Vrielynck S, et al. Among authors: sermet i. Arch Pediatr. 2007 Oct;14(10):1210-2. doi: 10.1016/j.arcped.2007.06.010. Epub 2007 Jul 12. Arch Pediatr. 2007. PMID: 17628456 French.
[Fungal infections in cystic fibrosis].
Le Bourgeois M, Sermet I, Bailly-Botuha C, Delacourt C, de Blic J. Le Bourgeois M, et al. Among authors: sermet i. Arch Pediatr. 2011 May;18 Suppl 1:S15-21. doi: 10.1016/S0929-693X(11)70936-8. Arch Pediatr. 2011. PMID: 21596282 French.
Lung clearance index: evidence for use in clinical trials in cystic fibrosis.
Kent L, Reix P, Innes JA, Zielen S, Le Bourgeois M, Braggion C, Lever S, Arets HG, Brownlee K, Bradley JM, Bayfield K, O'Neill K, Savi D, Bilton D, Lindblad A, Davies JC, Sermet I, De Boeck K; European Cystic Fibrosis Society Clinical Trial Network (ECFS-CTN) Standardisation Committee. Kent L, et al. Among authors: sermet i. J Cyst Fibros. 2014 Mar;13(2):123-38. doi: 10.1016/j.jcf.2013.09.005. Epub 2013 Dec 5. J Cyst Fibros. 2014. PMID: 24315208 Free article. Review.
Comparing Mycobacterium massiliense and Mycobacterium abscessus lung infections in cystic fibrosis patients.
Roux AL, Catherinot E, Soismier N, Heym B, Bellis G, Lemonnier L, Chiron R, Fauroux B, Le Bourgeois M, Munck A, Pin I, Sermet I, Gutierrez C, Véziris N, Jarlier V, Cambau E, Herrmann JL, Guillemot D, Gaillard JL; OMA group. Roux AL, et al. Among authors: sermet i. J Cyst Fibros. 2015 Jan;14(1):63-9. doi: 10.1016/j.jcf.2014.07.004. Epub 2014 Jul 30. J Cyst Fibros. 2015. PMID: 25085077 Free article.
Rapid Improvement after Starting Elexacaftor-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and Advanced Pulmonary Disease.
Burgel PR, Durieu I, Chiron R, Ramel S, Danner-Boucher I, Prevotat A, Grenet D, Marguet C, Reynaud-Gaubert M, Macey J, Mely L, Fanton A, Quetant S, Lemonnier L, Paillasseur JL, Da Silva J, Martin C; French Cystic Fibrosis Reference Network Study Group. Burgel PR, et al. Am J Respir Crit Care Med. 2021 Jul 1;204(1):64-73. doi: 10.1164/rccm.202011-4153OC. Am J Respir Crit Care Med. 2021. PMID: 33600738
[Cystic fibrosis: chemical drugs to cure genetic diseases].
Lallemand JY, Leclaire B, Sermet I, Lenoir G. Lallemand JY, et al. Among authors: sermet i. Bull Acad Natl Med. 2005 May;189(5):789-95; discussion 795-6. Bull Acad Natl Med. 2005. PMID: 16433451 French.
Recommendations for the classification of diseases as CFTR-related disorders.
Bombieri C, Claustres M, De Boeck K, Derichs N, Dodge J, Girodon E, Sermet I, Schwarz M, Tzetis M, Wilschanski M, Bareil C, Bilton D, Castellani C, Cuppens H, Cutting GR, Drevínek P, Farrell P, Elborn JS, Jarvi K, Kerem B, Kerem E, Knowles M, Macek M Jr, Munck A, Radojkovic D, Seia M, Sheppard DN, Southern KW, Stuhrmann M, Tullis E, Zielenski J, Pignatti PF, Ferec C. Bombieri C, et al. Among authors: sermet i. J Cyst Fibros. 2011 Jun;10 Suppl 2:S86-102. doi: 10.1016/S1569-1993(11)60014-3. J Cyst Fibros. 2011. PMID: 21658649 Free article.
Effectiveness of bacteriophages in the sputum of cystic fibrosis patients.
Saussereau E, Vachier I, Chiron R, Godbert B, Sermet I, Dufour N, Pirnay JP, De Vos D, Carrié F, Molinari N, Debarbieux L. Saussereau E, et al. Among authors: sermet i. Clin Microbiol Infect. 2014 Dec;20(12):O983-90. doi: 10.1111/1469-0691.12712. Epub 2014 Jul 26. Clin Microbiol Infect. 2014. PMID: 24920209 Free article.
Is the raised volume rapid thoracic compression technique ready for use in clinical trials in infants with cystic fibrosis?
Matecki S, Kent L, de Boeck K, Le Bourgeois M, Zielen S, Braggion C, Arets HG, Bradley J, Davis S, Sermet I, Reix P; respiratory function group of the European Cystic Fibrosis Society Clinical Trial Network. Matecki S, et al. Among authors: sermet i. J Cyst Fibros. 2016 Jan;15(1):10-20. doi: 10.1016/j.jcf.2015.03.015. Epub 2015 Apr 15. J Cyst Fibros. 2016. PMID: 25890589 Free article. Review.
Influence of perfusate temperature on nasal potential difference.
Bronsveld I, Vermeulen F, Sands D, Leal T, Leonard A, Melotti P, Yaakov Y, de Nooijer R, De Boeck K, Sermet I, Wilschanski M, Middleton PG; European Cystic Fibrosis Society – Diagnostic Network Working Group. Bronsveld I, et al. Among authors: sermet i. Eur Respir J. 2013 Aug;42(2):389-93. doi: 10.1183/09031936.00097712. Epub 2012 Oct 25. Eur Respir J. 2013. PMID: 23100510 Free article.
Defining DIOS and constipation in cystic fibrosis with a multicentre study on the incidence, characteristics, and treatment of DIOS.
Houwen RH, van der Doef HP, Sermet I, Munck A, Hauser B, Walkowiak J, Robberecht E, Colombo C, Sinaasappel M, Wilschanski M; ESPGHAN Cystic Fibrosis Working Group. Houwen RH, et al. Among authors: sermet i. J Pediatr Gastroenterol Nutr. 2010 Jan;50(1):38-42. doi: 10.1097/MPG.0b013e3181a6e01d. J Pediatr Gastroenterol Nutr. 2010. PMID: 19525866
A European consensus for the evaluation and management of infants with an equivocal diagnosis following newborn screening for cystic fibrosis.
Mayell SJ, Munck A, Craig JV, Sermet I, Brownlee KG, Schwarz MJ, Castellani C, Southern KW; European Cystic Fibrosis Society Neonatal Screening Working Group. Mayell SJ, et al. Among authors: sermet i. J Cyst Fibros. 2009 Jan;8(1):71-8. doi: 10.1016/j.jcf.2008.09.005. Epub 2008 Oct 28. J Cyst Fibros. 2009. PMID: 18957277 Free article.
Lung transplantation in childhood and adolescence: unicentric 14-year experience with sex matching as the main prognosticator.
Mangiameli G, Arame A, Boussaud V, Petitti T, Rivera C, Pricopi C, Badia A, Achouh P, Legras A, Guillemain R, Riquet M, Cholley B, Sermet I, Le Pimpec Barthes F. Mangiameli G, et al. Among authors: sermet i. Eur J Cardiothorac Surg. 2016 Mar;49(3):810-7. doi: 10.1093/ejcts/ezv243. Epub 2015 Jul 16. Eur J Cardiothorac Surg. 2016. PMID: 26188011
SLC34A3 mutations in patients with hereditary hypophosphatemic rickets with hypercalciuria predict a key role for the sodium-phosphate cotransporter NaPi-IIc in maintaining phosphate homeostasis.
Bergwitz C, Roslin NM, Tieder M, Loredo-Osti JC, Bastepe M, Abu-Zahra H, Frappier D, Burkett K, Carpenter TO, Anderson D, Garabedian M, Sermet I, Fujiwara TM, Morgan K, Tenenhouse HS, Juppner H. Bergwitz C, et al. Among authors: sermet i. Am J Hum Genet. 2006 Feb;78(2):179-92. doi: 10.1086/499409. Epub 2005 Dec 9. Am J Hum Genet. 2006. PMID: 16358214 Free PMC article.
Nasal potential difference measurements in diagnosis of cystic fibrosis: an international survey.
Naehrlich L, Ballmann M, Davies J, Derichs N, Gonska T, Hjelte L, van Konigsbruggen-Rietschel S, Leal T, Melotti P, Middleton P, Tümmler B, Vermeulen F, Wilschanski M; ECFS Diagnostic Network Working Group. Naehrlich L, et al. J Cyst Fibros. 2014 Jan;13(1):24-8. doi: 10.1016/j.jcf.2013.08.006. Epub 2013 Sep 7. J Cyst Fibros. 2014. PMID: 24022019 Free article.